Amyloidotic muscle pseudohypertrophy: case report.
The authors report one case of amyloidosis associated with muscular pseudohypertrophy in a 46-year-old woman, who developed weakness, macroglossia and muscle hypertrophy associated with primary systemic amyloidosis. Electromyography showed a myopathic pattern and bilateral carpal tunnel syndrome. The muscle biopsy presented with a type I and II fiber hypertrophy and infiltration of amyloid material in the interstitious space and artery walls. She underwent bone marrow transplantation with stabilization and subjective improvement of the clinical picture.
Scola
R H
RH
Serviço de Doenças Neuromusculares da Disciplina de Neurologia e de Propedêutica Médica, Departamento de Clínica Médica, Hospital de Clínicas, Universidade Federal do Paraná, Curitiba, PR, Brasil. scola@hc.ufpr.br
Werneck
L C
LC
Ramos
C S
CS
Pasquini
R
R
Graf
H
H
Arruda
W O
WO
D000686:Amyloidosis / Q000150:complications* / Q000628:therapy; D016026:Bone Marrow Transplantation / Q000379:methods; D005260:Female; D006801:Humans; D006984:Hypertrophy / Q000150:complications / Q000628:therapy; D008875:Middle Aged; D018482:Muscle, Skeletal / Q000473:pathology*; D009135:Muscular Diseases / Q000150:complications* / Q000628:therapy