Surgical treatment of aplasia cutis congenita of the scalp associated with bilateral coronal synostosis.
Aplasia cutis congenita is a rare condition characterized by the congenital absence of skin. The authors report a case of aplasia cutis congenita of the scalp associated with bilateral coronal synostosis. Simultaneous fronto-orbital advancement and skull reconstruction for large defect at the fontanelle were performed in the initial operation. A tissue expander made it possible to resect most of the hairless scar and totally cover the reconstructed defect and skull. During the second stage, the residual hairless scar was completely covered with hair-bearing scalp by tissue expansion and the residual skull defects were successfully reconstructed with split calvarial bone grafting.
Department of Plastic Surgery, Juntendo University School of Medicine, Tokyo, Japan. komuro@med.juntendo.ac.jp
Yuzo
Y
Komuro
Akira
A
Yanai
Hisakazu
H
Seno
Masayuki
M
Ichida
Masahiro
M
Inoue
Masakazu
M
Miyajima
Hajime
H
Arai
Kiyoshi
K
Sato
D000505:Alopecia / Q000601:surgery; D016025:Bone Transplantation; D002921:Cicatrix / Q000601:surgery; D003398:Craniosynostoses / Q000601:surgery*; D004476:Ectodermal Dysplasia / Q000601:surgery*; D005500:Follow-Up Studies; D005624:Frontal Bone / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D021621:Imaging, Three-Dimensional; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D009915:Orbit / Q000601:surgery; D010294:Parietal Bone / Q000002:abnormalities* / Q000601:surgery; D012535:Scalp / Q000002:abnormalities* / Q000601:surgery; D013524:Surgical Flaps; D015626:Tissue Expansion; D014057:Tomography, X-Ray Computed