Primary cardiac leiomyosarcoma originating from the pulmonary valve. Case report and review of the literature.
Primary cardiac tumours are rare findings (incidence 0.02% according to a recent meta-analysis) with dismal prognosis. Approximately 25% are malignant, mostly represented by sarcomas. Among these, leiomyosarcomas are exceptional. Treatment for primary cardiac leiomyosarcomas consists of radical surgical resection followed by adjuvant radiation therapy and/or chemotherapy. The mean survival after surgery and adjuvant therapies is 6.8 months. We present a rare case of a 40- year-old male patient with a primary cardiac leiomysarcoma originating from the pulmonary valve. This patient died after surgery and implantation of a homograft of the pulmonary trunk. Furthermore, the literature has been reviewed.
Schröder
S
S
Department of Internal Medicine, Division of Cardiology, University of Tübingen, Tübingen, Germany. Dr.Schroeder@t-online.de
Walker
T
T
Greschniok
A
A
Herdeg
C
C
Karsch
K R
KR
Ziemer
G
G
D000328:Adult; D006338:Heart Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D006801:Humans; D007890:Leiomyosarcoma / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D008297:Male; D011664:Pulmonary Valve