Chondromyxoid fibroma of the nasal bone with extension into the frontal and ethmoidal sinuses: report of one case and a review of the literature.
Chondromyxoid fibroma is a rare benign tumor that usually occurs in the long bones. A 50-year-old patient presented with chondromyxoid fibroma of the nasal bone with extension into the frontal and ethmoidal sinuses. This is the fourth case reported to date in the literature. The clinical manifestations of the tumor were very limited, and the appearance at rhinoscopy was misleading. Radiologic imaging showed a soft tissue lesion invading the adjacent bony structures and the dura mater. Surgery was performed by a combined team of otorhinolaryngologists and neurosurgeons, and total excision of the tumor was achieved. The histologic diagnosis of this tumor is difficult because of its similarities to chondrosarcoma. [Editorial comment: The authors concisely review management of this rare tumor, emphasizing that complete surgical excision, rather than curettage, is required for long term control.]
Department of ENT and Cervicofacial Surgery, Hôpital Kremlin Bicêtre, 78 avenue du Général Leclerc, Paris, France.
B
B
Baujat
P
P
Attal
E
E
Racy
J
J
Quillard
F
F
Parker
A
A
Evennou
S
S
Bobin
D005005:Ethmoid Sinus / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D005260:Female; D005626:Frontal Sinus / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008875:Middle Aged; D009295:Nasal Bone / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D009372:Neoplasms, Connective Tissue / Q000473:pathology* / Q000601:surgery; D009669:Nose Neoplasms / Q000473:pathology* / Q000601:surgery; D011859:Radiography