Rasmussen syndrome of chronic focal encephalitis.
Rasmussen syndrome of chronic focal encephalitis is a relatively rare disease, which presents with epilepsia partialis continua and hemiparesis in childhood. Though first described in the 1950s it still remains somewhat of an enigma. The immunological process involved in its pathogenesis is better understood now but the exact relationship to viral infections is still unclear. Medical treatment remains disappointing while results of surgical treatment are mixed. There are emerging insights into the disease, which are reviewed and a case study of a patient with Rasmussen syndrome is presented.
Gosalakkal
Jayaprakash Ayillath
JA
Department of Pediatric Neurology, NYU School of Medicine, New York, USA.
D001921:Brain / Q000276:immunology / Q000601:surgery / Q000821:virology; D002675:Child, Preschool; D003072:Cognition Disorders / Q000175:diagnosis; D004660:Encephalitis / Q000175:diagnosis* / Q000276:immunology / Q000601:surgery / Q000821:virology; D007839:Functional Laterality / Q000502:physiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D019635:Neurosurgical Procedures; D016133:Polymerase Chain Reaction; D018091:Receptors, AMPA / Q000276:immunology; D013064:Speech Disorders / Q000175:diagnosis
D018091:Receptors, AMPA; C104723:glutamate receptor ionotropic, AMPA 3