Bilateral orbital involvement in Erdheim-Chester disease.
Erdheim-Chester disease is an idiopathic condition characterized by a xanthogranulomatous process infiltrating the bones, lungs, heart, retroperitoneum and other tissues. This condition is often fatal. Ocular findings are rare. The authors report a case of bilateral xanthelasmas and bilateral massive orbital infiltration in a 61-year-old man with severe retroperitoneal fibrosis, renal and cardiovascular problems. The ophthalmic manifestations and differential diagnosis of this peculiar pathologic condition are discussed.
de Palma
Paolo
P
Department of Ophthalmology, University of Ferrara, Ferrara, Italy
Ravalli
Luca
L
Grisanti
Filippo
F
Rossi
Antonio
A
Marzola
Andrea
A
Nielsen
Ingrid
I