title: Two enlarged kidneys: a manifestation of Erdheim-Chester disease.
abstract: Erdheim-Chester disease is a rare form of non-Langerhans' cell histiocytosis. This disorder is characterized by a bone involvement and several extraskeletal manifestations. We describe the case of a patient with a pleural and pericardial effusion leading to tamponade. Pathological examination of pericardium and mediastinal adenopathy was normal. The abdominal computed tomography scan showed two enlarged kidneys suggestive of Erdheim-Chester disease. Bone scan scintigraphy demonstrated symmetrical increased labeling of the long bones. The biopsy of perirenal soft tissue confirmed the diagnosis of Erdheim-Chester disease.
authors.affiliation: Department of Internal Medicine, Groupe Hospitalier Saint-Jacques, Clermont-Ferrand, France.
authors.forename: M
authors.initials: M
authors.lastname: André
authors.forename: I
authors.initials: I
authors.lastname: Delèvaux
authors.forename: B
authors.initials: B
authors.lastname: de Fraissinette
authors.forename: J
authors.initials: J
authors.lastname: Ponsonnaille
authors.forename: N
authors.initials: N
authors.lastname: Costes Chalret
authors.forename: B
authors.initials: B
authors.lastname: Wechsler
authors.forename: J C
authors.initials: JC
authors.lastname: Piette
authors.forename: O
authors.initials: O
authors.lastname: Aumaître
mesh_terms: D001847:Bone Diseases / Q000209:etiology; D015616:Histiocytosis, Non-Langerhans-Cell / Q000150:complications*; D006801:Humans; D007668:Kidney / Q000473:pathology; D007674:Kidney Diseases / Q000209:etiology* / Q000473:pathology; D008297:Male; D008875:Middle Aged