[Congenital pulmonary fibrosarcoma. Differential diagnosis of infantile pulmonary spindle cell tumors].
Primary pulmonary mesenchymal tumors are rare causes of intrathoracic lesions in newborns. We describe a case of pulmonary spindle-cell tumor with features of infantile fibrosarcoma and discuss the differential diagnosis of spindle-cell lesions in this location. In view of further case reports of the literature, this neoplasia can best be categorized in a spectrum of fibroblastic/myofibroblastic differentiated spindle-cell tumors, with excellent prognosis. Especially in congenital lesions a favorable clinical course is to be expected after complete surgical resection. Additional radio- and/or chemotherapy is not recommended.
Kuhnen
C
C
Institut für Pathologie, Berufsgenossenschaftliche Kliniken Bergmannsheil-Ruhr-Universität Bochum, Bürkle-de-la-Camp-Platz 1, 44789 Bochum. patho-bhl@ruhr-uni-bochum.de
Harms
D
D
Niessen
K H
KH
Diehm
T
T
Müller
K M
KM
D003937:Diagnosis, Differential; D005354:Fibrosarcoma / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008175:Lung Neoplasms / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D012509:Sarcoma / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed