Solitary fibrous tumor of the orbit presenting 20 years after Hodgkin's disease.
A 54-year-old white male patient presented with a painless, slowly progressive proptosis and downward displacement of his right eye. He had been treated for Hodgkin's disease 20 years earlier. MRI revealed a well-circumscribed retro- and suprabulbar mass measuring 24 mm in its maximal diameter. The mass was isointense with brain on T1-weighted images, displayed a low signal on T2-weighted images and showed postcontrast enhancement. The tumor was removed in its entirety via an anterior orbitotomy. Histopathologic, immunohistochemical and ultrastructural studies revealed a solitary fibrous tumor. Both immunohistochemical and electron microscopic findings were essential in differentiating this entity from other similar soft-tissue lesions. Only 11 other cases of orbital solitary fibrous tumor have been reported in the literature. To our knowledge, this is the first one presenting after Hodgkin's disease.
Holbach
Leonard M
LM
Department of Ophthalmology & Eye Hospital, University of Erlangen-Nürnberg, Germany. leonard.holbach@augen.imed.unierlangen.de
Colombo
Fernando
F
Schlötzer-Schrehardt
Ursula
U
Kirchner
Thomas
T
D005094:Exophthalmos / Q000209:etiology; D005350:Fibroma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006689:Hodgkin Disease / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D016609:Neoplasms, Second Primary / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery