title: Limited dorsal myeloschisis associated with multiple vertebral segmentation disorder.
abstract: A 3-year-old girl was admitted to our department with spina bifida occulta. At birth, thoracic dysplasia with severe respiratory dysfunction and a soft pedunculated mass connecting with an intradural mass were noted. The patient did not start to walk and partial removal of the intradural mass was performed via a laminectomy of the fused vertebrae. There was no boundary between the spinal cord and the mass and the histological diagnosis of this mass was connective tissue. The anomalies in this case were considered to be multiple vertebral segmentation disorder (MVSD) and limited dorsal myeloschisis. The coincidence of these anomalies might suggest the causal genesis of MVSD.
authors.affiliation: Department of Neurosurgery, Oita Medical University, Hasama-machi, Oita, Japan. isonom@oita-med.ac.jp
authors.forename: Mitsuo
authors.initials: M
authors.lastname: Isono
authors.forename: Makoto
authors.initials: M
authors.lastname: Goda
authors.forename: Tohru
authors.initials: T
authors.lastname: Kamida
authors.forename: Keisuke
authors.initials: K
authors.lastname: Ishii
authors.forename: Hidenori
authors.initials: H
authors.lastname: Kobayashi
authors.forename: Tomomi
authors.initials: T
authors.lastname: Maeda
authors.forename: Kazuhide
authors.initials: K
authors.lastname: Imai
authors.forename: Tatsuro
authors.initials: T
authors.lastname: Izumi
mesh_terms: D002675:Child, Preschool; D004413:Dysostoses / Q000150:complications* / Q000151:congenital* / Q000473:pathology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008591:Meningomyelocele / Q000473:pathology* / Q000503:physiopathology; D016136:Spina Bifida Occulta / Q000150:complications* / Q000473:pathology* / Q000503:physiopathology; D013126:Spinal Nerve Roots / Q000002:abnormalities* / Q000473:pathology* / Q000503:physiopathology; D013904:Thoracic Vertebrae / Q000002:abnormalities* / Q000473:pathology* / Q000503:physiopathology