Bidirectional Glenn shunt in an infant with prune-belly syndrome.
The prune-belly syndrome (PBS) usually is described as a deficiency of the anterior abdominal muscle involving bilateral cryptorchidism and urinary tract malformations. In this report, we will present an eleven-month-old boy with PBS associated with a complex cardiac anomaly. A bilateral bidirectional Glenn shunt was performed with the diagnosis of isolated dextrocardia, single ventricle, pulmonary atresia, incomplete A-V septal defect, hemiazygos continuity, persistent right superior vena cava, patent ductus arteriosus-dependent pulmonary blood flow. The patient required special consideration for postoperative pulmonary care.
Doğan
R
R
Department of Thoracic and Cardiovascular Surgery, Hacettepe University, Faculty of Medicine, 06100 Ankara, Turkey. rdogan@hacettepe.edu.tr
Yilmaz
M
M
Duman U
U
U
Ozkutlu
S
S
D000009:Abdominal Muscles / Q000002:abnormalities / Q000601:surgery*; D003456:Cryptorchidism / Q000150:complications / Q000601:surgery; D003937:Diagnosis, Differential; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D011535:Prune Belly Syndrome / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D014551:Urinary Tract / Q000002:abnormalities / Q000601:surgery