Anaesthetic considerations for a child with combined Prader-Willi syndrome and mitochondrial myopathy.
We report the anaesthetic management of a child with Prader-Willi syndrome and mitochondrial myopathy for open heart surgery. We used ketamine, fentanyl, rocuronium and caudal morphine together with a propofol infusion with no untoward effects. The implications of both conditions for anaesthesia are discussed.
Sharma
A D
AD
Department of Anaesthesiology, Duke University Medical Center, Durham, NC 27710, USA.
Erb
T
T
Schulman
S R
SR
Sreeram
G
G
Slaughter
T F
TF
D000700:Analgesics; D000732:Androstanols; D000758:Anesthesia / Q000379:methods*; D000778:Anesthetics, Dissociative; D018686:Anesthetics, Intravenous; D002405:Catheterization, Central Venous; D002675:Child, Preschool; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000601:surgery*; D006801:Humans; D007649:Ketamine; D017240:Mitochondrial Myopathies / Q000150:complications*; D016343:Monitoring, Intraoperative; D009020:Morphine; D003473:Neuromuscular Nondepolarizing Agents; D011218:Prader-Willi Syndrome / Q000150:complications*; D015742:Propofol; D000077123:Rocuronium
D000700:Analgesics; D000732:Androstanols; D000778:Anesthetics, Dissociative; D018686:Anesthetics, Intravenous; D003473:Neuromuscular Nondepolarizing Agents; D007649:Ketamine; D009020:Morphine; D000077123:Rocuronium; D015742:Propofol