Dental findings in Morquio syndrome (mucopolysaccharidoses type IVa).
Morquio syndrome is a disorder of mucopolysaccharide metabolism with specific skeletal features. The clinical and radiographic appearance of the teeth resembles hypoplastic amelogenesis imperfecta with thin enamel of normal radiodensity. The dental practitioner has a part to play in collaboration with medical colleagues in the recognition and diagnosis of this condition.
Barker
D
D
Department of Child Dental Health, Dental Hospital and School, Richardson Road, Newcastle upon Tyne, UK NE2 4AZ.
Welbury
R R
RR
D000567:Amelogenesis Imperfecta / Q000175:diagnosis*; D002675:Child, Preschool; D003743:Dental Enamel / Q000002:abnormalities; D003744:Dental Enamel Hypoplasia / Q000175:diagnosis; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D009085:Mucopolysaccharidosis IV / Q000175:diagnosis*; D014075:Tooth Discoloration / Q000175:diagnosis