Anaesthetic management of a child with type VIIc Ehlers-Danlos syndrome.
Ehlers-Danlos syndrome type VIIc is characterized by altered tensile strength of connective tissue. Several severe complications exist but skin fragility is the origin of perioperative morbidity during routine procedures. We describe the difficulties encountered during the anaesthetic management of a child suffering from the disease, and suggest special care advices to avoid any skin injury.
Dubois
P E
PE
Department of Anaesthesia, University Clinics UCL of Mont-Godinne, B-5530 Yvoir, Belgium.
Veyckemans
F
F
Ledent
M M
MM
Michel
M
M
de Clety
S C
SC
D000769:Anesthesia, Inhalation / Q000009:adverse effects; D002648:Child; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005260:Female; D006484:Hemorrhoids / Q000601:surgery; D006554:Hernia, Umbilical / Q000601:surgery; D006801:Humans; D007442:Intubation, Intratracheal; D011183:Postoperative Complications / Q000209:etiology / Q000473:pathology; D013927:Thrombosis / Q000601:surgery