Bilateral ectopia lentis as a presenting feature of medulloepithelioma.
Ectopia lentis may be a feature of numerous systemic and ocular disorders. Kivela and Tarkkanen described an 8-year-old girl with medulloepithelioma who presented with ectopia lentis and a mass behind the temporal iris. Shields reported 2 children with medulloepithelioma who had ectopia lentis associated with neovascular glaucoma. To date, there has been no report of a child with ectopia lentis as the only presentation of an intraocular tumor. We present 2 children with malignant medulloepitheliomas who presented in this fashion.
Gupta
N K
NK
Lions Eye Institute, Albany Medical College, Albany, New York 12208, USA.
Simon
J W
JW
Walton
D S
DS
Augsburger
J J
JJ
D002675:Child, Preschool; D002924:Ciliary Body / Q000473:pathology*; D004479:Ectopia Lentis / Q000175:diagnosis* / Q000601:surgery; D015353:Eye Enucleation; D005260:Female; D006068:Gonioscopy; D006801:Humans; D007223:Infant; D007429:Intraocular Pressure; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis* / Q000601:surgery; D014604:Uveal Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014792:Visual Acuity