Old age presentation of the Dandy-Walker syndrome associated with unilateral sudden sensorineural deafness and vertigo.
Adult presentation of the Dandy-Walker syndrome is extremely rare. We report a case where the patient was first diagnosed at 75 years of age because of sudden onset of unilateral senorineural deafness and episodic vertigo. He remained well for a further three years until developing the more classical adult presenting features of cognitive impairment, disordered gait and ataxia. The radiological and otological investigative findings are discussed, together with their implications.
Freeman
S R M
SR
Department of Otorhinolaryngology, South Manchester University Hospitals Trust, Manchester, UK.
Jones
P H
PH
D000368:Aged; D001301:Audiometry, Pure-Tone; D003616:Dandy-Walker Syndrome / Q000150:complications* / Q000175:diagnosis; D016057:Evoked Potentials, Auditory, Brain Stem; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology*; D003639:Hearing Loss, Sudden / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D014057:Tomography, X-Ray Computed / Q000379:methods; D014717:Vertigo / Q000175:diagnosis / Q000209:etiology*