Oral manifestations of Ehlers-Danlos syndrome.
Ehlers-Danlos syndrome is a rare hereditary disease of the connective tissue which can present oral manifestations. A brief history of the disease is presented along with the epidemiology and characteristics of the 8 main phenotypes of the syndrome. The article also describes the case of a 12-year-old patient presenting with hypermobility of the temporo-mandibular joint and capillary fragility, and highlights the precautions to take when treating patients with this syndrome.
Létourneau
Y
Y
Centre de Santé, Basse Côte-Nord.
Pérusse
R
R
Buithieu
H
H
D002648:Child; D003744:Dental Enamel Hypoplasia / Q000209:etiology; D004535:Ehlers-Danlos Syndrome / Q000145:classification / Q000150:complications* / Q000473:pathology; D005260:Female; D006801:Humans; D007593:Joint Instability / Q000209:etiology*; D009059:Mouth Diseases / Q000209:etiology*; D009061:Mouth Mucosa / Q000473:pathology; D010518:Periodontitis / Q000209:etiology; D013705:Temporomandibular Joint Disorders / Q000209:etiology*