[Pheochromocytoma and von Recklinghausen's disease].
The association between von Recklinghausen's disease and pheochromocytoma is present about 10% of cases. We report a case of 49 years old women who presented with elevated blood pressure and von Recklinghausen's neurofibromatosis. Laboratory examination showed a marked level in the urinary excretion of cathecholamine. The computed tomography showed a right adrenal tumor suggesting a pheochromocytoma. The adrenalectomy was realised by transabdominal approach and the histological examination confirmed a benign pheochromocytoma. The authors discuss the pathogenetic hypothesis of this rare pathological association, the diagnostic methods and the therapeutic procedure.
Rabii
R
R
Service d'urologie, CHU Ibn Rochd, Casablanca, Maroc. rrabii@urologues.com
Fekak
H
H
Moufid
K
K
Joual
A
A
Bennani
S
S
el Mrini
M
M
Benjelloun
S
S
D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D000315:Adrenalectomy; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications*; D010673:Pheochromocytoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography