[Brugada syndrome or ARVD (arrhythmogenic right ventricular dysplasia) or both? Significance and value of right precordial ECG changes].
We report about a 20-year old patient suffering cardiopulmonary resuscitation due to ventricular fibrillation. We diagnosed Brugada syndrome after exclusion structural heart disease and a positive Ajmalin test and implanted an ICD. In that there is a 20-30% familiar disposition, it was necessary that all family members undergo a cardiac examination. It was found that one brother and one sister presented the beginning of a right ventricular dilatation and a fibrolipomatous area in the anterior wall segment of the right ventricle. This result is compatible with a "concealed" arrhythmogenic right ventricular dysplasia (ARVD). As a prognostic indication we decided to implant an ICD prophylactically. The case report demonstrates the value of familiar examination of patients with an unclear ventricular arrhythmogenic event.
Medizinische Klinik-Kardiologie Krankenhaus Siegburg Ringstrasse 49 53721 Siegburg, Germany. TSchmidt@aol.com
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T
Schmidt
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Gerckens
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Ortmeyer
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Bootsveld
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Lampe
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Grube
D000328:Adult; D000465:Algorithms; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis* / Q000235:genetics / Q000503:physiopathology / Q000628:therapy; D016887:Cardiopulmonary Resuscitation; D017147:Defibrillators, Implantable; D003937:Diagnosis, Differential; D004562:Electrocardiography; D005820:Genetic Testing; D006801:Humans; D008297:Male; D014693:Ventricular Fibrillation / Q000209:etiology* / Q000235:genetics / Q000628:therapy