Pulmonary atresia with intact ventricular septum and systemic-pulmonary collateral arteries.
Pulmonary atresia with intact ventricular septum and major systemic-pulmonary collateral arteries is a very rare congenital heart lesion with dismal natural history. Herein we report on a case of pulmonary atresia with intact ventricular septum with hypoplastic right ventricle, very small confluent pulmonary arteries, absent arterial duct, and pulmonary blood flow exclusively provided by bronchial-type systemic-pulmonary collateral arteries that was successfully treated at our institution.
Albanese
Sonia B
SB
Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Hospital, Rome, Italy. albanese@opbg.net
Carotti
Adriano
A
Toscano
Alessandra
A
Marino
Bruno
B
Di Donato
Roberto M
RM
D000714:Anastomosis, Surgical; D001011:Aorta / Q000002:abnormalities / Q000601:surgery; D003097:Collateral Circulation; D006346:Heart Septum / Q000473:pathology*; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D018633:Pulmonary Atresia / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D011652:Pulmonary Circulation; D011859:Radiography