title: [Anesthesia using propofol for a patient with arthrogryposis multiplex congenita].
abstract: Arthrogryposis multiplex congenita (AMC) is a syndrome with multiple persistent limb contractures, often accompanied by associated anomalies. Pediatric patients with AMC frequently require operations, necessitating general endotracheal anesthesia. We report on the anesthesia used for a 14-year-old male with AMC, who required the surgical removal of soft tissue from both hip joints. We used propofol and vecuronium bromide to induce anesthesia, and maintained anesthesia with 40% nitrous oxide, oxygen, and propofol at 6 mg.kg-1.1 hr-1. Both induction and maintenance were smooth, and no hyperthermia occurred perioperatively. Propofol can be safely used for anesthesia in AMC patients.
authors.affiliation: Department of Anesthesiology, School of Medicine, University of Occupational and Environmental Health, Kitakyushu 807-8555.
authors.forename: M
authors.initials: M
authors.lastname: Shiraishi
authors.forename: K
authors.initials: K
authors.lastname: Minami
authors.forename: A
authors.initials: A
authors.lastname: Shigematsu
mesh_terms: D000293:Adolescent; D000771:Anesthesia, Intravenous / Q000379:methods*; D018686:Anesthetics, Intravenous; D001176:Arthrogryposis; D006801:Humans; D008297:Male; D015742:Propofol
chemical_list: D018686:Anesthetics, Intravenous; D015742:Propofol