title: Primary monotypic epithelioid angiomyolipoma of bone.
abstract: OBJECTIVE
  Monotypic epithelioid angiomyolipoma is a distinct and definable variant of angiomyolipoma, composed of monomorphous epithelioid cells that show HMB45 immunoreactivity. Angiomyolipoma, including its morphological variants, belongs to the family of perivascular epithelioid cell tumour.
  
  
  RESULTS
  The tumour was examined using immunohistochemical staining and by transmission electron microscopy. Neoplastic cells showed a cytoplasmic granular positivity for HMB45.
  
  
  CONCLUSIONS
  Extrarenal angiomyolipomas are rare and, to the best of our knowledge, this is the first reported case of a primary monotypic epithelioid angiomyolipoma of bone in a patient without evidence of tuberous sclerosis.
authors.affiliation: Dipartimento di Anatomia Patologica, Facoltà di Medicina, Università Federico II, Napoli, Italy. insabato@unina.it
authors.forename: L
authors.initials: L
authors.lastname: Insabato
authors.forename: G
authors.initials: G
authors.lastname: De Rosa
authors.forename: L M
authors.initials: LM
authors.lastname: Terracciano
authors.forename: F
authors.initials: F
authors.lastname: Fazioli
authors.forename: F
authors.initials: F
authors.lastname: Di Santo
authors.forename: J
authors.initials: J
authors.lastname: Rosai
mesh_terms: D000328:Adult; D018207:Angiomyolipoma / Q000378:metabolism / Q000473:pathology*; D000951:Antigens, Neoplasm; D001859:Bone Neoplasms / Q000378:metabolism / Q000473:pathology*; D015622:Epithelioid Cells / Q000737:chemistry / Q000473:pathology*; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins / Q000032:analysis
chemical_list: D000951:Antigens, Neoplasm; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins