title: Successful surgical repair of Uhl's anomaly.
abstract: We report a case of Uhl's anomaly in a 5-month-old cyanotic infant who presented with thromboembolic stroke and acute hemiparesis. The patient underwent successfully an initial surgical repair, which included exclusion of the right ventricle by patch closure of the tricuspid valve, atrial septectomy and construction of a bidirectional Glenn shunt. This was followed by successful construction of a total cavopulmonary connection.
authors.affiliation: Maternity & Children Hospital, Jeddah, Saudi Arabia.
authors.forename: Nawal
authors.initials: N
authors.lastname: Azhari
authors.forename: Mervat
authors.initials: M
authors.lastname: Assaqqat
authors.forename: Ziad
authors.initials: Z
authors.lastname: Bulbul
mesh_terms: D006328:Cardiac Catheterization / Q000379:methods; D006348:Cardiac Surgical Procedures / Q000379:methods* / Q000401:mortality; D015150:Echocardiography, Doppler / Q000379:methods; D004562:Electrocardiography; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D008297:Male; D018570:Risk Assessment; D015996:Survival Rate; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome