title: Papillon-Lefèvre syndrome with pyogenic hepatic abscess: a rare association.
abstract: Papillon-Lefèvre syndrome in a 14-year-old boy presenting with palmoplantar keratoderma, periodontosis, recurrent pyogenic infections of the skin, and hepatic abscesses is reported for its rarity and unusual manifestations. The patient showed a dramatic response to acitretin therapy.
authors.affiliation: Department of Dermatology and Venereology, Maulana Azad Medical College and Associated Lok Nayak Hospital, New Delhi, India.
authors.forename: S
authors.initials: S
authors.lastname: Khandpur
authors.forename: B S
authors.initials: BS
authors.lastname: Reddy
mesh_terms: D017255:Acitretin / Q000627:therapeutic use; D000293:Adolescent; D000848:Anodontia / Q000473:pathology; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007641:Keratolytic Agents / Q000627:therapeutic use; D008100:Liver Abscess / Q000150:complications*; D008297:Male; D010214:Papillon-Lefevre Disease / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology
chemical_list: D007641:Keratolytic Agents; D017255:Acitretin