title: [Hereditary intermittent fevers, other than familial Mediterranean fevers].
abstract: Familial Mediterranean fever is no more the sole hereditary disease characterized by recurrent inflammatory attacks. Three other main entities have now been defined, both at clinical and genetic levels: a dominant disease due to mutations of one of the tumour necrosis factor receptor, called TRAPS for tumour necrosis factor receptor associated periodic syndrome, the hyper-immuno-globulinaemia D and periodic fever syndrome (HIDS), which is a metabolic disorder and the Muckle-Wells syndrome. A thorough diagnosis of these diseases is crucial for appropriate management and treatment.
authors.affiliation: Service de médecine interne L'Hôtel-Dieu 75181 Paris. gilles.grateau@htd.ap-hop-paris.fr
authors.forename: Gilles
authors.initials: G
authors.lastname: Grateau
authors.forename: Laurence
authors.initials: L
authors.lastname: Cuisset
authors.forename: Catherine
authors.initials: C
authors.lastname: Dodé
authors.forename: Marc
authors.initials: M
authors.lastname: Delpech
mesh_terms: D003937:Diagnosis, Differential; D005334:Fever / Q000209:etiology / Q000235:genetics* / Q000473:pathology; D006801:Humans; D007072:Immunoglobulin D; D007249:Inflammation; D010507:Periodicity; D011379:Prognosis; D018124:Receptors, Tumor Necrosis Factor / Q000235:genetics*; D013577:Syndrome
chemical_list: D007072:Immunoglobulin D; D018124:Receptors, Tumor Necrosis Factor
vernacular_title: Fièvres intermittentes héréditaires, autres que la fièvre méditerranéenne familiale.