title: Erdheim-Chester disease: a bilateral orbital mass as an indication of systemic disease.
abstract: A case of bilateral orbital mass and xanthelasma of the eyelids is presented. Histology confirmed it to be a form of histiocytosis, possibly an Erdheim-Chester disease. This was further confirmed by the presence of a retroperitoneal mass and hydronephrosis, which resolved with treatment. A review of the literature on and pathological features of this rare fatal disease is presented.
authors.affiliation: Consultant Ophthalmologists, Mount Elizabeth Medical Center, Singapore
authors.forename: Shantha
authors.initials: S
authors.lastname: Amrith
authors.forename: Cze
authors.initials: C
authors.lastname: Hong Low
authors.forename: Elizabeth
authors.initials: E
authors.lastname: Cheah
authors.forename: Yew
authors.initials: Y
authors.lastname: Oo Tan