Massive progression of diffuse hepatic lymphangiomatosis after liver resection and rapid deterioration after liver transplantation.
Hepatic involvement is an exceptional presentation of lymphangiomatosis. In this case report we describe a patient who underwent liver transplantation secondary to progressive hepatic involvement, which occurred 2 yr after partial hepatectomy. Within 1 yr after liver transplantation the disease condition deteriorated, with rapid progression of pre-existing skeletal lesions and development of pulmonary disease. We conclude that liver transplantation may be a treatment option for hepatic lymphangiomatosis. In the presence of pre-existing extrahepatic lesions, however, liver transplantation seems to be contraindicated.
Datz
C
C
Department of Internal Medicine, Landeskrankenhaus Salzburg, Austria.
Graziadei
I W
IW
Dietze
O
O
Jaschke
W
W
Königsrainer
A
A
Sandhofer
F
F
Margreiter
R
R
D000328:Adult; D000075202:Contraindications; D018450:Disease Progression; D005260:Female; D006498:Hepatectomy; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology* / Q000601:surgery*; D016031:Liver Transplantation; D008202:Lymphangioma / Q000473:pathology* / Q000601:surgery*; D013997:Time Factors