Secondary amyloidosis in progressive systemic sclerosis.
Progressive systemic sclerosis (PSS) is a connective tissue disease that may affect many organs, including the kidneys. It is quite rare to see secondary amyloidosis due to PSS. We present a patient with a 9-year history of PSS who developed nephrotic syndrome, and whose renal biopsy was compatible with secondary amyloidosis. He died from massive upper gastrointestinal bleeding caused by oesophageal telangiectasia.
Pamuk
G E
GE
Cerrahpaşa Medical School, University of Istanbul, Turkey. onpamuk80@hotmail.com
Pamuk
O N
ON
Altiparmak
M R
MR
Tanverdi
M
M
Uygun
N
N
Yurdakul
S
S
D000686:Amyloidosis / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D001707:Biopsy, Needle; D018450:Disease Progression; D004932:Esophageal and Gastric Varices / Q000175:diagnosis / Q000628:therapy; D017809:Fatal Outcome; D006471:Gastrointestinal Hemorrhage / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D012595:Scleroderma, Systemic / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D012720:Severity of Illness Index