Stable pulmonary capillary haemangiomatosis without symptomatic pulmonary hypertension.
Pulmonary capillary haemangiomatosis is a rare disorder characterised by multiple angiomatous lesions composed of proliferating capillary vessels in the lung parenchyma that usually progress rapidly to establish fatal pulmonary hypertension. The 29 year old man presented here, however, has been stable for 3.5 years since the diagnosis without symptoms of pulmonary hypertension. High resolution computed tomographic findings of the pulmonary lesions seemed specific to the disease.
Takiguchi
Y
Y
Department of Chest Medicine, Chiba University School of Medicine, 1-8-1 Inohana, Chuo-ku, Chiba 260-8670, Japan. yuichi@med.m.chiba-u.ac.jp
Uruma
T
T
Hiroshima
K
K
Motoori
K
K
Watanabe
R
R
Hamaoka
T
T
Okada
O
O
Kimura
H
H
Kuriyama
T
T
D000328:Adult; D018450:Disease Progression; D018324:Hemangioma, Capillary / Q000150:complications / Q000000981:diagnostic imaging* / Q000503:physiopathology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D008168:Lung / Q000000981:diagnostic imaging* / Q000503:physiopathology; D008175:Lung Neoplasms / Q000150:complications / Q000000981:diagnostic imaging* / Q000503:physiopathology; D008297:Male; D011856:Radiographic Image Enhancement; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D014165:Transfer Factor
D014165:Transfer Factor