Familial idiopathic dilatation of the right atrium with complete atrio-ventricular block: a new syndrome?
Familial occurrence of idiopathic dilatation of the right atrium is extremely rare. This is the first description of a family in which 2 siblings had a syndrome of idiopathic dilatation of the right atrium associated with complete atrio-ventricular block. The family workup did not show other family members to be affected, and the question we raise is whether or not this might be a new syndrome.
Blondheim
D S
DS
Department of Cardiology, Sieff Government Hospital, Safed, Israel. blond@netvision.net.il
Klein
R
R
Plich
M
M
Marmor
A T
AT
D000293:Adolescent; D000328:Adult; D004108:Dilatation, Pathologic / Q000235:genetics; D005192:Family Health; D005260:Female; D006325:Heart Atria / Q000473:pathology*; D006327:Heart Block / Q000235:genetics*; D006801:Humans; D009206:Myocardium / Q000473:pathology*