title: Diagnosis and treatment of congenital choledochal cyst: 20 years' experience in China.
abstract: OBJECTIVE
  To summarize the experience of diagnosis and treatment of congenital choledochal cyst in the past 20 years (1980-2000).
  
  
  METHODS
  The clinical data of 108 patients admitted from 1980 to 2000 were analyzed retrospectively.
  
  
  RESULTS
  Abdominal pain,jaundice and abdominal mass were presented in most child cases. Clinical symptoms in adult cases were non-specific, resulting in delayed diagnosis frequently. Fifty-seven patients (52.7%) had coexistent pancreatiobiliary disease. Carcinoma of the biliary duct occurred in 18 patients (16.6%). Ultrasonic examination was undertaken in 94 cases, ERCP performed in 46 cases and CT in 71 cases. All of the cases were correctly diagnosed before operation. Abnormal pancreatobiliary duct junction was found in 39 patients. Before 1985 the diagnosis and classification of congenital choledochal cyst were established by ultrasonography preoperatively and confirmed during operation, the main procedures were internal drainage by cyst enterostomy. After 1985, the diagnosis was established by ERCP and CT, and cystectomy with Roux-en-Y hepaticojejunostomy was the conventional procedures.In 1994, we reported a new and simplified operative procedure in order to reduce the risk of choledochal cyst malignancy. Postoperative complication was mainly retrograde infection of biliary tract, which could be controlled by the administration of antibiotics, there was no perioperative mortality.
  
  
  CONCLUSIONS
  The concept in diagnosis and treatment of congenital choledochal cyst has obviously been changed greatly.CT and ERCP were of great help in the classification of the disease.Currently, cystectomy with Roux-en-Y hepaticojejunostomy is strongly recommended as the choice for patients with type I and type IV cysts. Piggyback orthotopic liver transplantation is indicated in type V cysts (Caroli's disease) with frequently recurrent cholangitis.
authors.affiliation: Department of Surgery, The Second Affiliated Hospital of Zhejiang University School of Medicine, Hangzhou 310009, Zhejiang Province, China. slb5327694@sohu.com
authors.forename: L B
authors.initials: LB
authors.lastname: Shi
authors.forename: S Y
authors.initials: SY
authors.lastname: Peng
authors.forename: X K
authors.initials: XK
authors.lastname: Meng
authors.forename: C H
authors.initials: CH
authors.lastname: Peng
authors.forename: Y B
authors.initials: YB
authors.lastname: Liu
authors.forename: X P
authors.initials: XP
authors.lastname: Chen
authors.forename: Z L
authors.initials: ZL
authors.lastname: Ji
authors.forename: D T
authors.initials: DT
authors.lastname: Yang
authors.forename: H R
authors.initials: HR
authors.lastname: Chen
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D000713:Anastomosis, Roux-en-Y; D002648:Child; D002675:Child, Preschool; D002681:China; D015529:Choledochal Cyst / Q000175:diagnosis* / Q000601:surgery*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011183:Postoperative Complications; D012189:Retrospective Studies; D016896:Treatment Outcome