Resolution of electrical storms after discontinuation of ICD therapy in a child with long QT syndrome.
We report a case of a child with familial long QT syndrome (Jervell Lange-Nielsen) who had multiple electrical storms in the presence of b blocker and implantable cardioverter device (ICD) therapy. Discontinuation of ICD therapy and addition of oral amiodarone to b blockade therapy resulted in freedom from electrical storms.
Shah
M J
MJ
The Institute of Cardiovascular Diseases, Madras Medical Mission, Madras, India.
Rhodes
L A
LA
D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D000638:Amiodarone / Q000627:therapeutic use; D000889:Anti-Arrhythmia Agents / Q000627:therapeutic use; D002675:Child, Preschool; D017147:Defibrillators, Implantable; D006801:Humans; D029593:Jervell-Lange Nielsen Syndrome / Q000503:physiopathology* / Q000628:therapy; D008297:Male
D000319:Adrenergic beta-Antagonists; D000889:Anti-Arrhythmia Agents; D000638:Amiodarone