title: Myofibroblastic tumors involving bilateral adrenal glands and skin in a patient with common variable immunodeficiency.
abstract: Common variable immunodeficiency (CVID) is a heterogeneous form of primary immune deficiency characterized by hypogammaglobulinemia, recurrent bacterial infections, and various immunologic abnormalities. In addition to recurrent infections, patients with this syndrome have an increased incidence of autoimmune diseases and malignancy. A patient with CVID in whom myofibroblastic tumors affecting both adrenal glands and skin is presented.
authors.affiliation: Istanbul University, Istanbul Medical Faculty, Department of Pediatrics, 34390 Capa, Istanbul, Turkey.
authors.forename: Işik
authors.initials: I
authors.lastname: Yalçin
authors.forename: Ayper
authors.initials: A
authors.lastname: Somer
authors.forename: Ahmet
authors.initials: A
authors.lastname: Akçay
authors.forename: Nesimi
authors.initials: N
authors.lastname: Büyükbabani
authors.forename: Nuran
authors.initials: N
authors.lastname: Salman
authors.forename: Nermin
authors.initials: N
authors.lastname: Güler
mesh_terms: D000293:Adolescent; D000310:Adrenal Gland Neoplasms / Q000473:pathology* / Q000601:surgery; D017074:Common Variable Immunodeficiency / Q000150:complications*; D006801:Humans; D008297:Male; D018224:Myofibromatosis / Q000473:pathology* / Q000601:surgery; D012878:Skin Neoplasms / Q000473:pathology* / Q000601:surgery; D014382:Tuberculosis, Cutaneous / Q000150:complications; D014397:Tuberculosis, Pulmonary / Q000150:complications