[Pure primitive dysautonomia or Bradbury-Eggleston syndrome. Report of 3 cases].
The primary autonomic failure (Bradbury-Eggleston syndrome) is rare. We report three cases (two females and one male) who are 55 year old with orthostatic hypotension, tachycardia, and other signs of dysautonomia. They hadn't a pyramidal, extrapyramidal or cerebellar syndromes. The other causes of postural hypotension are excluded. The autonomic dysfunction was confirmed by autonomic reflex tests and by evaluating of cardiac reflex function; these included heart rate responses to deep breathing and to the valsalva maneuver. Hypotension occurs in a variety of clinical setting; ascertainment of the cause is by non means easy. Primary autonomic failure remains a diagnostic category based on exclusion; its pathophysiology isn't well know and its treatment is only symptomatic.
Marouene
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H
Service d'Exploration fonctionnelle Hôpital, Sfax.
Bellassoued
M
M
Mnif
M
M
Rekik
N
N
Chouayakh
F
F
Zouari
N
N
Abid
M
M
D001342:Autonomic Nervous System Diseases / Q000175:diagnosis / Q000473:pathology*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007024:Hypotension, Orthostatic / Q000209:etiology*; D008297:Male; D008875:Middle Aged; D013610:Tachycardia / Q000209:etiology*
Dysautonomie pure primitive ou syndrome de Bradbury Eggleston. A propos de 3 cas.