Fatal granulomatous disease of childhood: presenting as acute abdomen.
Fatal granulomatous disease of childhood is a rare disorder of phagocytic function. We report a 6-year-old boy who presented with acute abdomen. The diagnosis was established by mesenteric lymph node biopsy obtained at laparotomy. The boy succumbed within hours of surgery.
Department of Gastroenterology, SV Institute of Medical Sciences, Tirupati, AP. svimshosp@yahoo.com
M D
MD
Ibrarullah
M Kumaraswamy
MK
Reddy
D000006:Abdomen, Acute / Q000209:etiology*; D002648:Child; D017809:Fatal Outcome; D006105:Granulomatous Disease, Chronic / Q000150:complications* / Q000473:pathology; D006801:Humans; D008198:Lymph Nodes / Q000473:pathology; D008297:Male; D008643:Mesentery