title: [Anesthetic management of a child with dilated cardiomyopathy associated with congenital fiber-type disproportion].
abstract: A 3-year-old girl, who presented with dilated cardiomyopathy in conjunction with congenital fiber-type disproportion, underwent open reduction for congenital dislocation of the hip. Preoperative echocardiography demonstrated left ventricular dilatation with an ejection fraction (EF) of 0.33. Anesthesia was induced with intravenous ketamine and fentanyl, and maintained with fentanyl administered incrementally to a total dose of 10 micrograms.kg-1 and 1-1.5% isoflurane. During operation, we continuously monitored left ventricular wall motion and measured left ventricular diastolic dimension (LVDd), systolic dimension (LVDs), cardiac output (CO), EF, and fractional shortening (FS) with transesophageal echocardiography (TEE). At the end of surgery, preload (LVDd) and LV contractility (CO, EF, FS) decreased, but LV wall motion remained almost stable throughout the procedure. In conclusion, TEE was useful for intraoperative management of a child with dilated cardiomyopathy.
authors: Department of Anesthesiology, Osaka Medical Center and Research Institute for Maternal and Child Health, Izumi 594-1101.
authors: Yoshitaka
authors: Y
authors: Kawaraguchi
authors: Akihiro
authors: A
authors: Taniguchi
authors: Kazuo
authors: K
authors: Fukumitsu
authors: Keiko
authors: K
authors: Kinouchi
authors: Yoshikazu
authors: Y
authors: Miyamoto
authors: Osamu
authors: O
authors: Hirao
authors: Seiji
authors: S
authors: Kitamura
mesh_terms: D000758:Anesthesia / Q000379:methods*; D002311:Cardiomyopathy, Dilated / Q000150:complications* / Q000000981:diagnostic imaging; D002675:Child, Preschool; D017548:Echocardiography, Transesophageal; D005260:Female; D006618:Hip Dislocation, Congenital / Q000601:surgery*; D006801:Humans; D018485:Muscle Fibers, Skeletal / Q000473:pathology; D009135:Muscular Diseases / Q000151:congenital* / Q000473:pathology