Surgical treatment of aplasia cutis congenita of the scalp associated with bilateral coronal synostosis.
Aplasia cutis congenita is a rare condition characterized by the congenital absence of skin. The authors report a case of aplasia cutis congenita of the scalp associated with bilateral coronal synostosis. Simultaneous fronto-orbital advancement and skull reconstruction for large defect at the fontanelle were performed in the initial operation. A tissue expander made it possible to resect most of the hairless scar and totally cover the reconstructed defect and skull. During the second stage, the residual hairless scar was completely covered with hair-bearing scalp by tissue expansion and the residual skull defects were successfully reconstructed with split calvarial bone grafting.
Komuro
Yuzo
Y
Department of Plastic Surgery, Juntendo University School of Medicine, Tokyo, Japan. komuro@med.juntendo.ac.jp
Yanai
Akira
A
Seno
Hisakazu
H
Ichida
Masayuki
M
Inoue
Masahiro
M
Miyajima
Masakazu
M
Arai
Hajime
H
Sato
Kiyoshi
K
D000505:Alopecia / Q000601:surgery; D016025:Bone Transplantation; D002921:Cicatrix / Q000601:surgery; D003398:Craniosynostoses / Q000601:surgery*; D004476:Ectodermal Dysplasia / Q000601:surgery*; D005500:Follow-Up Studies; D005624:Frontal Bone / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D021621:Imaging, Three-Dimensional; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D009915:Orbit / Q000601:surgery; D010294:Parietal Bone / Q000002:abnormalities* / Q000601:surgery; D012535:Scalp / Q000002:abnormalities* / Q000601:surgery; D013524:Surgical Flaps; D015626:Tissue Expansion; D014057:Tomography, X-Ray Computed