title: Congenital conductive hearing loss.
abstract: Congenital conductive hearing loss due to ossicular deformities can be treated by either rehabilitation with a hearing aid or surgical reconstruction. We present the results of exploratory tympanotomy performed in a large paediatric otolaryngology centre in 67 patients with non-serous congenital conductive hearing loss. Forty-two children had malformation of one or more ossicles without fixation of the stapes, and 19 had fixed stapes. In 26 cases, the surgeon decided not to perform surgical correction. Seven operated patients were lost to follow-up. As a group, 47 per cent of the patients who underwent reconstruction showed no significant benefit from surgery, with post-operative air-bone gaps (ABG) greater than 30 dB. Assessment of the results by pathology showed that 64 per cent of the patients with mobile stapes had an air-bone gap within 30 dB compared to only 33 per cent of the patients with fixed stapes. One patient sustained severe sensorineural loss after the procedure. Considering that exploratory tympanotomy is a relatively minimal, benign procedure but that findings during exploration may exclude the option of reconstruction (in 39 per cent of our patients), we suggest exploring the ear, but in a more realistic, informed way.
authors.affiliation: Departments of Otolaryngology, The Hospital for Sick Children, Toronto, Canada. eraveh@netvision.net.il
authors.forename: Eyal
authors.initials: E
authors.lastname: Raveh
authors.forename: Weili
authors.initials: W
authors.lastname: Hu
authors.forename: Blake Croll
authors.initials: BC
authors.lastname: Papsin
authors.forename: Vito
authors.initials: V
authors.lastname: Forte
mesh_terms: D000293:Adolescent; D001301:Audiometry, Pure-Tone; D002648:Child; D004432:Ear, Middle / Q000002:abnormalities*; D005500:Follow-Up Studies; D006314:Hearing Loss, Conductive / Q000151:congenital / Q000601:surgery*; D006801:Humans; D009998:Ossicular Prosthesis; D019933:Ossicular Replacement / Q000379:methods; D013200:Stapes Mobilization / Q000379:methods*; D016896:Treatment Outcome; D014433:Tympanoplasty / Q000379:methods*