[Ehlers-Danlos syndrome associated with acute pancreatitis].
Ehlers-Danlos syndrome is an inherited connective tissue disease characterized by articular laxity, hyperelastic skin and tissue fragility. The syndrome is genetically, biochemically and clinically heterogeneous and several well-defined subtypes have been identified. We describe a patient with the type IV variant of this syndrome who developed acute spontaneous pancreatitis.
Indart
A
A
Servicio de Aparato Digestivo, Hospital de Aránzazu, San Sebastián.
Zugasti
P
P
Alzate
L F
LF
Arenas
J I
JI
D000208:Acute Disease; D000328:Adult; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D017809:Fatal Outcome; D006801:Humans; D008297:Male; D010195:Pancreatitis / Q000150:complications*
Síndrome de Ehlers-Danlos asociado a pancreatitis aguda.