Disabling pansclerotic morphea of childhood and hypogammaglobulinemia: a curious association.
This communication describes a 1.5-year-old girl who presented with multiple episodes of infection since early infancy and stiffening of limbs for 2 months. Biopsy of the involved areas showed features consistent with pansclerotic morphea. Immunoglobulin estimation revealed hypogammaglobulinemia. This unique combination of pansclerotic morphea with hypogammaglobulinemia has not been reported before.
Devidayal
Department of Pediatrics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Singh
S
S
Kumar
L
L
Radotra
B D
BD
D000361:Agammaglobulinemia / Q000150:complications* / Q000175:diagnosis; D001707:Biopsy, Needle; D002675:Child, Preschool; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018570:Risk Assessment; D012594:Scleroderma, Localized / Q000150:complications* / Q000175:diagnosis / Q000473:pathology*; D012720:Severity of Illness Index