[Massive lytic osteodystrophy or Gorham-Stout disease of the craniomaxillofacial area].
Gorham's disease also called idiopathic massive osteolysis represents a rare affection with unknown aetiology. This disease was described in different bones of the body but its location on maxillo-facial skeleton is particular by the number of cases in the world (only 32), by morphological, functional consequences and the prognosis. The authors describe a new case of male teenager (17 years old) who had a massive osteolysis of mandibular ramus, upper maxillary, malaire, sphenoid, temporal and occipital left bone. The authors give precision about epidemiological data, methods of diagnosis and therapeutic procedures.
Hôpital des Spécialités, Service ORL, BP 6220, Rabat-Instituts, Maroc.
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Oujilal
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A
Lazrak
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H
Benhalima
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M
Boulaich
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Amarti
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A
Saidi
M
M
Kzadri
D000293:Adolescent; D005147:Facial Bones / Q000473:pathology; D005500:Follow-Up Studies; D006801:Humans; D007091:Image Processing, Computer-Assisted; D021621:Imaging, Three-Dimensional; D008279:Magnetic Resonance Imaging; D008297:Male; D008336:Mandibular Diseases / Q000175:diagnosis* / Q000532:radiotherapy; D008439:Maxillary Diseases / Q000175:diagnosis* / Q000532:radiotherapy; D010015:Osteolysis, Essential / Q000175:diagnosis* / Q000473:pathology / Q000532:radiotherapy; D012886:Skull / Q000473:pathology; D014057:Tomography, X-Ray Computed