Childhood infundibular stenosis.
Infundibular stenosis is a rare condition marked by dilation of one or more calices proximal to a stenotic infundibulum. Contrary to older reports, more recent information suggests that progressive renal dysfunction occurs in a significant number of these patients. We present a case of incidentally discovered infundibular stenosis. On the basis of the existing published reports, we make several recommendations. Close monitoring for a decline in renal function secondary to hyperfiltration injury is essential, and a worsening should prompt referral to a pediatric nephrologist. Progressive hydronephrosis should be corrected surgically, although proof of effect on the disease process is lacking in the evidence-based reports.
Nurzia
Michael J
MJ
Department of Surgery (Division of Urology), University of Medicine and Dentistry of New Jersey, Robert Wood Johnson University Hospital, New Brunswick, New Jersey 08903-0019, USA.
Costantinescu
Alexandru R
AR
Barone
Joseph G
JG
D002675:Child, Preschool; D003251:Constriction, Pathologic / Q000150:complications / Q000000981:diagnostic imaging; D004108:Dilatation, Pathologic / Q000150:complications / Q000000981:diagnostic imaging; D018450:Disease Progression; D006801:Humans; D007223:Infant; D007670:Kidney Calices / Q000000981:diagnostic imaging; D007682:Kidney Pelvis / Q000000981:diagnostic imaging; D008297:Male; D011859:Radiography