title: Solitary fibrous tumor of the orbit presenting 20 years after Hodgkin's disease.
abstract: A 54-year-old white male patient presented with a painless, slowly progressive proptosis and downward displacement of his right eye. He had been treated for Hodgkin's disease 20 years earlier. MRI revealed a well-circumscribed retro- and suprabulbar mass measuring 24 mm in its maximal diameter. The mass was isointense with brain on T1-weighted images, displayed a low signal on T2-weighted images and showed postcontrast enhancement. The tumor was removed in its entirety via an anterior orbitotomy. Histopathologic, immunohistochemical and ultrastructural studies revealed a solitary fibrous tumor. Both immunohistochemical and electron microscopic findings were essential in differentiating this entity from other similar soft-tissue lesions. Only 11 other cases of orbital solitary fibrous tumor have been reported in the literature. To our knowledge, this is the first one presenting after Hodgkin's disease.
authors.affiliation: Department of Ophthalmology & Eye Hospital, University of Erlangen-Nürnberg, Germany. leonard.holbach@augen.imed.unierlangen.de
authors.forename: Leonard M
authors.initials: LM
authors.lastname: Holbach
authors.forename: Fernando
authors.initials: F
authors.lastname: Colombo
authors.forename: Ursula
authors.initials: U
authors.lastname: Schlötzer-Schrehardt
authors.forename: Thomas
authors.initials: T
authors.lastname: Kirchner
mesh_terms: D005094:Exophthalmos / Q000209:etiology; D005350:Fibroma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006689:Hodgkin Disease / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D016609:Neoplasms, Second Primary / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery