[Multiple pigmented basalioma of the scalp in a patient with Curschmann-Steinert myotonia dystrophica. Confirmation of a rare symptom constellation].
A 50-year-old woman presented with myotonic dystrophy (Curschmann-Steinert disease) and multiple pigmented basal cell carcinomas of the scalp. She also had typical androgenetic alopecia seen in this disorder. In 1986 Stieler and Plewig described the first patient with myotonic dystrophy and multiple basal cell carcinomas. There may be a genetic predisposition for cutaneous tumors with follicular origin, as multiple pilomatricomas also occur frequently in such patients.
Abteilung für Dermatologie, Kantonsspital Aarau, CH-5001 Aarau.
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D000505:Alopecia / Q000209:etiology; D002280:Basal Cell Carcinoma / Q000150:complications* / Q000473:pathology; D005260:Female; D006258:Head and Neck Neoplasms / Q000150:complications* / Q000473:pathology; D006801:Humans; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000150:complications*; D009378:Neoplasms, Multiple Primary / Q000150:complications* / Q000473:pathology; D012535:Scalp / Q000473:pathology; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000150:complications* / Q000473:pathology