title: [Contribution of imaging to the diagnosis of Darier-Ferrand's cranio-facial dermatofibrosarcoma. Report of 2 cases].
abstract: Dermatofibrosarcoma protubans of Darier-Ferrand is observed in about 0.1% of al malignant skin tumors. Head and face localization in uncommon, estimated to account for about 1 to 10% of all lesions. Relapse is frequent and metastasis in uncommon. Diagnosis is often made late. Surgery is the basic treatment. We report two cases of dermatofibrosarcoma of Darier-Ferrand with head and face localizations. In one case, the tumor extended inside the skull and spread to the superior longitudinal sinus. This is the only such reported case found in the literature. CT scan is more useful for studying the bony tables and the cranial content. MRI provides precision for soft tissue tumors and angio-MRI is particularly useful for analysing with accuracy vascular relations of the tumor.
authors.affiliation: Service de Neuroradiologie, Hôpital des spécialités, Rabat, Maroc.
authors.forename: A
authors.initials: A
authors.lastname: Taleb
authors.forename: K
authors.initials: K
authors.lastname: Fahoume
authors.forename: A
authors.initials: A
authors.lastname: Hommadi
authors.forename: N
authors.initials: N
authors.lastname: Chakir
authors.forename: M
authors.initials: M
authors.lastname: Jiddane
mesh_terms: D000328:Adult; D000368:Aged; D018223:Dermatofibrosarcoma / Q000175:diagnosis*; D005153:Facial Neoplasms / Q000175:diagnosis*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis*; D012878:Skin Neoplasms / Q000175:diagnosis*; D012888:Skull Neoplasms / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed
vernacular_title: Apport de l'imagerie dans le diagnostic du dermatofibrosarcome crânio-facial de darier-ferrand. A propos de deux observations.