Serum hyperviscosity syndrome responding to therapeutic plasmapheresis in a patient with primary Sjögren's syndrome.
Hyperviscosity syndrome is a disorder first described in patients with Waldenström's macroglobulinemia and is not commonly seen in rheumatic diseases. Its association with Sjögren's syndrome is very rare and it has been reported in very few patients. We report the case of a patient with primary Sjögren's syndrome presenting as hyperviscosity syndrome who was successfully treated with therapeutic plasma exchange.
Simón
J Abraham
JA
Department of Immunology and Rheumatology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Vasco de Quiroga 15, Tlalpan 14000, Mexico City, DF, Mexico.
Lazo-Langner
Alejandro
A
Duarte-Rojo
Andrés
A
Velázquez-González
Antonio
A
Sánchez-Guerrero
Sergio A
SA
Sánchez-Guerrero
Jorge
J
D000328:Adult; D001323:Autoantibodies / Q000097:blood; D001327:Autoimmune Diseases / Q000097:blood*; D001809:Blood Viscosity; D005260:Female; D006801:Humans; D010951:Plasma Exchange; D012859:Sjogren's Syndrome / Q000097:blood*; D013577:Syndrome
D001323:Autoantibodies