Encephalocele as a late complication of cranial vault reconstruction in a patient with Crouzon's syndrome.
Encephalocele is a rare late complication of craniosynostosis repair. An undiagnosed nick to the dura is the etiology of this complication. It usually presents within a few months to years after repair. This case report describes a patient with Crouzon's Disease who had a craniosynostosis repair as an infant and presents 22 years later with an encephalocele. The patient had a thorough physical exam, 2D, and 3D CT Scans as a preoperative workup. Surgical intervention included repair of the encephalocele, cranialization of the frontal sinus with bone grafting, and Lefort III osteomies for mid face advancement. The patient benefited from a two-team simultaneous approach between Neurosurgery and Plastic Surgery. The patient also benefited from an aggressive one-stage repair of all her defects and deformities.
Divisions of Plastic Surgery and Neurosurgery, University of Mississippi Medical Center Jackson, Mississippi 39214, USA.
Jeffrey
J
Caplan
Michael
M
Angel
Andrew
A
Parent
D000328:Adult; D016025:Bone Transplantation; D003394:Craniofacial Dysostosis / Q000601:surgery*; D003398:Craniosynostoses / Q000601:surgery; D004677:Encephalocele / Q000209:etiology* / Q000601:surgery; D005260:Female; D005546:Forehead / Q000601:surgery; D005624:Frontal Bone / Q000601:surgery*; D005626:Frontal Sinus / Q000601:surgery; D006801:Humans; D021621:Imaging, Three-Dimensional; D008279:Magnetic Resonance Imaging; D008437:Maxilla / Q000601:surgery; D009300:Nasal Septum / Q000601:surgery; D019340:Osteotomy, Le Fort; D010159:Palate / Q000601:surgery; D011183:Postoperative Complications; D014057:Tomography, X-Ray Computed / Q000379:methods; D015050:Zygoma / Q000601:surgery