Congenital mitral-aortic discontinuity.
Mitral-aortic (M-A) discontinuity is an uncommonly observed congenital malformation. From the embryologic point of view, it is a failure of the superior endocardial cushion of the A-V canal reach and insert into the aortic root (the mitral-aortic fibrous trigone). It should be differentiated from aorto-left ventricular discontinuity, a complication of endocarditis with excavating abscesses without boundaries. In congenital mitral-aortic discontinuity, the anterior leaflet of the mitral valve fails to insert into the aortic root. We report our experience with 2 patients. In patient 1, the severe left ventricular outflow obstruction was mainly caused by the mobile anterior leaflet of the mitral valve.
Liotta
Domingo
D
Dupuytren-Quilmes Private Hospital, Cardiac Surgery, Faculty of Medicine, University of Morón, Buenos Aires, Argentina. medicina@unimoron.edu.ar
Diluch
Armando
A
Malusardi
Adriano
A
del Rio
Miguel
M
D000328:Adult; D001011:Aorta / Q000002:abnormalities*; D001022:Aortic Valve Insufficiency / Q000209:etiology; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000209:etiology; D006801:Humans; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities*; D014694:Ventricular Outflow Obstruction / Q000209:etiology