Cavopulmonary connection after repair of pulmonary vein stenoses.
We report a case of heterotaxia with single-ventricle physiology undergoing successively pulmonary artery banding (PAB) at 8 months of age, repair of pulmonary vein (PV) stenoses at 15 months of age, and a fenestrated total cavopulmonary connection (TCPC) combined with repair of a regurgitant common atrioventricular (AV) valve and a Damus-Stansel operation for a restrictive subaortic ventricle at 5 years of age, followed by percutaneous closure of the fenestration. The child is now 10 years old and is, to the best of our knowledge, the only reported long-term survivor of a Fontan type procedure done after repair of PV stenoses.
Department of Cardiac Surgery and Pediatric Cardiology, H pital Universitaire des Enfants Reine Fabiola, Free University of Brussels, Belgium. thierry.bové@az.vub.ac.be
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D002648:Child; D002675:Child, Preschool; D003241:Consanguinity; D005260:Female; D005500:Follow-Up Studies; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000235:genetics / Q000601:surgery*; D006801:Humans; D007223:Infant; D011667:Pulmonary Veins / Q000002:abnormalities / Q000601:surgery; D011668:Pulmonary Veno-Occlusive Disease / Q000235:genetics / Q000601:surgery*; D012086:Reoperation