title: Intraabdominal lymphangiomyoma in an infant with protein-losing enteropathy and hemihypertrophy.
abstract: Lymphangiomyoma is an extremely rare tumor occurring exclusively in women of reproductive age. The tumor is characterized by proliferation of immature smooth muscle along the lymphatic vessels of the abdomen, thorax and lung. Although lymphangiomyoma has been reported in a young girl and a girl infant, none has been reported in boys. We report herein a case of lymphangiomyoma in a two-year-old boy. The unusual presentation in this patient was that the tumor arose from the small bowel mesentery without any evidence of lung involvement. The tumor was extirpated and lymphangiomyomatosis was confirmed pathologically.
authors.affiliation: Department of Pediatric Surgery, Inönü University Faculty of Medicine, Malatya, Turkey.
authors.forename: U
authors.initials: U
authors.lastname: Koltuksuz
authors.forename: U
authors.initials: U
authors.lastname: Ozgen
authors.forename: S
authors.initials: S
authors.lastname: Ozen
authors.forename: K
authors.initials: K
authors.lastname: Saraç
authors.forename: M H
authors.initials: MH
authors.lastname: Gürsoy
mesh_terms: D000714:Anastomosis, Surgical; D006801:Humans; D007223:Infant; D007414:Intestinal Neoplasms / Q000150:complications / Q000473:pathology / Q000601:surgery; D007421:Intestine, Small; D008203:Lymphangiomyoma / Q000150:complications / Q000473:pathology / Q000601:surgery; D008297:Male; D011504:Protein-Losing Enteropathies / Q000209:etiology*; D014057:Tomography, X-Ray Computed