title: Clinical experience in anesthetic management for children with mucopolysaccharidoses: Report of ten cases.
abstract: The mucopolysaccharidoses (MPS) are hereditary disorders. Children with these disorders have multisystem disease and present significant challenges for the anesthesiologist. The establishment and maintenance of an adequate airway represents the most commonly encountered anesthesia-related problem in these patients. We report ten children with MPS who required surgical intervention. One patient died and the others had a good outcome. In this report, we share our experience and discuss the anesthetic risks and management of MPS patients.
authors.affiliation: Department of Anesthesiology, Mackay Memorial Hospital, 92, Chung-Shan North Road, Sec. 2, Taipei, Taiwan.
authors.forename: Y L
authors.initials: YL
authors.lastname: Chan
authors.forename: S P
authors.initials: SP
authors.lastname: Lin
authors.forename: T T
authors.initials: TT
authors.lastname: Man
authors.forename: C R
authors.initials: CR
authors.lastname: Cheng
mesh_terms: D000768:Anesthesia, General / Q000009:adverse effects* / Q000379:methods*; D002648:Child; D017809:Fatal Outcome; D006801:Humans; D007431:Intraoperative Complications; D007442:Intubation, Intratracheal / Q000379:methods; D017214:Laryngeal Masks; D008297:Male; D009083:Mucopolysaccharidoses / Q000503:physiopathology* / Q000601:surgery; D011183:Postoperative Complications