title: Bilateral ectopia lentis as a presenting feature of medulloepithelioma.
abstract: Ectopia lentis may be a feature of numerous systemic and ocular disorders. Kivela and Tarkkanen described an 8-year-old girl with medulloepithelioma who presented with ectopia lentis and a mass behind the temporal iris. Shields reported 2 children with medulloepithelioma who had ectopia lentis associated with neovascular glaucoma. To date, there has been no report of a child with ectopia lentis as the only presentation of an intraocular tumor. We present 2 children with malignant medulloepitheliomas who presented in this fashion.
authors.affiliation: Lions Eye Institute, Albany Medical College, Albany, New York 12208, USA.
authors.forename: N K
authors.initials: NK
authors.lastname: Gupta
authors.forename: J W
authors.initials: JW
authors.lastname: Simon
authors.forename: D S
authors.initials: DS
authors.lastname: Walton
authors.forename: J J
authors.initials: JJ
authors.lastname: Augsburger
mesh_terms: D002675:Child, Preschool; D002924:Ciliary Body / Q000473:pathology*; D004479:Ectopia Lentis / Q000175:diagnosis* / Q000601:surgery; D015353:Eye Enucleation; D005260:Female; D006068:Gonioscopy; D006801:Humans; D007223:Infant; D007429:Intraocular Pressure; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis* / Q000601:surgery; D014604:Uveal Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014792:Visual Acuity