Transposition with absent pulmonary valve syndrome: early repair of a rare case.
The congenital absence of the pulmonary valve cusps can occur either isolated or in association with other heart lesions. We report a very rare case of a 40-day-old infant with transposition of the great arteries, ventricular septal defect, pulmonary annular stenosis, absent pulmonary valve and aneurysmal dilation of the central pulmonary arteries, who received surgical treatment at our institution.
Oppido
G
G
Department of Pediatric Cardiology, Bambino Gesù Hospital, Rome, Italy.
Carotti
A
A
Albanese
S B
SB
Amodeo
A
A
Pasquini
L
L
Di Donato
R M
RM
D019917:Blood Vessel Prosthesis Implantation; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography; D013536:Suture Techniques; D014188:Transposition of Great Vessels / Q000000981:diagnostic imaging / Q000601:surgery*