Surgical treatment of hereditary lens subluxations.
OBJECTIVE
To evaluate the effectiveness and results of pars plana vitreolensectomy approach with transscleral fixation of intraocular lens in hereditary lens subluxations.


METHODS
Fifteen eyes of 9 consecutive patients with a mean age of 12.8+/-6.2 years (6-26 years) with hereditary lens subluxation were operated on and the results were evaluated in a prospective study. Surgery was considered if best spectacle corrected visual acuity (BSCVA) was less than 20/70. All eyes underwent a 2-port pars plana vitreolensectomy and transscleral fixation of an intraocular lens (IOL).


RESULTS
The mean follow-up period was 12.6+/-7.5 months (6-22 months). There was no major intraoperative complication. Preoperatively, 8 eyes (53.3%) had a BSCVA of counting fingers (CF) and 7 eyes (46.6%) had a BSCVA of 20/200 to 20/70. Postoperatively, 14 eyes (93.3%) had a BSCVA of 20/50 or better. None of the patients had IOL decentration or intraocular pressure (IOP) increase during the follow-up period. There was a macular hole formation in 1 eye postoperatively.


CONCLUSIONS
The early results of pars plana vitreolensectomy with IOL implantation using scleral fixation technique had shown that it not only promises a rapid visual rehabilitation but it is also a relatively safe method. More serious complications, however, may occur in the long term.
Ozdek
Sengul
S
Department of Ophthalmology, Dokuz Eylül University, Izmir, Turkey.
Sari
Ayca
A
Bilgihan
Kamil
K
Akata
Fikret
F
Hasanreisoglu
Berati
B
D000293:Adolescent; D000328:Adult; D002648:Child; D005139:Eyeglasses; D005260:Female; D006801:Humans; D007906:Lens Subluxation / Q000235:genetics* / Q000601:surgery*; D007908:Lens, Crystalline / Q000601:surgery*; D008297:Male; D013508:Ophthalmologic Surgical Procedures / Q000009:adverse effects; D011446:Prospective Studies; D012167:Retinal Perforations / Q000209:etiology; D016896:Treatment Outcome; D014792:Visual Acuity; D014821:Vitrectomy / Q000009:adverse effects