[Cardiorespiratory system in adult patients with mucoviscidosis].
OBJECTIVE
To study cardiorespiratory system in adult patients with mucoviscedosis.


METHODS
External respiration function, echocardiographic and dopplercardiographic evidence were analysed for 22 patients with mucoviscedosis.


RESULTS
66.7% examinees had mixed pulmonary ventilation disorders, 46% were found to have low diffuse capacity of the lungs correlating in degree with ventilatory abnormalities. Dilated right heart and high systolic pressure in the pulmonary artery were registered in 14% patients with marked obstruction. Left ventricular systolic and diastolic defects occurred in 23%.


CONCLUSIONS
Adult patients with mucoviscedosis have mixed disorders of pulmonary ventilation, high pressure in pulmonary circulation and developing pulmonary heart in patients with severe obstruction.
Naumenko
Zh K
ZhK
Nekliudova
G V
GV
Cherniak
A V
AV
Amelina
E L
EL
Kalmanova
E N
EN
Chuchalin
A G
AG
D000293:Adolescent; D000328:Adult; D003550:Cystic Fibrosis / Q000000981:diagnostic imaging / Q000503:physiopathology*; D015150:Echocardiography, Doppler; D006321:Heart / Q000503:physiopathology*; D006801:Humans; D012129:Respiratory Function Tests; D012137:Respiratory System / Q000503:physiopathology*