Living related kidney transplantation in a 15-year-old patient with type I hyperoxaluria: a case report.
The following is a case report of a patient with type I hyperoxaluria who received a living related renal transplant for end-stage renal disease. The deficiency or complete absence of the hepatic enzyme alanine glyoxalate aminotransferase characterizes type I hyperoxaluria. When deficient, an overproduction of oxalate occurs, which then can be deposited in multiple end-organ systems. When performing surgery on a patient with type I hyperoxaluria, the anesthetist needs to be aware that these patients can have a host of problems ranging from cardiovascular anomalies to end-stage renal disease. A careful assessment of each system needs to be performed, along with vigilant planning of the anesthetic regimen. Through proper planning and implementation, a safe and effective anesthetic usually can be performed.
Weir
Jeffrey W
JW
Western Pennsylvania Hospital, Pittsburgh, Pa., USA.
Ciancione
Jerry
J
O'Donnell
John
J
D000293:Adolescent; D006801:Humans; D006960:Hyperoxaluria, Primary / Q000601:surgery*; D016030:Kidney Transplantation; D019520:Living Donors; D008297:Male; D009719:Nurse Anesthetists