title: Tracheobronchial stent insertions in the management of major airway obstruction in a patient with Hunter syndrome (type-II mucopolysaccharidosis).
abstract: We report a case of a 22-year-old male with Hunter syndrome who developed progressive major airway obstruction and was treated with insertion of plastic and metallic stents, with dramatic improvement in the patient's symptomatic and functional status. To the best of our knowledge, this is the first reported case of endoluminal stents being used in the management of major airway obstruction in a patient with Hunter syndrome.
authors.affiliation: Department of Radiology, Guy's and St. Thomas' Hospitals, St. Thomas' Street, London SE1 9RT, UK.
authors.forename: S M
authors.initials: SM
authors.lastname: Davitt
authors.forename: A
authors.initials: A
authors.lastname: Hatrick
authors.forename: T
authors.initials: T
authors.lastname: Sabharwal
authors.forename: A
authors.initials: A
authors.lastname: Pearce
authors.forename: M
authors.initials: M
authors.lastname: Gleeson
authors.forename: A
authors.initials: A
authors.lastname: Adam
mesh_terms: D000328:Adult; D002404:Catheterization; D006801:Humans; D008173:Lung Diseases, Obstructive / Q000209:etiology* / Q000628:therapy*; D008297:Male; D016532:Mucopolysaccharidosis II / Q000150:complications*; D012008:Recurrence; D015607:Stents; D014135:Tracheal Stenosis / Q000209:etiology / Q000628:therapy