[Benign myoclonic epilepsy in infant].
OBJECTIVE
To review the concept of benign myoclonic epilepsy of infancy in the literature as compared with our series of patients.


METHODS
We review the literature and describe seven personal patients, three males and four females, diagnosed with benign myoclonic epilepsy of infancy according to Dravet's criteria.


RESULTS
Six of the seven patients were followed along 6 26 years, three of whom showed an unfavourable evolution of their intellectual and behavioral development. Three of the seven patients, not necessarily the same just mentioned, presented with generalized seizures later during their follow up: tonic clonic in one, Petit Mal status in another, and absences with marked eyelid myoclonia in the third. Four of the seven patients showed well defined eyelid myoclonias simultaneously occurring with the arms and head myoclonic seizures at the beginning of the illness, without inferring a prognostic value of their intellectual development or their response to antiepileptic treatment.
Prats-Viñas
J M
JM
Unidad de Neuropediatría; Hospital de Cruces, Barakaldo, 48903, Espana. med002206@nacom.es
Garaizar
C
C
Ruiz-Espinoza
C
C
D000927:Anticonvulsants / Q000627:therapeutic use; D002675:Child, Preschool; D004569:Electroencephalography; D004831:Epilepsies, Myoclonic / Q000175:diagnosis / Q000188:drug therapy / Q000453:epidemiology*; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D012720:Severity of Illness Index
D000927:Anticonvulsants