Primitive neuroectodermal tumor involving the frontal skull base in an infant.
We report here a case of a primitive neuroectodermal tumor involving the frontal skull base in a 5-month-old male infant. He presented with rapidly progressing exophthalmos on the left side. Preoperative magnetic resonance imaging revealed a well-demarcated, enhanced mass of 6 cm in diameter in the intradural extra-axial frontal region. The tumor was totally removed by surgery. Pathological findings were consistent with a primitive neuroectodermal tumor (PNET). Intradural extra-axial PNET is very rare, and its prognosis is poor.
Niwa
J
J
Department of Neurosurgery, Hakodate Municipal Hospital, Japan. niwa@hospital.hakodate.hokkaido.jp
Shimoyama
N
N
Takahashi
Y
Y
D002533:Cerebral Angiography; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D011379:Prognosis; D019291:Skull Base / Q000473:pathology; D019292:Skull Base Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D014057:Tomography, X-Ray Computed