A 15-year-old boy with central nervous system vasculopathy presenting with dysarthria-clumsy hand syndrome.
Dysarthria-clumsy hand stroke syndrome has been described frequently in adults but not in children. We report a 15-year-old right-handed boy with sudden onset of dysarthria, dysphagia, right facial weakness, and mild right-hand clumsiness. Computed tomographic scan and magnetic resonance imaging demonstrated infarction in the genu and posterior limb of the left internal capsule. Magnetic resonance angiography and conventional angiography demonstrated stenosis of the supraclinoid portion of the left internal carotid artery and the origin of the left ophthalmic artery. Lacunar infarction in an older adult is not the only mechanism leading to dysarthria-clumsy hand syndrome.
Golomb
Meredith R
MR
Department of Pediatrics, The Hospital for Sick Children, Toronto, Ontario, Canada. mgolomb@earthlink.net
Weiss
Shelly K
SK
Ibrahim
Shahnaz H
SH
deVeber
Gabrielle A
GA
D000293:Adolescent; D016893:Carotid Stenosis / Q000150:complications / Q000503:physiopathology; D002544:Cerebral Infarction / Q000150:complications* / Q000503:physiopathology*; D004401:Dysarthria / Q000150:complications* / Q000503:physiopathology*; D006225:Hand / Q000503:physiopathology*; D006801:Humans; D020772:Internal Capsule / Q000098:blood supply / Q000503:physiopathology*; D008297:Male; D011149:Pons / Q000098:blood supply / Q000503:physiopathology*; D013577:Syndrome