title: Cochlear implantation in maternal inherited diabetes and deafness syndrome.
abstract: We describe a rare case of a gradually progressive hearing loss in a patient with maternally inherited diabetes and deafness (MIDD) syndrome successfully rehabilitated with a cochlear implant. The possible aetiology of the hearing loss in these cases is discussed.
authors.affiliation: Department of Otolaryngology, Belfast City Hospital, UK. rautvivek@hotmail.com
authors.forename: V
authors.initials: V
authors.lastname: Raut
authors.forename: A R
authors.initials: AR
authors.lastname: Sinnathuray
authors.forename: J G
authors.initials: JG
authors.lastname: Toner
mesh_terms: D000328:Adult; D019929:Cochlear Implantation; D004252:DNA Mutational Analysis; D003922:Diabetes Mellitus, Type 1 / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006319:Hearing Loss, Sensorineural / Q000235:genetics / Q000601:surgery*; D006801:Humans; D017241:MELAS Syndrome / Q000235:genetics; D008297:Male; D009035:Mothers; D017354:Point Mutation; D013577:Syndrome