title: Anesthetic considerations for a patient with compound heterozygous medium-chain Acyl-CoA dehydrogenase deficiency.
abstract: We describe the anesthetic management of a parturient with compound heterozygous medium chain acyl-CoA dehydrogenase deficiency, the most common disorder of fatty acid metabolism.
authors.affiliation: Department of Anesthesiology, Perioperative and Pain Medicine, Brigham and Women's Hospital, Harvard Medical School, Boston, MA 02115, USA. swgasmac@aol.com
authors.forename: Steven Y
authors.initials: SY
authors.lastname: Wang
authors.forename: Suresh
authors.initials: S
authors.lastname: Kannan
authors.forename: Dennis
authors.initials: D
authors.lastname: Shay
authors.forename: Scott
authors.initials: S
authors.lastname: Segal
authors.forename: Sanjay
authors.initials: S
authors.lastname: Datta
authors.forename: Lawrence
authors.initials: L
authors.lastname: Tsen
mesh_terms: D044944:Acyl-CoA Dehydrogenases / Q000172:deficiency*; D000328:Adult; D000767:Anesthesia, Epidural; D000773:Anesthesia, Obstetrical; D001786:Blood Glucose / Q000378:metabolism; D036861:Delivery, Obstetric; D005260:Female; D006801:Humans; D007751:Labor, Induced; D008052:Lipid Metabolism, Inborn Errors / Q000150:complications*; D011247:Pregnancy
chemical_list: D001786:Blood Glucose; D044944:Acyl-CoA Dehydrogenases