[Irreversible acute heart failure caused by cardiac hemochromatosis secondary to multiple transfusions].
We report a 64 years old male, admitted for dyspnea and edema of two weeks duration. A sideroblastic anemia, requiring multiple transfusions, was diagnosed four years earlier. The chest X-ray showed an enlarged heart and right pleural effusion. A low left ejection fraction was evidenced by echocardiogram. Doppler analysis of the mitral flow revealed a restrictive hemodynamic pattern. A diagnosis of secondary cardiac hemochromatosis deposit was made. Nine days after admission the patient died due to heart failure. The clinical presentation of cardiac hemochromatosis as a sudden and irreversible heart failure, as well as the importance of early diagnosis and surveillance of high-risk patients is emphasized.
Martí
Vicens
V
Departamento de Cardiología, Hospital de la Santa Creu i Sant Pau, Barcelona, España.
Guarinos
Jordi
J
Aminian
Nasrim
N
Guillaumet
Eva
E
Domínguez de Rozas
José M
JM
D000208:Acute Disease; D009202:Cardiomyopathies / Q000150:complications*; D017809:Fatal Outcome; D006333:Heart Failure / Q000209:etiology*; D006432:Hemochromatosis / Q000150:complications*; D006801:Humans; D008297:Male; D008875:Middle Aged; D065227:Transfusion Reaction