Trans-sphenoidal encephalocele in association with Dandy-Walker complex and cardiovascular anomalies.
We present a case of trans-sphenoidal encephalomeningocele in association with a posterior cranial fossa malformation which fulfils the criteria for the Dandy-Walker complex [1]. Congenital cardiovascular defects were also present. An abnormality of neural crest development may be responsible for the combined occurrence of these anomalies.
Joy
H M
HM
Department of Neuroradiology, Wessex Neurological Centre, Southampton General Hospital, UK.
Barker
C S
CS
Small
J H
JH
Armitage
M
M
D000328:Adult; D003616:Dandy-Walker Syndrome / Q000150:complications* / Q000175:diagnosis; D004677:Encephalocele / Q000150:complications* / Q000175:diagnosis; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications*; D006801:Humans; D008279:Magnetic Resonance Imaging; D014057:Tomography, X-Ray Computed