Temporomandibular region in the Franceschetti's Syndrome. Anatomical study.
Franceschetti's syndrome is a rare, non-fatal, hereditary malformation, usually bilateral, which symmetrically affects orbits, mandible and ear. The authors propose an anatomical description of the temporomandibular region after the dissection of a newborn baby suffering from Franceschetti's Syndrome, dead soon after the birth. A discussion on the different etiopathogenical theories is made. The authors conclude that an alteration of the development of nerve trigeminal branches is the cause of the malformations.
Cannistrà
C
C
Unité de Chirurgie Plastique, Département de Chirurgie, C.H.U., Bichat Claude Bernard, Paris.
Barbet
J P
JP
Houette
A
A
Iannetti
G
G
D004424:Ear Canal / Q000002:abnormalities; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008335:Mandibular Condyle / Q000002:abnormalities; D008342:Mandibulofacial Dysostosis / Q000209:etiology / Q000473:pathology*; D011626:Pterygoid Muscles / Q000002:abnormalities; D013100:Sphenoid Bone / Q000002:abnormalities; D013699:Temporal Arteries / Q000002:abnormalities; D013701:Temporal Bone / Q000002:abnormalities; D013703:Temporal Muscle / Q000002:abnormalities; D013704:Temporomandibular Joint / Q000002:abnormalities* / Q000473:pathology; D014276:Trigeminal Nerve / Q000002:abnormalities; D015050:Zygoma / Q000002:abnormalities