title: Bilateral linear scleroderma "en coup de sabre" associated with facial atrophy and neurological complications.
abstract: BACKGROUND
  Linear scleroderma "en coup de sabre" (LSCS) usually affects one side of the face and head in the frontoparietal area with band-like indurated skin lesions. The disease may be associated with facial hemiatrophy. Various ophthalmological and neurological abnormalities have been observed in patients with LSCS. We describe an unusual case of LSC.
  
  
  METHODS
  A 23 year old woman presented bilateral LSCS and facial atrophy. The patient had epileptic seizures as well as oculomotor and facial nerve palsy on the left side which also had pronounced skin involvement. Clinical features of different stages of the disease are presented.
  
  
  CONCLUSIONS
  The findings of the presented patient with bilateral LSCS and facial atrophy provide further evidence for a neurological etiology of the disease and may also indicate that classic progressive facial hemiatrophy (Parry-Romberg syndrome) and LSCS actually represent different spectra of the same disease.
authors.affiliation: Department of Dermatology, Ruhr-University Bochum, Gudrunstrasse 56, D-44791, Bochum, Germany. t.gambichler@derma.de
authors.forename: T
authors.initials: T
authors.lastname: Gambichler
authors.forename: A
authors.initials: A
authors.lastname: Kreuter
authors.forename: K
authors.initials: K
authors.lastname: Hoffmann
authors.forename: F G
authors.initials: FG
authors.lastname: Bechara
authors.forename: P
authors.initials: P
authors.lastname: Altmeyer
authors.forename: T
authors.initials: T
authors.lastname: Jansen
mesh_terms: D000328:Adult; D000505:Alopecia / Q000209:etiology; D001284:Atrophy / Q000209:etiology; D001763:Blepharoptosis / Q000209:etiology; D002921:Cicatrix / Q000209:etiology; D005150:Facial Hemiatrophy / Q000175:diagnosis / Q000209:etiology*; D005260:Female; D006801:Humans; D009460:Neurologic Examination; D015840:Oculomotor Nerve Diseases / Q000175:diagnosis / Q000209:etiology*; D012594:Scleroderma, Localized / Q000150:complications / Q000175:diagnosis*; D012867:Skin / Q000473:pathology