Spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome.
OBJECTIVE
To describe a case of spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome, a disorder characterized by vascular fragility and associated severe bleeding problems.


METHODS
Observational case report. Spontaneous unilateral retrobulbar hemorrhage in a 22-year-old man with type IV Ehlers-Danlos syndrome was documented by clinical and radiographic examination.


RESULTS
The retrobulbar hemorrhage was self-limited and resolved without visual sequelae.


CONCLUSIONS
Spontaneous retrobulbar hemorrhage should be recognized as part of the spectrum of type IV Ehlers-Danlos syndrome, and clinicians must be alert to diagnosis and treatment of this vision-threatening problem.
Shaikh
Saad
S
William Beaumont Hospital, Royal Oak, Michigan 48073, USA. saads@earthlink.net
Braun
Maria
M
Eliason
Joseph
J
D000328:Adult; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D019315:Retrobulbar Hemorrhage / Q000000981:diagnostic imaging / Q000209:etiology*; D014057:Tomography, X-Ray Computed