Resolution of secondary pulmonary arteriovenous malformations after embolization of a congenital superior-mesenteric-vein-to-left-renal-vein shunt.
A 7-year-old boy who presented with cyanosis and exercise intolerance was diagnosed with pulmonary arteriovenous malformations (PAVMs) secondary to a congenital superior-mesenteric-vein-to-left-renal-vein (SMV-LRV) shunt. Resolution of the PAVMs (confirmed by chest computed tomography [CT]) occurred after embolization of this shunt. Although the pathogenesis of his PAVM is not well known, this case demonstrated a close relationship between a congenital SMV-LRV shunt and the development of PAVM.
Chiu
Shuenn-Nan
SN
Department of Pediatrics, National Taiwan University Hospital, No. 7 Chung-Shan S. Road, Taipei, Taiwan.
Ni
Yen-Hsuan
YH
Wang
Jou-Kou
JK
Lee
Yung-Chie
YC
Lee
Meng-Luen
ML
Tsang
Yuk-Ming
YM
Chen
Shyh-Jye
SJ
D001165:Arteriovenous Malformations / Q000000981:diagnostic imaging / Q000378:metabolism / Q000628:therapy*; D002648:Child; D004621:Embolization, Therapeutic / Q000379:methods*; D019332:Endothelin-1 / Q000378:metabolism; D006801:Humans; D008297:Male; D008642:Mesenteric Veins / Q000002:abnormalities*; D011651:Pulmonary Artery / Q000002:abnormalities*; D011859:Radiography; D012082:Renal Veins / Q000002:abnormalities*
D019332:Endothelin-1