Spontaneous aortic dissection and rupture in a patient with neurofibromatosis.
Vascular involvement in neurofibromatosis type I is a well-recognized but rare feature of the disease. This case report is the first such describing acute aortic dissection and rupture in a patient who also had incidental aneurysms of his carotid and iliac arteries. A review of the literature about pathogenesis and management strategies is also presented.
Chew
D K
DK
Division of Vascular Surgery, Brigham and Women's Hospital, Harvard Medical School, Boston, Mass 02115, USA. dchew@partners.org
Muto
P M
PM
Gordon
J K
JK
Straceski
A J
AJ
Donaldson
M C
MC
D000328:Adult; D000784:Aortic Dissection / Q000209:etiology*; D017544:Aortic Aneurysm, Abdominal / Q000209:etiology*; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications*; D012422:Rupture, Spontaneous