Localized neurological necrotizing vasculitides. Three cases with isolated mononeuritis multiplex.
Localized vasculitic neuropathies are increasingly reported. We describe 3 cases of peripheral neuropathy with necrotizing vasculitis confined to nerves and muscles without systemic involvement. These neuropathies were severe and relapsing, in contrast to a usually benign prognosis. Our cases appear to be isolated vasculitic neuropathies, with vasculitis strictly limited to the peripheral neuromuscular system without nonspecific clinical and/or biological systemic involvement.
Abgrall
S
S
Service de Médecine Interne, H pital Avicenne and Université Paris, Nord, Bobigny, France.
Mouthon
L
L
Cohen
P
P
Authier
F J
FJ
Nizou
R
R
Ropert
A
A
Ghérardi
R
R
Guillevin
L
L
D000368:Aged; D001706:Biopsy; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D020422:Mononeuropathies / Q000209:etiology / Q000473:pathology*; D018482:Muscle, Skeletal / Q000098:blood supply / Q000473:pathology; D009336:Necrosis; D010525:Peripheral Nerves / Q000098:blood supply / Q000473:pathology; D012008:Recurrence; D014657:Vasculitis / Q000150:complications / Q000473:pathology*