title: [Anesthetic management of a patient with Cockayne's syndrome].
abstract: Cockayne's syndrome is a disease of childhood characterized by mental retardation and premature aging. An 11-year-old girl with Cockayne's syndrome underwent general anesthesia for acute appendicitis. Although we had expected the difficulty of intubation because of her small jaw with limited movement, we could visualize her vocal cord, and intubate easily. High peak airway pressure was needed to ventilate her lung after intubation suggesting decreased lung compliance for this syndrome. We have to consider anesthetic problems resulting not only from pediatric but also from geriatric anesthesia for the management of this syndrome.
authors.affiliation: Department of Anesthesiology, Oita Medical University, Oita 879-5503.
authors.forename: A
authors.initials: A
authors.lastname: Hasegawa
authors.forename: K
authors.initials: K
authors.lastname: Goto
authors.forename: K
authors.initials: K
authors.lastname: Ito
authors.forename: H
authors.initials: H
authors.lastname: Iwasaka
authors.forename: T
authors.initials: T
authors.lastname: Noguchi
mesh_terms: D000208:Acute Disease; D000768:Anesthesia, General / Q000379:methods*; D001064:Appendicitis / Q000601:surgery; D002648:Child; D003057:Cockayne Syndrome / Q000150:complications*; D005260:Female; D006801:Humans; D007442:Intubation, Intratracheal