Alveolar soft-part sarcoma: a rare soft-tissue malignancy with distinctive clinical and radiological features.
Alveolar soft-part sarcoma (ASPS) is a rare tumour. Certain distinctive clinical and radiological features suggest the correct diagnosis. There is moderate predilection for young women. ASPS almost always arises in skeletal muscle and occurs most frequently in the lower limbs. There is often a long clinical history and a large mass at presentation. Two young females with ASPS presented with very vascular tumours in the thigh, with prominent intra- and extra-tumoural blood vessels. The imaging findings and the existing literature are reviewed.
Pang
L M
LM
Department of Diagnostic Radiology and Organ Imaging, Chinese University of Hong Kong.
Roebuck
D J
DJ
Griffith
J F
JF
Kumta
S M
SM
Metreweli
C
C
D000293:Adolescent; D000328:Adult; D001706:Biopsy; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D005260:Female; D006801:Humans; D018810:Magnetic Resonance Angiography; D018234:Sarcoma, Alveolar Soft Part / Q000175:diagnosis* / Q000473:pathology; D012983:Soft Tissue Neoplasms / Q000175:diagnosis* / Q000473:pathology; D013848:Thigh / Q000473:pathology; D014057:Tomography, X-Ray Computed