[Bietti's crystalline dystrophy. A 5-year progression].
METHODS
The case of a 54 year old male patient with Bietti's Crystalline Dystrophy is presented. Bietti's Crystalline Dystrophy is a rare form of tapetoretinal degeneration associated with retinal crystalline deposits, geographic areas of atrophy of the retinal pigment epithelium and choriocapillaris in the posterior pole as well as pigment clumps in the mid-periphery. The case of one patient with a 5 year follow-up is described.


CONCLUSIONS
Minimal changes were observed by means of the ophthalmoscopic and fluorescein angiographic examinations. A slow progression of the pigmentary epithelium defects and of the choriocapillary atrophy was observed.
Sánchez Vicente
J L
JL
Hospital del Insalud de Ceuta, 11130 Chiclana, Espana.
Herrador Montiel
A
A
Díez-Garretas
C
C
Guiote Linares
J R
JR
D001284:Atrophy; D002829:Choroid / Q000473:pathology; D002894:Chromosomes, Human, Pair 4 / Q000235:genetics; D003460:Crystallization; D003937:Diagnosis, Differential; D018450:Disease Progression; D004596:Electroretinography; D005451:Fluorescein Angiography; D005500:Follow-Up Studies; D005808:Genes, Recessive; D006801:Humans; D008297:Male; D008875:Middle Aged; D010857:Pigment Epithelium of Eye / Q000473:pathology; D011859:Radiography; D012168:Retinal Pigments / Q000032:analysis / Q000737:chemistry; D012174:Retinitis Pigmentosa / Q000000981:diagnostic imaging / Q000235:genetics / Q000473:pathology*; D014792:Visual Acuity
D012168:Retinal Pigments