title: Disabling pansclerotic morphea of childhood and hypogammaglobulinemia: a curious association.
abstract: This communication describes a 1.5-year-old girl who presented with multiple episodes of infection since early infancy and stiffening of limbs for 2 months. Biopsy of the involved areas showed features consistent with pansclerotic morphea. Immunoglobulin estimation revealed hypogammaglobulinemia. This unique combination of pansclerotic morphea with hypogammaglobulinemia has not been reported before.
authors.affiliation: Department of Pediatrics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.lastname: Devidayal
authors.forename: S
authors.initials: S
authors.lastname: Singh
authors.forename: L
authors.initials: L
authors.lastname: Kumar
authors.forename: B D
authors.initials: BD
authors.lastname: Radotra
mesh_terms: D000361:Agammaglobulinemia / Q000150:complications* / Q000175:diagnosis; D001707:Biopsy, Needle; D002675:Child, Preschool; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018570:Risk Assessment; D012594:Scleroderma, Localized / Q000150:complications* / Q000175:diagnosis / Q000473:pathology*; D012720:Severity of Illness Index