title: Anaesthetic management of a patient with Emery-Dreifuss muscular dystrophy.
abstract: Emery-Dreifuss muscular dystrophy is a rare form of muscular dystrophy associated with cardiac implications such as cardiomyopathy and arrhythmias leading to sudden death. We describe the anesthetic management of a patient with Emery-Dreifuss muscular dystrophy who presented for orthopaedic surgery and discuss the disorder and its potential anaesthetic implications.
authors.affiliation: Department of Anaesthesia and Intensive Care, All India Institute of Medical Sciences, New Delhi.
authors.forename: D
authors.initials: D
authors.lastname: Shende
authors.forename: R
authors.initials: R
authors.lastname: Agarwal
mesh_terms: D000125:Achilles Tendon / Q000601:surgery*; D000293:Adolescent; D000767:Anesthesia, Epidural / Q000379:methods*; D005500:Follow-Up Studies; D006801:Humans; D007431:Intraoperative Complications / Q000517:prevention & control*; D008297:Male; D020389:Muscular Dystrophy, Emery-Dreifuss / Q000175:diagnosis* / Q000628:therapy; D019637:Orthopedic Procedures / Q000379:methods; D010138:Pacemaker, Artificial; D011300:Preoperative Care / Q000379:methods; D018570:Risk Assessment; D016896:Treatment Outcome