[Syndromes 6. Crouzon's disease].
Morbus Crouzon is a syndrome with craniosynostosis. Besides a deviating form of the skull this causes a retropositioned middle third of the face. Therefore pseudo-exophthalmos, strabismus and an Angle Class III relation of the jaws are usually seen. The eyes are especially vulnerable. Since the symptoms are rather symmetrical, a good result of the corrections can usually be achieved. The form of the skull will be corrected in very early childhood, while the deformities of the face are by preference operated after completion of growth. However, different reasons can be found to start correction in an earlier stage.
Freihofer
H P
HP
Afdeling Mond- en Kaakchirurgie, Academisch Ziekenhuis Nijmegen, postbus 9101, 6500 HB Nijmegen.
D003394:Craniofacial Dysostosis / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D003398:Craniosynostoses / Q000473:pathology*; D003937:Diagnosis, Differential; D006801:Humans; D008313:Malocclusion, Angle Class III / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D012886:Skull / Q000473:pathology; D013577:Syndrome
Syndromen 6. Morbus Crouzon.