An unusual etiology of hypertension in a 5-year-old boy.
Ganglioneuromas are rare benign tumors of neural crest origin, arising from ganglia of the sympathetic nervous system and adrenal medulla. These masses are usually detected during the first 2 decades of life and are generally discovered incidentally. We present a 5-year-old boy with sickle beta-thalassemia whose hypertension is caused by a perihilar ganglioneuroma encasing the right renal artery and distorting the right renal vein. The tumor was resected and the child's blood pressure subsequently normalized.
Menschik
David
D
LeBonheur Children's Medical Center, Memphis, TN 38103, USA.
Lovvorn
Harold
H
Hill
Ashley
A
Kelly
Patrick
P
Jones
Deborah P
DP
D000755:Anemia, Sickle Cell / Q000150:complications; D002675:Child, Preschool; D005729:Ganglioneuroma / Q000150:complications* / Q000473:pathology; D006801:Humans; D006977:Hypertension, Renal / Q000209:etiology* / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D010524:Peripheral Nervous System Neoplasms / Q000150:complications* / Q000473:pathology; D017086:beta-Thalassemia / Q000150:complications