Active aortitis in relapsing polychondritis.
Relapsing polychondritis (RP) is a rare inflammatory multiorgan disorder affecting cartilaginous structures and other connective tissues. Serious cardiovascular complications have been reported in patients with RP, the most frequent being aortic or mitral regurgitation and aortic aneurysms. Aortitis is a very rare complication. An unusual case of active aortitis in a patient with RP, despite intensive immunosuppressive treatment, is described with a special emphasis on the pathological findings.
Selim
A G
AG
Department of Histopathology, Royal Brompton Hospital, Imperial College, School of Medicine, Sydney Street, London SW3 6NP, UK.
Fulford
L G
LG
Mohiaddin
R H
RH
Sheppard
M N
MN
D001011:Aorta / Q000473:pathology / Q000601:surgery; D001022:Aortic Valve Insufficiency / Q000150:complications / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D001025:Aortitis / Q000150:complications* / Q000473:pathology / Q000601:surgery; D004452:Echocardiography; D005260:Female; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D008875:Middle Aged; D011081:Polychondritis, Relapsing / Q000150:complications* / Q000473:pathology / Q000601:surgery