Cardiac amyloidosis: a case report and therapeutic implications.
Primary amyloidosis with cardiac involvement presenting as congestive heart failure (CHF) usually carries an unfavorable prognosis, with median survival of about 6 months. We are reporting a case of cardiac amyloidosis with an initial presentation of CHF in which the patient survived for more than 9 years. The prognosis most likely depends on the period of disease remission (i.e., negative serum and urine immunoelectrophoresis), which, in turn, depends on response to chemotherapy.
Kotha
Anu Radha
AR
Division of Cardiology, New York Medical College/Westchester Medical Center, Valhalla, New York 10595, USA.
Weiss
Melvin B
MB
D000686:Amyloidosis / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D003937:Diagnosis, Differential; D018450:Disease Progression; D004452:Echocardiography; D006331:Heart Diseases / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D006333:Heart Failure / Q000378:metabolism / Q000628:therapy; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000209:etiology / Q000378:metabolism / Q000628:therapy; D008297:Male; D008875:Middle Aged