title: Anaesthetic management of a patient with myotonic dystrophy.
abstract: A 13-year-old boy with myotonic dystrophy underwent insertion of a percutaneous gastrostomy feeding tube under general anaesthesia. We used a laryngeal mask airway and a spontaneously breathing technique with propofol total intravenous anaesthesia. Postoperative vomiting and aspiration, 12 h after the procedure, subsequently required intubation and ventilation. We discuss the anaesthetic management of this case and review the features of the disease to be considered when contemplating anaesthesia in such patients.
authors.affiliation: Department of Anaesthesia, Addenbrookes Hospital, Hilla Road, Cambridge CB2 2QQ, UK.
authors.forename: R J
authors.initials: RJ
authors.lastname: White
authors.forename: S
authors.initials: S
authors.lastname: Bass
mesh_terms: D000293:Adolescent; D000768:Anesthesia, General / Q000379:methods*; D018686:Anesthetics, Intravenous; D004750:Enteral Nutrition; D005774:Gastrostomy; D006801:Humans; D017214:Laryngeal Masks; D008297:Male; D009223:Myotonic Dystrophy; D011183:Postoperative Complications; D020250:Postoperative Nausea and Vomiting / Q000628:therapy; D015742:Propofol; D012121:Respiration, Artificial
chemical_list: D018686:Anesthetics, Intravenous; D015742:Propofol