Papillon Lefevre syndrome: management of a case.
Papillon Lefevre Syndrome is a rare syndrome autosomal recessive in nature, manifesting as keratosis palmoplantaris with periodontitis. A case of Papillon Lefevre Syndrome present in a 12 year old boy is presented. Only the permanent maxillary canines were present in the oral cavity when the patient was first seen, and despite efforts towards preservation, they had to be extracted. (complete dentures were made and the patient was followed up for 26 months.
Nadkarni
U M
UM
Department of Pediatric Dentistry, Nair Hospital Dental College, Mumbai.
Jawdekar
A M
AM
Damle
S G
SG
Sujan
S G
SG
D016301:Alveolar Bone Loss / Q000209:etiology; D002648:Child; D003824:Denture, Complete; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D010214:Papillon-Lefevre Disease / Q000235:genetics / Q000628:therapy*; D010510:Periodontal Diseases / Q000209:etiology / Q000628:therapy*; D016388:Tooth Loss / Q000209:etiology; D014086:Tooth Mobility / Q000209:etiology