[Syndromes 9. Hemifacial microsomia].
Hemifacial microsomia is also known under quite a number of synonyms. Pathognomonic for these usually sporadic cases are: marked three dimensional asymmetry of the mandible, the ear, the maxilla, the zygoma and the orbit. The more distal the structure, the more marked the asymmetry. Many other optional symptoms are described. The differential diagnosis is almost never a problem in this aspecific complex of symptoms. Surgical therapy asks for expert treatment. The treatment contains usually several operations of which one to three are really major. Even then, very good results are mainly obtained in the less pronounced cases only.
Freihofer
H P
HP
Afdeling Mond- en kaakchirurgie, Academisch Ziekenhuis Nijmegen, Postbus 9101, 6500 HB Nijmegen.
D002508:Cephalometry; D003937:Diagnosis, Differential; D004413:Dysostoses / Q000175:diagnosis* / Q000601:surgery; D005145:Face / Q000033:anatomy & histology*; D005146:Facial Asymmetry / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D008334:Mandible / Q000002:abnormalities / Q000601:surgery; D013577:Syndrome; D015050:Zygoma / Q000002:abnormalities / Q000601:surgery
Syndromen 9. Dysostosis otomandibularis.