[Endomyocardial fibrosis in Behcet's disease: a case report of a pseudo-tumoral form].
Endomyocardial fibrosis is very rare in Behcet's disease. The authors report the case of a 28 year old patient with Behcet's disease complicated by a pseudo-tumoral right ventricular formation on echocardiography. This misleading appearance suggested the diagnosis of cardiac thrombus or tumour and led to a surgical approach which revealed a fibrous moderator band suggesting endomyocardial fibrosis, confirmed by antomopathological analysis. Besides the originality of this case and the unusual pseudo-tumoral presentation, the authors underline the difficulties of establishing the diagnosis, despite the advances of medical imaging. The pseudo-tumoral intra-cardiac lesion in a suggestive clinical context (Behcet's disease) should raise suspicion of the diagnosis of endomyocardial fibrosis.
Belmadani
K
K
Service de médecine B, hôpital militaire d'instruction Mohammed-V, Rabat, Maroc.
Dahreddine
A
A
Benyass
A
A
Hda
A
A
Boukili
M A
MA
Ohayon
V
V
Archane
M I
MI
Pavie
A
A
Gandjbakhch
I
I
D000328:Adult; D001528:Behcet Syndrome / Q000150:complications*; D003328:Coronary Thrombosis / Q000175:diagnosis / Q000473:pathology; D003937:Diagnosis, Differential; D004452:Echocardiography; D004719:Endomyocardial Fibrosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology; D006338:Heart Neoplasms / Q000175:diagnosis / Q000473:pathology; D006801:Humans; D008297:Male