[Frantz's solid cystic papillary pancreatic carcinoma].
The authors report their own case of a young woman recently operated for a rare form of pancreatic tumor of exocrine origin, so-called Frantz's solid-cystic-papillary carcinoma, for which only a little more than 300 cases have been reported in the world literature. The authors discuss the pathogenesis (it is possible that Frantz's tumor is related to female sex hormones that may play a role in its growth but not in its genesis), clinical (the presentation is not specific and, despite the aid of modern diagnostic imaging, the preoperative diagnosis may be very difficult and this unusual tumor should be considered in the differential diagnosis of large abdominal masses, especially in young females), histological, radiological and surgical features of this tumor. The recommended treatment, given the low grade of malignancy of the tumor and the excellent overall prognosis, has to be as conservative as possible, with respect to the oncological radicality, but every attempt should be made for complete excision since surgical curability is high and radio-chemo-therapy is of no use for its treatment. Since regrowth of the tumor may occur, prolonged follow-up is mandatory.
Berretta
S
S
Dipartimento di Chirurgia, Cattedra di Chirurgia Oncologica, Università degli Studi, Catania, Italy.
Barbagallo
E
E
D'Agata
A
A
Berretta
M
M
D000328:Adult; D002291:Carcinoma, Papillary / Q000175:diagnosis* / Q000601:surgery; D005260:Female; D006801:Humans; D010190:Pancreatic Neoplasms / Q000175:diagnosis* / Q000601:surgery