[Aortic dissection in pregnancy in Marfan syndrome--case report and treatment concept].
METHODS
Herein we report the case of a 37 year old pregnant women with Marfan syndrome with dilatation of the aorta ascendens of 42 mm preconceptionAl. The dilatation remained stable until 34 weeks of gestation when a aortic dissection (De Bakey type I) occurRed rapidly. The patient underwent a cesarean section and hysterectomy, followed by surgery of the aorta asc. by means of implantation of a valved graft immediately.


CONCLUSIONS
The criteria of a dilatation of the aorta ascendens < 40 mm does not identify reliably those patients who are at risk of dissection during pregnancy. A interdisciplinary approach together with obstetricians, cardiologists and cardiac surgeons is mandatory in all cases of Marfan syndrome and pregnancy.
Preiss
M
M
Klinik für Herz-Thoraxchirurgie, Universitätsklinik Kantonsspital Basel, Basel, Schweiz. michael-preiss@usa.net
Hösli
I
I
Holzgreve
W
W
Zerkowski
H R
HR
D000784:Aortic Dissection / Q000000981:diagnostic imaging* / Q000601:surgery; D001011:Aorta / Q000000981:diagnostic imaging / Q000601:surgery; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging* / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation; D002585:Cesarean Section; D017548:Echocardiography, Transesophageal; D005260:Female; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D007044:Hysterectomy; D007231:Infant, Newborn; D008382:Marfan Syndrome / Q000000981:diagnostic imaging* / Q000601:surgery; D010348:Patient Care Team; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000000981:diagnostic imaging* / Q000601:surgery; D011474:Prosthesis Design; D016216:Ultrasonography, Prenatal