Marfan's syndrome: a review.
Marfan's syndrome is an inherited disorder of connective tissue, in which the most pronounced abnormalities occur in the musculoskeletal, cardiovascular and ocular systems. Aortic dilatation and dissection are the major causes of morbidity and mortality. Recent advances in surgical techniques and earlier intervention have reduced postoperative mortality and morbidity.
Aburawi
E H
EH
Department of Paediatric Cardiology, Freeman Hospital, Newcastle upon Tyne NE7 7DN.
O'Sullivan
J
J
Hasan
A
A
D000293:Adolescent; D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D000328:Adult; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D002648:Child; D002675:Child, Preschool; D002985:Clinical Protocols; D003937:Diagnosis, Differential; D005260:Female; D020022:Genetic Predisposition to Disease; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008382:Marfan Syndrome / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D008875:Middle Aged; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000628:therapy; D014463:Ultrasonography
D000319:Adrenergic beta-Antagonists