Treatment of a case of primary retroperitoneal mucinous cystadenocarcinoma: is adjuvant hysterectomy and bilateral salpingo-oophorectomy justified?
OBJECTIVE
We present a case of primary retroperitoneal mucinous cystadenocarcinoma in a 38-year-old woman.


METHODS
The tumor was resected with a segment of adjacent descending colon. Five years after the operation, the patient is well, without evidence of recurring disease, based on clinical investigation and modern imaging techniques.


RESULTS
In the light of the literature, it appears most likely that this rare tumor is caused by coelomic metaplasia. On the basis of the histopathologic findings in our case and the reports from the literature, we recommend radical tumor excision en bloc with all infiltrated adjacent structures.


CONCLUSIONS
Added removal of unaffected uterus and adnexes makes young women infertile and climacteric and is not yet validated by long-term results.
Department of Surgery, Kantonales Spital Altstätten, St Gallen, Switzerland.
Thomas M
TM
Kessler
Wolfgang
W
Kessler
Jörg
J
Neuweiler
Bernhard H
BH
Nachbur
D000328:Adult; D018282:Cystadenocarcinoma, Mucinous / Q000175:diagnosis / Q000601:surgery*; D005187:Fallopian Tubes / Q000601:surgery; D005260:Female; D006801:Humans; D007044:Hysterectomy; D010052:Ovariectomy; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis / Q000601:surgery*