Aortico-pulmonary paraganglioma associated with bilateral carotid body tumors. Diagnostic presentation and clinical implications.
A case of mediastinal paraganglioma in association with bilateral carotid body tumors is presented. Characteristic radiological findings included a hypointense signal in T1-weighted, a hyperintense signal in T2-weighted magnetic resonance (MR) images and a vascular enhancement pattern in dynamic contrast enhanced MR imaging. Thus, feeding vessels could be depicted noninvasively. The importance of family screening in affected individuals is stressed, as a hereditary form of the disease exists in which multiple paragangliomas are common.
Hann
U
U
Department of Diagnostic Radiology, Eberhard-Karl University of Tübingen, Germany. ulrich.hahn@med.uni-tuebingen.de
Geist-Barth
B
B
Menon
A K
AK
Greschniok
A
A
Hoffmann
J
J
Raygrotzki
S
S
D001013:Aorta, Thoracic; D002345:Carotid Body Tumor / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008479:Mediastinal Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D010236:Paraganglioma, Extra-Adrenal / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D011651:Pulmonary Artery; D014057:Tomography, X-Ray Computed