Scoliosis in Gordon's syndrome.
Gordon's Syndrome is described as an autosomal dominant condition with the characteristics of short stature, a stiff spine, camptodactyly (89%), cleft palate (27%) and club feet (73%). The authors present a case report of a patient with this rare entity complicated by an unusual complex spinal deformity. There are no prior reports in the literature concerning operative or nonoperative management of deformity in this patient population. Scoliosis in Gordon's Syndrome shares the characteristics of an arthrogrypotic neuromuscular curve and demands extensive soft tissue release for optimal correction.
Wild
A
A
Orthopaedic University Hospital, Heinrich-Heine-University, Düsseldorf, Germany. wild@med.uni-duesseldorf.de
Schillians
N
N
Kumar
M
M
Mehdian
S H
SH
D000015:Abnormalities, Multiple / Q000235:genetics*; D000293:Adolescent; D002972:Cleft Palate / Q000150:complications* / Q000235:genetics; D003025:Clubfoot / Q000150:complications* / Q000235:genetics; D005260:Female; D005385:Fingers / Q000002:abnormalities*; D005799:Genes, Dominant; D006801:Humans; D009984:Orthopedic Fixation Devices; D019637:Orthopedic Procedures; D012600:Scoliosis / Q000150:complications* / Q000601:surgery*; D013577:Syndrome