title: Amyotrophic form of Creutzfeldt-Jakob disease with rapid course in 82-year-old man.
abstract: The authors present a case of Creutzfeldt-Jakob disease in 82-year-old man. Besides the onset of the disease in the elderly and short survival time (8 weeks), other uncommon clinical and morphological features also characterized our case. An evident amyotrophic syndrome, confirmed in morphological findings, developed soon after the CJD onset. The spongiform change also observed within the white matter of cerebral hemispheres allowed us to diagnose the 'panencephalopathic' form of CJD.
authors.affiliation: Department of Neurology, Pomeranian Academy of Medicine, Szczecin, Warsaw.
authors.forename: P
authors.initials: P
authors.lastname: Nowacki
authors.forename: J
authors.initials: J
authors.lastname: Kulczycki
authors.forename: A
authors.initials: A
authors.lastname: Narolewska
authors.forename: H
authors.initials: H
authors.lastname: Grzelec
mesh_terms: D000368:Aged; D000369:Aged, 80 and over; D001921:Brain / Q000473:pathology; D002452:Cell Count; D007562:Creutzfeldt-Jakob Syndrome / Q000145:classification / Q000473:pathology*; D018450:Disease Progression; D004569:Electroencephalography; D017809:Fatal Outcome; D005911:Gliosis / Q000209:etiology / Q000473:pathology; D006801:Humans; D008297:Male; D009046:Motor Neurons / Q000473:pathology; D013116:Spinal Cord / Q000473:pathology; D014617:Vacuoles / Q000648:ultrastructure