title: Rare association of hypertrophic cardiomyopathy and complete atrioventricular block with prompt disappearance of outflow gradient after DDD pacing.
abstract: Although arrhythmias are common in hypertrophic cardiomyopathy (HCM), complete atrioventricular (AV) block is very unusual. A 27-year-old female presented with a recent history of syncope and exercise intolerance. ECG demonstrated complete AV block. Two-dimensional Doppler echocardiography revealed HCM with a 60 mmHg left ventricular outflow tract (LVOT) gradient. A temporary transvenous ventricular pacemaker was inserted urgently, and subsequently replaced by a permanent DDD pacemaker. All symptoms were eliminated. This symptomatic improvement was associated with complete disappearance of LVOT gradient at the time of implantation. No gradient was observed during early follow-up and at 6 months after DDD pacemaker implantation.
authors.affiliation: Department of Cardiology, Izmir Ataturk State Hospital, Turkey.
authors.forename: M
authors.initials: M
authors.lastname: Yesil
authors.forename: S
authors.initials: S
authors.lastname: Bayata
authors.forename: I
authors.initials: I
authors.lastname: Susam
authors.forename: H
authors.initials: H
authors.lastname: Dinçkal
authors.forename: N
authors.initials: N
authors.lastname: Postaci
mesh_terms: D000328:Adult; D002304:Cardiac Pacing, Artificial; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications*; D004562:Electrocardiography; D005260:Female; D006327:Heart Block / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D006801:Humans; D012008:Recurrence; D013575:Syncope / Q000209:etiology; D018487:Ventricular Dysfunction, Left / Q000209:etiology*