[Rare association of rare diseases: Langerhans-cell histiocytosis and lymphangioleiomyomatosis in the lung].
This is a case history of a 24-year-old female patient in whom two rare pulmonary diseases occurred: Langerhans cell histiocytosis and four years later lymphangioleiomyomatosis were diagnosed. Both diseases were verified by the examination of the lung tissue removed by the surgery for pneumothorax. The patient's symptoms were characterised by coughing, dyspnoe, repeated pneumothorax. The authors summarised the characteristics and treatment of these diseases. This case history is worth of reporting for its unique rareness.
Márk
Z
Z
Fóvárosi Onkormányzat Szent János Kórház, Budapest. markzs@matavnet.hu
Sápi
Z
Z
Mészáros
Z
Z
Strausz
J
J
D000328:Adult; D003937:Diagnosis, Differential; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D018192:Lymphangioleiomyomatosis / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D011379:Prognosis