title: Congenital lobar emphysema: Like father, like son.
abstract: Congenital lobar emphysema (CLE) is an uncommon cause of progressive respiratory distress that typically presents in the first few days of life. There has been a previous report of CLE in a mother and daughter. The authors describe 2 cases involving the right upper and middle lobes in a father and son secondary to relative deficiency of the bronchial cartilage. This provides additional evidence for inherited factors in the etiology of CLE.
authors: Sydney, New South Wales, Australia.
authors: P A
authors: PA
authors: Roberts
authors: A J A
authors: AJ
authors: Holland
authors: R J
authors: RJ
authors: Halliday
authors: S M
authors: SM
authors: Arbuckle
authors: D T
authors: DT
authors: Cass
mesh_terms: D000328:Adult; D001980:Bronchi / Q000473:pathology; D002356:Cartilage / Q000002:abnormalities* / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011656:Pulmonary Emphysema / Q000151:congenital* / Q000000981:diagnostic imaging / Q000235:genetics* / Q000601:surgery; D011859:Radiography