title: Atypical pityriasis rubra pilaris associated with arthropathy and osteoporosis: a case report with 15-year follow-up.
abstract: Pityriasis rubra pilaris (PRP) is an idiopathic papulosquamous disease that clinically presents with palmoplantar keratoderma and follicular hyperkeratotic papules that coalesce into scaly erythematous plaques. We report a unique case of atypical PRP beginning at 1 year of age with associated severe arthropathy and osteoporosis. We further discuss the clinical and histopathologic aspects of PRP, its possible etiology, and other associated conditions.
authors.affiliation: Section of Dermatology, University of Arizona College of Medicine, Tucson, Arizona, USA. fbehr@u.arizona.edu
authors.forename: Fiona D
authors.initials: FD
authors.lastname: Behr
authors.forename: Jerry L
authors.initials: JL
authors.lastname: Bangert
authors.forename: Ronald C
authors.initials: RC
authors.lastname: Hansen
mesh_terms: D001168:Arthritis / Q000150:complications* / Q000000981:diagnostic imaging; D002648:Child; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000150:complications; D008297:Male; D010014:Osteolysis / Q000150:complications; D010024:Osteoporosis / Q000150:complications* / Q000000981:diagnostic imaging; D010916:Pityriasis Rubra Pilaris / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D011859:Radiography; D012867:Skin / Q000473:pathology