title: Nephron-sparing nephrectomy for giant renal angiomyolipoma associated with lymphangioleiomyomatosis.
abstract: Renal angiomyolipomas are benign tumors known to occur sporadically and in association with genetic syndromes, including tuberous sclerosis and lymphangioleiomyomatosis. Surgical removal or radiographic embolization of angiomyolipomas larger than 4 cm is usually indicated because of an increased risk of spontaneous hemorrhage. We describe successful nephron-sparing surgery for a giant angiomyolipoma and discuss relevant management issues in a patient with lymphangioleiomyomatosis who had previously undergone bilateral pulmonary transplantation.
authors.affiliation: Section of Urologic Oncology, Urological Institute, Cleveland Clinic Foundation, Cleveland, Ohio 44195, USA.
authors.forename: Thomas H S
authors.initials: TH
authors.lastname: Hsu
authors.forename: Jerome
authors.initials: J
authors.lastname: O'Hara
authors.forename: Atul
authors.initials: A
authors.lastname: Mehta
authors.forename: Abraham
authors.initials: A
authors.lastname: Levitin
authors.forename: Eric A
authors.initials: EA
authors.lastname: Klein
mesh_terms: D000328:Adult; D018207:Angiomyolipoma / Q000473:pathology / Q000601:surgery*; D004621:Embolization, Therapeutic; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology / Q000601:surgery*; D016040:Lung Transplantation; D018192:Lymphangioleiomyomatosis / Q000150:complications*; D009392:Nephrectomy / Q000379:methods*