title: [Diagnostic criteria of atypical benign partial epilepsy syndrome in childhood].
abstract: The paper presents an analysis of clinical-neuropsychological peculiarities of the syndrome of atypical benign partial childhood epilepsy (pseudolennox syndrome) of 6 patients (3 boys, 3 girls). An age of the onset of the disease was between 1.5-4 years. There was polymorphism of paroxysms, their high frequency with an obligate presence of hemifacial fits and atypical absences. Night generalized tonic-clonic attacks and the falling attacks were found in 67% of the patients. Spectrum of the neurological disorders included disorders of speech and a slight cerebella symptomatology. Regional "rolandic" activity and diffuse epileptiformed disorders, increasing into a phase of a slow sleep, were registered by EEG. Resistance to anticonvulsive therapy was revealed. The authors had demonstrated a nosologic independence of pseudolennox syndrome and had considered worth while to pick it out in a group of cryptogenic partial forms of epilepsy together with the epileptic aphasia of Landu-Kleffner and an epilepsy with the continuous peak-waves during the slow sleep.
authors.forename: K Iu
authors.initials: KIu
authors.lastname: Mukhin
authors.forename: L Iu
authors.initials: LIu
authors.lastname: Glukhova
authors.forename: A S
authors.initials: AS
authors.lastname: Petrukhin
authors.forename: N S
authors.initials: NS
authors.lastname: Iukhalina
authors.forename: O V
authors.initials: OV
authors.lastname: Gaman
mesh_terms: D000927:Anticonvulsants / Q000627:therapeutic use; D001037:Aphasia / Q000175:diagnosis / Q000209:etiology; D001921:Brain / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D004569:Electroencephalography; D004828:Epilepsies, Partial / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D004832:Epilepsy, Absence / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D019305:Epilepsy, Rolandic / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009483:Neuropsychological Tests; D012720:Severity of Illness Index; D016896:Treatment Outcome
chemical_list: D000927:Anticonvulsants
vernacular_title: Diagnosticheskie kriterii sindroma atipichnoĭ dobrokachestvennoĭ partsial'noĭ épilepsii detskogo vozrasta.