[Anesthetic management in a patient with Simpson-Golabi-Behmel syndrome].
We report the anesthetic management of a 4-yr-old boy with Simpson-Golabi-Behmel syndrome. This syndrome is an X-linked condition characterized by pre- and postnatal overgrowth with visceral and skeletal anomalies. Affected males have a distinctive facial appearance with wide nasal bridge, anteverted nostrils, wide-open mouth, enlarged tongue, and large protruding maxilla and jaw. Although it had been speculated preoperatively that airway management would be complicated by the macroglossia, there was no difficulty in endotracheal intubation in the present patient. Preparations for difficult airway management should be made by the anesthesiologist before induction of anesthesia.
Tsuchiya
K
K
Department of Anesthesiology and Critical Care Medicine, Asahikawa Medical College, Asahikawa 078-8510.
Takahata
O
O
Sengoku
K
K
Hamada
I
I
Suzuki
A
A
Iwasaki
H
H
D000015:Abnormalities, Multiple; D000769:Anesthesia, Inhalation; D002675:Child, Preschool; D005145:Face / Q000002:abnormalities*; D008040:Genetic Linkage; D005877:Gigantism; D006801:Humans; D007430:Intraoperative Care; D008260:Macroglossia; D008297:Male; D013577:Syndrome; D014059:Tongue / Q000601:surgery; D014960:X Chromosome