[Case report of scimitar syndrome in infancy: intracardiac repair after coil embolization of systemic arterial supply to sequestered lung].
A 10-month-old girl was diagnosed with atrial septal defect and pulmonary sequestration and scimitar syndrome. Cardiac catheterization revealed severe pulmonary hypertension, with systemic pulmonary artery pressure 97 mmHg, pulmonary resistance 10.3 U, and Qp/Qs 0.45. Systemic pulmonary artery pressure was decreased from 108 to 75 mmHg by oxygenation. We performed coil embolization of the systemic artery and repair of the partial anomalous pulmonary venous return, division and reimplantation of the anomalous vein into the right atrium, and a patch was inserted to redirect flow to the left atrium. The severe pulmonary hypertension was improved and echocardiography showed systemic pulmonary artery pressure of 45 mmHg. The postoperative hemodynamic and respiratory condition was satisfactory.
Ishibashi
N
N
Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
Takahashi
Y
Y
Kikuchi
T
T
Kobayashi
N
N
Suzuki
R
R
Mizutani
S
S
D001998:Bronchopulmonary Sequestration / Q000628:therapy*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D004621:Embolization, Therapeutic; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications; D007223:Infant; D012587:Scimitar Syndrome / Q000601:surgery*