Treatment of hand deformities in a long-term survivor with dermolytic bullous dermatosis-recessive (DBD-R).
Treatment of hand deformities in a long-term survivor with dermolytic bullous dermatosis-recessive is described. An "open method" is sufficient for dealing with volar skin defects. There is still no effective treatment for perfect control of blister formation. But appropriate surgery, followed by careful post-operative rehabilitation can give reasonable hand function.
Sugawara
S
S
Juntendo University School of Medicine, Department of Orthopaedic Surgery, Shinobu Sugawara, 2-1-1 Hongo, Bunkyo-ku, Tokyo, 113-8421, Japan.
Kusunose
K
K
Kaneko
K
K
D000328:Adult; D003131:Combined Modality Therapy; D003286:Contracture / Q000209:etiology / Q000601:surgery; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D006227:Hand Deformities, Acquired / Q000209:etiology* / Q000601:surgery*; D018737:Hand Strength; D006801:Humans; D008297:Male; D019637:Orthopedic Procedures / Q000379:methods; D020127:Recovery of Function; D012720:Severity of Illness Index; D016038:Skin Transplantation / Q000379:methods; D016896:Treatment Outcome