title: [Primary cholangiocarcinoma associated with Caroli disease].
abstract: A 68 years old male presented with right hypochondrium abdominal pain and jaundice with no other clinical finding. CAT Scan and Ultrasonography showed right lobe bile duct dilatation. Magnetic Resonance Cholangiopancreatography gave an outstanding vision of a restricted right lobe bile duct dilatation associated to choledocholithiasis. A right hepatectomy and bile duct exploration were performed. The histopathological study disclosed a Caroli disease associated to a primary cholangiocarcinoma. Caroli disease is a congenital disorder characterized by intrahepatic cystic bile duct dilatation with a high risk association with cholangiocarcinoma.
authors.affiliation: Departamento de Cirugía, Universidad de la Frontera, Clínica Alemana de Temuco, Servicio de Medicina Interna, Hospital Regional Temuco, Chile.
authors.forename: G
authors.initials: G
authors.lastname: Faría
authors.forename: X
authors.initials: X
authors.lastname: de Aretxabala
authors.forename: A
authors.initials: A
authors.lastname: Sierralta
authors.forename: P
authors.initials: P
authors.lastname: Flores
authors.forename: L
authors.initials: L
authors.lastname: Burgos
mesh_terms: D000368:Aged; D001650:Bile Duct Neoplasms / Q000150:complications* / Q000601:surgery; D001653:Bile Ducts, Intrahepatic / Q000601:surgery; D016767:Caroli Disease / Q000150:complications* / Q000601:surgery; D018281:Cholangiocarcinoma / Q000150:complications* / Q000601:surgery; D006801:Humans; D008297:Male