[Syndromes 12. Turner syndrome].
Turner syndrome is one of the most common chromosomal disorders. The incidence is about 1 on 2,500 till 1 on 10,000 living female young births. Short stature is the most common finding in patients with Turner syndrome. Besides short stature and gonadal dysgenesis, typical craniofacial and dental features are also present. Disturbance of the enchondral ossification results in abnormal craniofacial morphology. Oestrogen medication, to induce their puberty, and recombinant human growth therapy, to improve final height of these patients, are the most common treatment possibilities. It is the intention of this short paper to inform the dentist/orthodontist about the general aspects of the Turner syndrome. This information can be used in their treatment plan.
Verdonck
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Afdeling Orthodontie, School voor Tandheelkunde, Mondziekten en Kaakchirurgie, Katholieke Universiteit te Leuven, België.
van Erum
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D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D019465:Craniofacial Abnormalities / Q000209:etiology*; D019140:Dental Care for Children; D003937:Diagnosis, Differential; D005260:Female; D006059:Gonadal Dysgenesis / Q000209:etiology; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D009426:Netherlands / Q000453:epidemiology; D010347:Patient Care Planning; D014424:Turner Syndrome / Q000175:diagnosis* / Q000453:epidemiology / Q000473:pathology / Q000628:therapy
Syndromen 12. Het Turner-syndroom.