Successful laparoscopic operation of bilateral pheochromocytoma in a patient with Beckwith-Wiedemann syndrome.
We report the case of a 20-year-old female patient with Beckwith-Wiedemann syndrome presenting with high blood pressure and bilateral adrenal pheochromocytoma successfully removed with laparoscopy in the same time. To our knowledge, the present case is the first observation of a bilateral pheochromocytoma occurring in the Beckwith-Wiedemann syndrome. It provides further support for a genetic anomaly in this condition. Our case also indicates the interest of laparoscopy for the surgical treatment of adrenal pheochromocytoma, even in bilateral tumors.
Bémurat
L
L
Hôpital Saint André, service de Cardiologie/Hypertension artérielle, Bordeaux, France.
Gosse
P
P
Ballanger
P
P
Tauzin-Fin
P
P
Barat
P
P
Lacombe
D
D
Lemétayer
P
P
Clémenty
J
J
D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000473:pathology / Q000601:surgery*; D000328:Adult; D001506:Beckwith-Wiedemann Syndrome / Q000150:complications* / Q000473:pathology / Q000601:surgery*; D005260:Female; D006801:Humans; D010535:Laparoscopy; D010673:Pheochromocytoma / Q000150:complications* / Q000473:pathology / Q000601:surgery*