Diffuse, retroperitoneal mesenteric and intrahepatic periportal plexiform neurofibroma in a 5-year-old boy.
We present a case of plexiform neurofibroma involving the retroperitoneum, mesentery, and liver in a 5-year-old boy who underwent evaluation for extent of a palpable left neck mass. The mass had intrathoracic extension with great vessel encasement and extension into the abdomen. Abdominal CT revealed a diffuse low-attenuation non-enhancing mass encasing the retroperitoneal vessels with serpiginous extension into the liver along the portal vein. This spread pattern of plexiform neurofibroma is an unusual manifestation of neurofibromatosis in a young child.
Fenton
L Z
LZ
Department of Radiology, The Children's Hospital, 1056 East 19th Avenue, B125, Denver, CO 80128, USA. fenton.laura@tchden.org
Foreman
N
N
Wyatt-Ashmead
J
J
D002675:Child, Preschool; D006801:Humans; D008113:Liver Neoplasms / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008297:Male; D008643:Mesentery; D018318:Neurofibroma, Plexiform / Q000175:diagnosis*; D009456:Neurofibromatosis 1 / Q000175:diagnosis; D010534:Peritoneal Neoplasms / Q000175:diagnosis*; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed