title: Implantation of the malformed cochlea.
abstract: OBJECTIVE
  This study assesses the results of cochlear implantation in children with cochlear malformations.
  
  
  METHODS
  Retrospective, matched-pairs analysis of prospectively collected data.
  
  
  METHODS
  University-based regional cochlear implant center.
  
  
  METHODS
  Seventeen children with osseous cochlear malformations who had undergone implantation were matched and compared with a group of children with normal cochleae who had undergone implantation.
  
  
  METHODS
  All subjects received a multichannel cochlear implant and habilitation.
  
  
  METHODS
  All subjects were tested with the Early Speech Perception test, and the Glendonald Auditory Speech Perception tests for words and sentences. Patients were classified in a standardized speech perception category based on performance on the Early Speech Perception test.
  
  
  RESULTS
  All subjects demonstrated improving performance on all measures of speech perception over time. Overall, the two groups showed no statistically significant differences in performance at 6 and 24 months. However, subjects with malformed cochleae evidenced slower rates of improvement than did their matched control subjects. Subjects with more severe malformations demonstrated poorer performance, but this may have been attributable to preoperative factors rather than to implant performance.
  
  
  CONCLUSIONS
  Children with radiographic cochlear malformations benefit from cochlear implantation with multichannel devices. They ultimately perform as well as their matched counterparts with normal cochleae, although they may improve more slowly over time.
authors.affiliation: Department of Otolaryngology-Head and Neck Surgery, University of Michigan Health System, Ann Arbor, Michigan, U.S.A.
authors.forename: D J
authors.initials: DJ
authors.lastname: Eisenman
authors.forename: C
authors.initials: C
authors.lastname: Ashbaugh
authors.forename: T A
authors.initials: TA
authors.lastname: Zwolan
authors.forename: H A
authors.initials: HA
authors.lastname: Arts
authors.forename: S A
authors.initials: SA
authors.lastname: Telian
mesh_terms: D002648:Child; D002675:Child, Preschool; D003051:Cochlea / Q000002:abnormalities* / Q000601:surgery; D019929:Cochlear Implantation / Q000534:rehabilitation; D004558:Electric Stimulation / Q000295:instrumentation; D004867:Equipment Design; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D006801:Humans; D007223:Infant; D011446:Prospective Studies; D012189:Retrospective Studies; D013067:Speech Perception / Q000502:physiology