Bronchial mucoepidermoid tumour in a child presenting with organomegaly due to secondary amyloidosis: case report and review of the literature.
Childhood bronchial mucoepidermoid tumours (BMET) are rare. A 12-year-old boy with hepatosplenomegaly underwent liver biopsy which diagnosed amyloidosis. Chest radiograph and CT, performed for recurrent respiratory symptoms, identified a left lower lobe tumour, which was subsequently excised. Histology showed a BMET. A literature review reveals 51 reported cases of BMET in children. Common presenting symptoms include fever, cough and recurrent pneumonia. Diagnosis is often delayed and patients with recurrent respiratory symptoms should undergo CT or bronchoscopy. The association between amyloidosis and BMET in this case is unique and has not been previously described, but may be coincidental.
Andronikou
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Red Cross Children's Hospital, University of Cape Town, Department of Paediatric Radiology, Klipfontein Road, Rondebusch, Cape Town, South Africa. docsav@mweb.co.za
Kader
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D000686:Amyloidosis / Q000150:complications* / Q000473:pathology; D001984:Bronchial Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D001999:Bronchoscopy; D002648:Child; D006529:Hepatomegaly / Q000209:etiology*; D006801:Humans; D008107:Liver Diseases / Q000150:complications* / Q000473:pathology; D008297:Male; D018298:Mucoepidermoid Tumor / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D013163:Splenomegaly / Q000209:etiology*; D014057:Tomography, X-Ray Computed