Sézary syndrome in a Malay--case report and literature review.
Sézary syndrome is a rare form of primary cutaneous T cell lymphoma. It is a distinct systemic variant of mycosis fungoides, marked by erythroderma, lymphadenopathy and circulating cerebriform lymphocytes in the peripheral blood. We report a case of Sézary syndrome in a 61-year-old Malay man with a five-year history of indurated plaques, ulcers and tumours on the head and trunk, with characteristic findings on physical examination, skin biopsy, electron microscopy, immunophenotyping and peripheral blood film. A literature review on Sézary syndrome is presented.
Yuen
P
P
Department of Medicine, National University Hospital, Singapore.
Chan
H L
HL
Lee
Y S
YS
D001706:Biopsy; D005145:Face / Q000473:pathology*; D006801:Humans; D016130:Immunophenotyping; D008296:Malaysia; D008297:Male; D008875:Middle Aged; D010808:Physical Examination; D012751:Sezary Syndrome / Q000276:immunology / Q000473:pathology*; D012883:Skin Ulcer / Q000209:etiology / Q000473:pathology*