title: [Congenital pulmonary fibrosarcoma. Differential diagnosis of infantile pulmonary spindle cell tumors].
abstract: Primary pulmonary mesenchymal tumors are rare causes of intrathoracic lesions in newborns. We describe a case of pulmonary spindle-cell tumor with features of infantile fibrosarcoma and discuss the differential diagnosis of spindle-cell lesions in this location. In view of further case reports of the literature, this neoplasia can best be categorized in a spectrum of fibroblastic/myofibroblastic differentiated spindle-cell tumors, with excellent prognosis. Especially in congenital lesions a favorable clinical course is to be expected after complete surgical resection. Additional radio- and/or chemotherapy is not recommended.
authors.affiliation: Institut für Pathologie, Berufsgenossenschaftliche Kliniken Bergmannsheil-Ruhr-Universität Bochum, Bürkle-de-la-Camp-Platz 1, 44789 Bochum. patho-bhl@ruhr-uni-bochum.de
authors.forename: C
authors.initials: C
authors.lastname: Kuhnen
authors.forename: D
authors.initials: D
authors.lastname: Harms
authors.forename: K H
authors.initials: KH
authors.lastname: Niessen
authors.forename: T
authors.initials: T
authors.lastname: Diehm
authors.forename: K M
authors.initials: KM
authors.lastname: Müller
mesh_terms: D003937:Diagnosis, Differential; D005354:Fibrosarcoma / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008175:Lung Neoplasms / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D012509:Sarcoma / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed