Orbital lipomatous haemangiopericytoma: an unusual variant.
Haemangiopericytoma (HPC) of the orbit is a rare tumour occurring in all age groups and presenting with slowly progressive proptosis, ocular motility impairment and visual loss. Although most are benign tumours that are resectable at diagnosis, one-third of these tumours demonstrate malignant features and recur locally or metastasize, usually with a fatal outcome. In 1995, a morphologically unique variant, termed lipomatous haemangiopericytoma (L-HPC), was described. Only one case has been reported previously arising in the orbit. In this paper, a case is reported of L-HPC occurring in the orbit and consider the prognostic implications of this HPC variant.
Davies
Peter E J
PE
Department of Ophthalmology, Royal Adelaide Hospital, South Australia, Australia. pejd@hotmail.com
Davis
Garry J
GJ
Dodd
Tom
T
Selva
Dinesh
D
D000368:Aged; D004172:Diplopia / Q000175:diagnosis; D005094:Exophthalmos / Q000175:diagnosis; D006393:Hemangiopericytoma / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008068:Lipomatosis / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D008297:Male; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014792:Visual Acuity