title: Massive progression of diffuse hepatic lymphangiomatosis after liver resection and rapid deterioration after liver transplantation.
abstract: Hepatic involvement is an exceptional presentation of lymphangiomatosis. In this case report we describe a patient who underwent liver transplantation secondary to progressive hepatic involvement, which occurred 2 yr after partial hepatectomy. Within 1 yr after liver transplantation the disease condition deteriorated, with rapid progression of pre-existing skeletal lesions and development of pulmonary disease. We conclude that liver transplantation may be a treatment option for hepatic lymphangiomatosis. In the presence of pre-existing extrahepatic lesions, however, liver transplantation seems to be contraindicated.
authors.affiliation: Department of Internal Medicine, Landeskrankenhaus Salzburg, Austria.
authors.forename: C
authors.initials: C
authors.lastname: Datz
authors.forename: I W
authors.initials: IW
authors.lastname: Graziadei
authors.forename: O
authors.initials: O
authors.lastname: Dietze
authors.forename: W
authors.initials: W
authors.lastname: Jaschke
authors.forename: A
authors.initials: A
authors.lastname: Königsrainer
authors.forename: F
authors.initials: F
authors.lastname: Sandhofer
authors.forename: R
authors.initials: R
authors.lastname: Margreiter
mesh_terms: D000328:Adult; D000075202:Contraindications; D018450:Disease Progression; D005260:Female; D006498:Hepatectomy; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology* / Q000601:surgery*; D016031:Liver Transplantation; D008202:Lymphangioma / Q000473:pathology* / Q000601:surgery*; D013997:Time Factors