Hepatopulmonary syndrome occurring after orthotopic liver transplantation.
Hepatopulmonary syndrome (HPS) is an infrequent complication of liver cirrhosis. Orthotopic liver transplantation (OLT) has gained increasing acceptance as a treatment modality for HPS, although there have been reports of HPS developing after OLT with documented recurrence of cirrhosis. We describe the case of a 9-year-old boy who underwent OLT at 7 months of age because of biliary atresia. He subsequently developed HPS in the setting of chronic rejection without cirrhosis or evidence of portal hypertension. Re-OLT resulted in resolution of HPS and a good clinical outcome.
Avendano
C E
CE
Department of Medicine, Division of Pulmonary and Critical Care Medicine, Medical University of South Carolina, Charleston, SC 29425, USA.
Flume
P A
PA
Baliga
P
P
Lewin
D N
DN
Strange
C
C
Reuben
A
A
D002648:Child; D006084:Graft Rejection / Q000150:complications; D020065:Hepatopulmonary Syndrome / Q000209:etiology* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D008099:Liver / Q000473:pathology; D016031:Liver Transplantation / Q000009:adverse effects*; D008297:Male; D012086:Reoperation; D013997:Time Factors