Primary rhabdomyosarcoma of the diaphragm: case report and literature review.
The authors report a case of primary rhabdomyosarcoma of the diaphragm, an extremely rare presentation with only 14 cases reported in the literature. An 18-year-old male presented 2 spontaneous occurrences of pneumothorax. Computed tomography and magnetic resonance showed a tumoral mass on the right diaphragmatic surface, and after biopsy, the diagnosis was compatible with spindle cell rhabdomyosarcoma. Because the visceral pleura was invaded by the tumoral mass, a right pleuropneumonectomy was performed. The patient received adjuvant chemotherapy, and there was no evidence of disease 15 months after the operation. Based on the Intergroup Rhabdomyosarcoma Study Group (IRSG) criteria, which consider the extent of the disease and its surgical resectability, rhabdomyosarcomas can be classified into 4 groups. In clinical group I, which was the classification of our patient, the tumor is localized and completely resectable, which implies a good prognosis. Rhabdomyosarcoma is a rare tumor, and a good outcome may result if it is completely resected.
Medeiros
Cleverson Winston de Liz
CW
Hospital Nossa Senhora das Graças, Curitiba, Paraná.
Kondo
William
W
Baptista
Ivo
I
Vizzotto
Alvo Orlando
AO
Noronha
Lúcia de
Ld
Hakim Neto
Calixto Antonio
CA
D000293:Adolescent; D017024:Chemotherapy, Adjuvant; D003964:Diaphragm; D006801:Humans; D009682:Magnetic Resonance Spectroscopy; D008297:Male; D019042:Muscle Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery; D018233:Rhabdomyosarcoma, Embryonal / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery; D014057:Tomography, X-Ray Computed