[Diffuse hemangiomatosis of the liver and spleen in an adult].
Diffuse hemangiomatoses are extremely rare in adults. The etiology and natural history of the disease are not well understood. A case of diffuse hemangiomatosis of the liver and spleen associated with progressive liver failure, thrombocytopenia, and disturbance of blood coagulation (comparable to Kasabach-Merritt syndrome) is presented in a 62-year-old male. We describe the histopathological and immunohistochemical findings and illustrate the morphological aspects of differential diagnosis, distinguishing the disease from other vascular proliferations.
Langner
C
C
Institut für Pathologie, Karl-Franzens-Universität Graz, Osterreich. cord.langner@kfunigraz.ac.at
Thonhofer
R
R
Hegenbarth
K
K
Trauner
M
M
D001706:Biopsy; D003937:Diagnosis, Differential; D004730:Endothelium, Vascular / Q000473:pathology; D006391:Hemangioma / Q000473:pathology*; D018324:Hemangioma, Capillary / Q000473:pathology; D006392:Hemangioma, Cavernous / Q000473:pathology; D006801:Humans; D008099:Liver / Q000473:pathology; D008113:Liver Neoplasms / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D013154:Spleen / Q000473:pathology; D013160:Splenic Neoplasms / Q000473:pathology*
Diffuse Hämangiomatose von Leber und Milz beim Erwachsenen.