[Prune belly syndrome and congenital kidney tumors].
BACKGROUND
High end sonography allows the prenatal localization of the kidneys and the corresponding urine drainage system as early as 10-13 weeks of gestation. In mid second trimester, the voiding and filling of the urinary bladder can be demonstrated by ultrasound. Obstructions are the most common abnormalities of the urogenital tract. Though less frequent in incidence, more complex sequences of anomalies such as Prune Belly Syndrome or Megacystis-Microcolon-Intestinal-Hypoperistalsis-Syndrome (MMIHS) can also be detected in early gestational age.


METHODS
Pathogenesis, prenatal diagnosis, pre- and postnatal treatment options and prognosis are discussed.


CONCLUSIONS
The same risk-adapted procedures aimed to protect the fetal urinary excretory function known in the therapeutic regimen of obstructive uropathy are available as treatment options. These range from non-invasive ultrasound for diagnosis and surveillance to needle procedures or even endoscopic interventions. Another rare entity of renal abnormalities are congenital neoplasm's--megaloblastic nephroma, nephroblastoma and neuroblastoma.


CONCLUSIONS
Prognosis and obstetrical management are to be determined individually for each patient.
Strauss
A
A
Klinik und Poliklinik für Frauenheilkunde und Geburtshilfe-Grosshadern, Klinikum der Universität München. Alexander.Strauss@gyn.med.uni-muenchen.de
Girschick
G
G
Fuchshuber
S
S
Hasbargen
U
U
Müller-Wimbauer
M
M
Hepp
H
H
D000310:Adrenal Gland Neoplasms / Q000151:congenital* / Q000000981:diagnostic imaging; D005260:Female; D005865:Gestational Age; D006801:Humans; D007231:Infant, Newborn; D007680:Kidney Neoplasms / Q000151:congenital* / Q000000981:diagnostic imaging; D008297:Male; D018201:Nephroma, Mesoblastic / Q000151:congenital* / Q000000981:diagnostic imaging; D009447:Neuroblastoma / Q000151:congenital* / Q000000981:diagnostic imaging; D011247:Pregnancy; D011379:Prognosis; D011535:Prune Belly Syndrome / Q000000981:diagnostic imaging*; D016216:Ultrasonography, Prenatal; D009396:Wilms Tumor / Q000000981:diagnostic imaging*