Anesthetic considerations for a patient with compound heterozygous medium-chain Acyl-CoA dehydrogenase deficiency.
We describe the anesthetic management of a parturient with compound heterozygous medium chain acyl-CoA dehydrogenase deficiency, the most common disorder of fatty acid metabolism.
Wang
Steven Y
SY
Department of Anesthesiology, Perioperative and Pain Medicine, Brigham and Women's Hospital, Harvard Medical School, Boston, MA 02115, USA. swgasmac@aol.com
Kannan
Suresh
S
Shay
Dennis
D
Segal
Scott
S
Datta
Sanjay
S
Tsen
Lawrence
L
D044944:Acyl-CoA Dehydrogenases / Q000172:deficiency*; D000328:Adult; D000767:Anesthesia, Epidural; D000773:Anesthesia, Obstetrical; D001786:Blood Glucose / Q000378:metabolism; D036861:Delivery, Obstetric; D005260:Female; D006801:Humans; D007751:Labor, Induced; D008052:Lipid Metabolism, Inborn Errors / Q000150:complications*; D011247:Pregnancy
D001786:Blood Glucose; D044944:Acyl-CoA Dehydrogenases