Total deficiency of specific von Willebrand factor-cleaving protease and recovery following plasma therapy in one patient with hemolytic-uremic syndrome.
Veyradier
A
A
Brivet
F
F
Wolf
M
M
Boyer-Neumann
C
C
Obert
B
B
Girma
J P
JP
Meyer
D
D
D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; D000328:Adult; D001803:Blood Transfusion; D005260:Female; D006463:Hemolytic-Uremic Syndrome / Q000175:diagnosis / Q000201:enzymology* / Q000628:therapy*; D006801:Humans; D008666:Metalloendopeptidases / Q000172:deficiency*; D010949:Plasma / Q000201:enzymology
D051722:ADAM Proteins; D008666:Metalloendopeptidases; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human