title: [Anesthetic management of a child with congenital sensory neuropathy with anhydrosis].
abstract: Congenital sensory neuropathy with anhydrosis is a rare disorder characterized by insensitivity to pain with normal tactile perception, self-mutilation, anhydrosis, recurrent unexplained fever, mental retardation and variable autonomic abnormality. We managed a 14-year-old boy with this syndrome who underwent repair of right femur fracture. Anesthesia was induced with propofol and ketamine. Adequate depth of anesthesia was carefully controlled by processed electroencephalogram, and core body temperature was maintained at 37.0 degrees C during the surgery. The patient was well sedated, and nausea and vomiting were not noted postoperatively. Use of droperidol and propofol may be beneficial for anesthetic management of this syndrome, because droperidol exerts residual hypnotic effect postoperatively, and both drugs have antiemetic property.
authors.affiliation: Department of Anesthesiology, Yamanashi Medical University, Yamanashi 409-3898.
authors.forename: Y
authors.initials: Y
authors.lastname: Terada
authors.forename: A
authors.initials: A
authors.lastname: Furuya
authors.forename: T
authors.initials: T
authors.lastname: Ishiyama
authors.forename: T
authors.initials: T
authors.lastname: Matsukawa
authors.forename: T
authors.initials: T
authors.lastname: Kumazawa
mesh_terms: D000293:Adolescent; D000771:Anesthesia, Intravenous; D004329:Droperidol; D004569:Electroencephalography; D005264:Femoral Fractures / Q000601:surgery; D009477:Hereditary Sensory and Autonomic Neuropathies; D006801:Humans; D007649:Ketamine; D008297:Male; D016343:Monitoring, Intraoperative; D019637:Orthopedic Procedures; D020250:Postoperative Nausea and Vomiting / Q000517:prevention & control; D015742:Propofol
chemical_list: D007649:Ketamine; D004329:Droperidol; D015742:Propofol