Angiomatosis of bone and soft tissue: a spectrum of disease from diffuse lymphangiomatosis to vanishing bone disease in young patients.
The application of cross-sectional imaging in the investigation of patients with angiomatosis reveals that lymphangiomatosis and vanishing bone disease should not be considered as separate entities, but rather as a spectrum of disease. We present a pictorial review of eight patients demonstrating the manifestations of soft tissue and bony involvement. We highlight a subgroup of patients with chyloid pleural effusions who have a poor prognosis.
Aviv
R I
RI
Department of Radiology, Great Ormond Street Hospital, UK. richardaviv@lineone.net
McHugh
K
K
Hunt
J
J
D000293:Adolescent; D000328:Adult; D000798:Angiomatosis / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D001847:Bone Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D001859:Bone Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D002423:Cause of Death; D002648:Child; D002675:Child, Preschool; D018450:Disease Progression; D005260:Female; D006801:Humans; D007223:Infant; D008202:Lymphangioma / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D008279:Magnetic Resonance Imaging; D008297:Male; D010015:Osteolysis, Essential / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D010996:Pleural Effusion / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D011379:Prognosis; D014057:Tomography, X-Ray Computed