[Bilateral exophthalmos diabetes insipidus: Erdheim-Chester disease. Clinical and radiological findings].
The authors report a case of a 61-year-old man presenting bilateral exophthalmos and diabetes insipidus. A retro-orbital biopsy revealed nonspecific fibrocollagenic infiltration. The diagnosis of Erdheim-Chester disease was evoked when a multivisceral affection (retroperitoneal and mediastinal periaortic fibrosis) with specific bone localization became evident. The histopatholgical study of a bone biopsy showed xanthogranulomatous infiltration. The patient died a few months later of an intercurrent infection.
Le Goff
L
L
Service d'Ophtalmologie de Marseille, CHU Timone, 264, rue Saint-Pierre, 13385 Marseille, France.
Berros
P
P
Denis
D
D
Ridings
B
B
D003919:Diabetes Insipidus / Q000150:complications*; D031249:Erdheim-Chester Disease / Q000150:complications*; D005094:Exophthalmos / Q000150:complications*; D006801:Humans; D008297:Male; D008875:Middle Aged