[Von Hippel-Lindau disease associated with renal cell carcinoma and bilateral cystadenoma of the epididymis: a case report].
We present a case report of von Hippel-Lindau disease associated with renal cell carcinoma and bilateral cystadenoma of the epididymis. A 26-year-old man appeared with painless tumors of the bilateral scrotal contents. Ultrasonography and other radiographic examinations including computed tomographic scan and dripinfusion pyelography showed multiocular tumors in the bilateral epididymis and a right renal tumor 3 cm in diameter. The tumors of the bilateral epididymis were surgically resected and of the right renal tumor enucleated. Histopathological examination revealed cystadenoma of the epididymis and renal cell carcinoma (clear cell carcinoma, G1, pT1a). He has not received adjuvant therapy, and is doing well with no evidence of metastatic disease 2 years after surgery.
Inamoto
T
T
Department of Urology, Osaka Medical College.
Azuma
H
H
Watsuji
T
T
Iwamoto
Y
Y
Segawa
N
N
Sakamoto
T
T
Kotake
Y
Y
Gohji
K
K
Ueda
H
H
Katsuoka
Y
Y
D000328:Adult; D002292:Carcinoma, Renal Cell / Q000209:etiology* / Q000601:surgery; D003537:Cystadenoma / Q000209:etiology* / Q000601:surgery; D004822:Epididymis / Q000601:surgery; D006801:Humans; D007680:Kidney Neoplasms / Q000209:etiology* / Q000601:surgery; D008297:Male; D017354:Point Mutation; D013736:Testicular Neoplasms / Q000209:etiology* / Q000601:surgery; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000235:genetics