Dentatorubral-pallidoluysian atrophy (DRPLA) presenting with psychosis.
The authors report on four DRPLA patients who manifested delusions. All patients demonstrated autosomal dominant DRPLA confirmed by standard gene analysis. Patients with DRPLA can exhibit a variety of psychiatric symptoms in addition to extrapyramidal and cerebellar symptoms.
Adachi
N
N
National Center of Neurology and Psychiatry, Kodaira, Japan. adac-chan@tky2.3web.ne.jp
Arima
K
K
Asada
T
T
Kato
M
M
Minami
N
N
Goto Yi
Onuma
T
T
Ikeuchi
T
T
Tsuji
S
S
Hayashi
M
M
Fukutani
Y
Y
D000328:Adult; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D020191:Myoclonic Epilepsies, Progressive / Q000150:complications* / Q000235:genetics; D011618:Psychotic Disorders / Q000209:etiology* / Q000235:genetics