Supravalvular congenital mitral stenosis.
Congenital supravalvular mitral stenosis is a rare malformation characterized by the presence of a shelf-like fibrous membrane, with 1 or 2 small orifices, covering and obstructing the mitral valve. The membrane is positioned closely to the mitral valve (and sometimes it is attached to it); therefore, a preoperative diagnosis is inevitably difficult, even with the use of biplane echocardiography. Two patients with supravalvular mitral stenosis aged 3 years and 3 months are described. In 1 patient, a preoperative diagnosis was made, and both successfully underwent correction.
Moraes
Fernando
F
Instituto do Coração de Pernambuco, Real Hospital Português, Recife, PE.
Lapa
Cleuza
C
Ventura
Cristina
C
Santana
Rejane
R
Tenorio
Euclides
E
Gomes
Claudio
C
Moraes
Carlos R
CR
D002675:Child, Preschool; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008297:Male; D008946:Mitral Valve Stenosis / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery