Cochlear implantation in a patient with superficial siderosis of the central nervous system.
OBJECTIVE
To perform an assessment of the viability of cochlear implantation in a patient with superficial siderosis of the brain.


METHODS
Case review.


METHODS
Tertiary referral center.


METHODS
Patient with superficial siderosis of the brain.


METHODS
Cochlear implantation.


METHODS
Electrically evoked auditory brainstem responses and fitting strategy for cochlear implant based on patient's subjective responses.


RESULTS
After some time, C levels and T levels showed a pattern comparable with the evoked auditory brainstem responses.


CONCLUSIONS
Bilateral profound hearing loss after superficial siderosis of the brain is no absolute contraindication for implantation. Furthermore, evoked auditory brainstem measurements can potentially guide the fitting process of the implant in difficult cases.
Dhooge
Ingeborg J M
IJ
Department of Otorhinolaryngology, Ghent University Hospital, De Pintelaan 185, B-9000 Ghent, Belgium. ingeborg.dhooge@rug.ac.be
De Vel
Eddy
E
Urgell
Henri
H
Gallégo
Stéphane
S
Vinck
Bart
B
D001927:Brain Diseases / Q000150:complications* / Q000175:diagnosis; D002531:Cerebellum / Q000473:pathology; D003054:Cochlear Implants; D000075202:Contraindications; D003638:Deafness / Q000209:etiology* / Q000503:physiopathology / Q000628:therapy*; D016057:Evoked Potentials, Auditory, Brain Stem; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D017755:Prosthesis Fitting; D012806:Siderosis / Q000150:complications* / Q000175:diagnosis