title: Plexiform fibrohistiocytic tumor: a rare low-grade malignancy of children and young adults.
abstract: Plexiform fibrohistiocytic tumor (PFT) is a low-grade, superficial, soft tissue neoplasm with a limited but significant ability to metastasize. This type of tumor only rarely presents in the skin of the head and neck. Clinicians first encountering young patients with facial neoplasia, such as a PFT, might be unaware of its exact oncologic potential and instead be primarily concerned with the cosmetic outcome. We treated a 17-year-old boy with a PFT on his cheek who was initially treated only by shave biopsy. The tumor subsequently recurred and metastasized to the cervical lymph nodes 3 years after the initial biopsy. Therefore, appropriate initial therapy for PFT requires complete excision with negative resection margins.
authors.affiliation: Department of Otolaryngology, Mount Sinai School of Medicine, New York, NY 10029-3136, USA.
authors.forename: Leal G
authors.initials: LG
authors.lastname: Segura
authors.forename: Jeff
authors.initials: J
authors.lastname: Harris
authors.forename: Beverly
authors.initials: B
authors.lastname: Wang
authors.forename: Al
authors.initials: A
authors.lastname: Rienzo
authors.forename: Mark L
authors.initials: ML
authors.lastname: Urken
authors.forename: Margaret
authors.initials: M
authors.lastname: Brandwein
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D002610:Cheek / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D002648:Child; D005153:Facial Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*; D006801:Humans; D008297:Male; D012983:Soft Tissue Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*; D014057:Tomography, X-Ray Computed