Persistent esophagotrachea: description of a case.
Esophagotrachea is the most severe form of laryngo-tracheo-esophageal cleft. This congenital anomaly is due to the anomalous differentiation of the primitive cephalic gut into trachea and esophagus. We present a case of a new born female with a common tracheoesophageal canal up to the carina. Atresia ani, a vulvo-vestibular fistula, sacral ipoplasia and others associated anomalies were also present. The baby underwent surgery after a laringo-tracheoscopy and a barium study of the esophagus. The prognosis of this extremely rare malformation is generally poor and the baby died on the fifth day after surgery for a serious ipertensive pneumothorax.
Roggini
M
M
Radiology Department of Pediatric Clinic University of Rome La Sapienza.
Carbone
I
I
Bosco
S
S
Cozzi
D A
DA
Andreoli
G
G
Capocaccia
P
P
D004947:Esophagus / Q000002:abnormalities* / Q000000981:diagnostic imaging; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011859:Radiography; D014132:Trachea / Q000002:abnormalities* / Q000000981:diagnostic imaging