Major complex pelvic arteriovenous malformation in a patient with Down syndrome.
Pelvic arteriovenous malformations (AVM) are rare, and the treatment of this condition presents an interesting challenge. We report the first case of a major AVM in a patient with Down syndrome which was revealed by a massive hematuria. Arteriography showed a bilateral complex iliac artery malformation. The first proximal embolization (unilateral) did not prevent bladder hemorrhage, and the second distal (bilateral) immobilization produced bladder necrosis. However, the patient died despite an emergency cystectomy.
Kassardjian
Zareh
Z
Department of Urology, Hôpital Foch, Suresnes, France.
Lebret
Thierry
T
Mellot
François
F
Hervé
Jean-Marie
JM
Barré
Philippe
P
Lugagne
Pierre-Marie
PM
Scherrer
Antoine
A
Botto
Henry
H
D001165:Arteriovenous Malformations / Q000150:complications*; D004314:Down Syndrome / Q000150:complications*; D006417:Hematuria / Q000209:etiology; D006801:Humans; D007083:Iliac Artery / Q000002:abnormalities; D008297:Male; D008875:Middle Aged; D010388:Pelvis / Q000098:blood supply*