Rare venous connection causes severe cyanosis after the Fontan operation.
We describe a rare case of cyanosis following the Fontan operation secondary to right-to-left shunting through a pulmonary vein connected to both the left atrium and the hepatic veins. This is a hazardous anomaly in a Fontan candidate and should be considered in those with unexpected postoperative desaturation.
Nomura
F
F
Cardiothoracic Surgical Unit, Green Lane Hospital, Auckland, New Zealand. fnomura@kure-nh.go.jp
Finucane
K
K
Kerr
A R
AR
D000792:Angiography; D002648:Child; D002675:Child, Preschool; D003490:Cyanosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D003937:Diagnosis, Differential; D018729:Fontan Procedure; D006325:Heart Atria / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D006503:Hepatic Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011183:Postoperative Complications / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D012086:Reoperation