Aortic origin of the right pulmonary artery associated with ductus arteriosus in an adult. A case report.
We describe the case of a 26-year-old female in functional class I (NYHA), with aortic origin of the right pulmonary artery associated with a persistent ductus arteriosus and severe pulmonary artery hypertension (101/40-70 mm Hg), which remained elevated (89/40-60 mm Hg) after the administration of 100% oxygen. Right pulmonary artery pressure (125/60-86 mm Hg) was higher than that of main pulmonary artery and similar to aorta pressure. The patient was successfully treated: surgical closure of the ductus arteriosus and end-to-end anastomosis between the pulmonary artery and right pulmonary artery were carried out. Systolic pulmonary arterial pressure, estimated by echocardiography Doppler, was 60 mm Hg six months after surgery. Cross-sectional echocardiogram showed the anastomosis of the right pulmonary artery with the main pulmonary artery. Pulmonary gammagraphy showed both lungs perfused through the main pulmonary artery; right lung perfusion was lesser than left lung perfusion, 30 vs. 70% respectively. Aortic origin of a right or left pulmonary artery is a heart disease seen in patients during the course of the first year of life. Its frequency is < 1% among all the congenital cardiopathies and the survival rate to adult life is very low. The originality of this paper is the presentation of a rare congenital cardiopathy treated surgically in an adult.
Rangel
A
A
Departamento de Hemodinamia, Hospital de Especialidades, Centro Médico La Raza, IMSS, Calles de Seris y Zaachila, 02990 México, D.F.
Argüero
R
R
Albarrán
H
H
Ocampo
S
S
Baleón
R
R
Nandayapa
O
O
Careaga
G
G
Quintero
L R
LR
Chávez
E
E
D000328:Adult; D004374:Ductus Arteriosus, Patent / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011859:Radiography; D011877:Radionuclide Imaging; D014463:Ultrasonography