Fatal granulomatous disease of childhood: presenting as acute abdomen.
Fatal granulomatous disease of childhood is a rare disorder of phagocytic function. We report a 6-year-old boy who presented with acute abdomen. The diagnosis was established by mesenteric lymph node biopsy obtained at laparotomy. The boy succumbed within hours of surgery.
Ibrarullah
M D
MD
Department of Gastroenterology, SV Institute of Medical Sciences, Tirupati, AP. svimshosp@yahoo.com
Reddy
M Kumaraswamy
MK
D000006:Abdomen, Acute / Q000209:etiology*; D002648:Child; D017809:Fatal Outcome; D006105:Granulomatous Disease, Chronic / Q000150:complications* / Q000473:pathology; D006801:Humans; D008198:Lymph Nodes / Q000473:pathology; D008297:Male; D008643:Mesentery