An autopsy case of pulmonary capillary hemangiomatosis without evidence of pulmonary hypertension.
We report a case of pulmonary capillary hemangiomatosis (PCH) affecting a 37-year-old woman. PCH is a rare disease accompanying intrapulmonary capillary growth and pulmonary hypertension. In the present case, capillaries infiltrated the alveolar and bronchial walls but not the vascular walls. No signs or symptoms of pulmonary hypertension or right heart hypertrophy/dilatation were present. These findings suggest that vascular involvement in PCH is responsible for the induction of pulmonary hypertension.
Umezu
H
H
Department of Surgical Pathology, Niigata University Hospital, Niigata city, Japan. umezu@med.niigata-u.ac.jp
Naito
M
M
Yagisawa
K
K
Hattori
A
A
Aizawa
Y
Y
D000328:Adult; D004452:Echocardiography; D004487:Edema / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D018324:Hemangioma, Capillary / Q000150:complications / Q000473:pathology*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology / Q000473:pathology*; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000473:pathology; D008168:Lung / Q000098:blood supply / Q000473:pathology*; D008175:Lung Neoplasms / Q000150:complications / Q000473:pathology*; D011650:Pulmonary Alveoli / Q000473:pathology