title: Hepatopulmonary syndrome occurring after orthotopic liver transplantation.
abstract: Hepatopulmonary syndrome (HPS) is an infrequent complication of liver cirrhosis. Orthotopic liver transplantation (OLT) has gained increasing acceptance as a treatment modality for HPS, although there have been reports of HPS developing after OLT with documented recurrence of cirrhosis. We describe the case of a 9-year-old boy who underwent OLT at 7 months of age because of biliary atresia. He subsequently developed HPS in the setting of chronic rejection without cirrhosis or evidence of portal hypertension. Re-OLT resulted in resolution of HPS and a good clinical outcome.
authors.affiliation: Department of Medicine, Division of Pulmonary and Critical Care Medicine, Medical University of South Carolina, Charleston, SC 29425, USA.
authors.forename: C E
authors.initials: CE
authors.lastname: Avendano
authors.forename: P A
authors.initials: PA
authors.lastname: Flume
authors.forename: P
authors.initials: P
authors.lastname: Baliga
authors.forename: D N
authors.initials: DN
authors.lastname: Lewin
authors.forename: C
authors.initials: C
authors.lastname: Strange
authors.forename: A
authors.initials: A
authors.lastname: Reuben
mesh_terms: D002648:Child; D006084:Graft Rejection / Q000150:complications; D020065:Hepatopulmonary Syndrome / Q000209:etiology* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D008099:Liver / Q000473:pathology; D016031:Liver Transplantation / Q000009:adverse effects*; D008297:Male; D012086:Reoperation; D013997:Time Factors