title: Living-donor lobar lung transplantation for primary ciliary dyskinesia.
abstract: A ventilator-dependent patient with primary ciliary dyskinesia underwent successful living-donor lobar lung transplantation. The case was a 24-year-old woman who had developed recurrent lower respiratory infection and became ventilator-dependent due to severe bronchiectasis. Transmission electron microscopy of the resected bronchus demonstrated inner dynein arm deficiency.
authors: Department of Surgery II, Okayama University School of Medicine, Japan. hdate@nigeka2.hospital.okayama-u.ac.jp
authors: H
authors: H
authors: Date
authors: M
authors: M
authors: Yamashita
authors: I
authors: I
authors: Nagahiro
authors: M
authors: M
authors: Aoe
authors: A
authors: A
authors: Andou
authors: N
authors: N
authors: Shimizu
mesh_terms: D000328:Adult; D001987:Bronchiectasis / Q000473:pathology / Q000601:surgery; D002923:Cilia / Q000473:pathology; D002925:Ciliary Motility Disorders / Q000473:pathology / Q000601:surgery*; D004398:Dyneins / Q000172:deficiency; D005260:Female; D006801:Humans; D019520:Living Donors; D016040:Lung Transplantation / Q000473:pathology*; D008854:Microscopy, Electron
chemical_list: D004398:Dyneins