Biventricular implantable cardioverter defibrillator use in a patient with heart failure and ventricular tachycardia secondary to Emery-Dreifuss syndrome.
We report a case of fully transvenous single-unit biventricular implantable cardioverter defibrillator (ICD) use in a 43-year-old woman with a manifesting carrier form of muscular dystrophy (Emery-Dreifuss syndrome). The indication for biventricular ICD use was progressive heart failure with ventricular arrhythmia, permanent atrial fibrillation and previous VVIR pacemaker insertion. Single-unit transvenous biventricular ICD implantation was undertaken without complication. No potentially serious device malfunction was noted during subsequent follow-up. We conclude that single-unit biventricular ICD implantation is feasible for pacing and ventricular tachyarrhythmia control in patients with underlying atrial fibrillation.
Department of Cardiology, Harefield Hospital, Uxbridge, Middlesex, UK.
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Walker
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Levy
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Rex
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Paul
D000328:Adult; D017147:Defibrillators, Implantable; D004867:Equipment Design; D005260:Female; D006333:Heart Failure / Q000209:etiology* / Q000628:therapy*; D006801:Humans; D020389:Muscular Dystrophy, Emery-Dreifuss / Q000150:complications*; D017180:Tachycardia, Ventricular / Q000209:etiology* / Q000628:therapy*