[Arnold-Chiari II malformation and basilar impression. Report of one case (a literature review)].
OBJECTIVE
To tell the rare association of Arnold-Chiari II malformation and basilar impression and to describe an exceptional clinical state with a particular surgical approach.


METHODS
To analyse a case of a patient suffering from this congenital malformation, her progressive clinical state, the surgical approach.


RESULTS
N.G. a 42-year-old woman, suffers from a cerebello-spino-medullar disturbance responsible for a major dependence and respiratory insufficiency with a risk of death. The results of the surgical treatment meant to decompress the craniovertebral junction are exceptional.


CONCLUSIONS
The analysis of the literature show the special feature of this case as much for the rarity of the diagnosis as for the progressive clinical state and the remarkable post operative result.


CONCLUSIONS
The association of these two malformations is seldom alluded to in the literature and such a post operative result has apparently never been described. In addition, this case tends to prove that a second operation's worth considering if the first has shown its short-fall whichever the patient's clinical state.
Thiébaut
M
M
service de médecine physique et réadaptation fonctionnelle, hôpital Morvan, 5, avenue Foch, 29609, Brest, France.
Le Bigot
P
P
Besson
G
G
Dorval
M P
MP
Martin
C
C
D000328:Adult; D001139:Arnold-Chiari Malformation / Q000150:complications* / Q000601:surgery; D015897:Comorbidity; D016757:Death, Sudden, Cardiac; D018450:Disease Progression; D005260:Female; D006801:Humans; D010985:Platybasia / Q000150:complications* / Q000601:surgery; D012131:Respiratory Insufficiency / Q000209:etiology; D012307:Risk Factors; D016896:Treatment Outcome