Impact of pregnancy on respiratory capacity in women with muscular dystrophy and kyphoscoliosis. A case report.
BACKGROUND
Restriction of the chest wall in pregnancy prevents adaptive physiologic hyperventilation. This in turn might gradually promote respiratory insufficiency.


METHODS
Two consecutive pregnancies occurred in a woman with severe kyphoscoliosis due to juvenile muscular dystrophy. The patient died postpartum.


CONCLUSIONS
Pregnancies with restrictive lung diseases, including severe scoliosis and kyphoscoliosis, should be considered high risk and thus should be monitored and managed carefully.
Gamzu
Ronni
R
Department of Obstetrics and Gynecology, Lis Maternity Hospital, Tel-Aviv Sourasky Medical Center, 6 Weizman Street, Tel Aviv 64239, Israel. ronn@post.tau.ac.il
Shenhav
Michael
M
Fainaru
Ofer
O
Almog
Benny
B
Kupferminc
Michael
M
Lessing
Joseph B
JB
D000328:Adult; D017809:Fatal Outcome; D005260:Female; D005865:Gestational Age; D006801:Humans; D008176:Lung Volume Measurements; D009136:Muscular Dystrophies / Q000150:complications* / Q000175:diagnosis; D011247:Pregnancy; D011248:Pregnancy Complications / Q000175:diagnosis / Q000209:etiology*; D011256:Pregnancy Outcome; D018566:Pregnancy, High-Risk; D011659:Pulmonary Gas Exchange; D012131:Respiratory Insufficiency / Q000175:diagnosis / Q000209:etiology*; D012600:Scoliosis / Q000150:complications* / Q000175:diagnosis; D012720:Severity of Illness Index