[Anesthesia for cesarean section in a patient with McArdle disease and hereditary dilated cardiomyopathy].
A caesarean section was indicated in a 29-year-old parturient affected by a muscular deficit in myophosphorylase responsible for a type V glycogen storage disease (McArdle disease). This metabolic myopathy had been diagnosed two years previously, whereas the patient already suffered from a hereditary form of dilated cardiomyopathy. The muscular disease was invalidating on the functional level with exercise intolerance. The cardiopathy was little symptomatic but the dysfunction of the left ventricle worsened during the pregnancy with an ejection fraction calculated to 43%. In this case, we report the realization of a general anaesthesia in a patient who had epidural anaesthesia for a previous caesarean section.
Service d'anesthésie-réanimation chirurgicale, Hôtel-Dieu, 44093 Nantes, France. thierry.lepoivre@free.fr
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D000328:Adult; D000768:Anesthesia, General; D000773:Anesthesia, Obstetrical; D002311:Cardiomyopathy, Dilated / Q000150:complications* / Q000235:genetics; D002585:Cesarean Section; D005260:Female; D006012:Glycogen Storage Disease Type V / Q000150:complications*; D006801:Humans; D011247:Pregnancy; D013318:Stroke Volume; D018487:Ventricular Dysfunction, Left / Q000503:physiopathology