[Obstructive esophageal membrane in recessive dystrophic epidermolysis bullosa].
BACKGROUND
Dysphagia is a rare complication of esophageal webs.


OBJECTIVE
To describe a patient with dystrophic epidermolysis bullosa who developed dysphagia produced by an esophageal web that simulated carcinoma.


METHODS
A 26 year-old male with dystrophic epidermolysis bullosa developed severe dysphagia and subsequently aphagia secondary to an upper third esophageal obstruction. A (CT) scan showed a circumferential esophageal wall thickening of the affected area. The patient was submitted to surgical neck exploration with endoscopic assistance to identify the obstruction and a esophagotomy was carried on detecting a complete esophageal web that was excised.


CONCLUSIONS
Esophageal web must be considered a cause of esophageal obstruction in patients with dystrophic epidermolysis bullosa.
Ruíz-Molina
J M
JM
Departamento de Gastroenterología, División de Cirugía Oncológica, Instituto Nacional de Cancerología (México), Av. San Fernando No. 22, CP 14000, Delegación Tlalpan, México, DF.
Ortíz-Mendoza
C M
CM
D000328:Adult; D003937:Diagnosis, Differential; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications*; D004938:Esophageal Neoplasms / Q000175:diagnosis; D004940:Esophageal Stenosis / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008297:Male
Membrana esofágica obstructiva en epidermólisis ampollosa distrófica recesiva.