Major complex pelvic arteriovenous malformation in a patient with Down syndrome.
Pelvic arteriovenous malformations (AVM) are rare, and the treatment of this condition presents an interesting challenge. We report the first case of a major AVM in a patient with Down syndrome which was revealed by a massive hematuria. Arteriography showed a bilateral complex iliac artery malformation. The first proximal embolization (unilateral) did not prevent bladder hemorrhage, and the second distal (bilateral) immobilization produced bladder necrosis. However, the patient died despite an emergency cystectomy.
Department of Urology, Hôpital Foch, Suresnes, France.
Zareh
Z
Kassardjian
Thierry
T
Lebret
François
F
Mellot
Jean-Marie
JM
Hervé
Philippe
P
Barré
Pierre-Marie
PM
Lugagne
Antoine
A
Scherrer
Henry
H
Botto
D001165:Arteriovenous Malformations / Q000150:complications*; D004314:Down Syndrome / Q000150:complications*; D006417:Hematuria / Q000209:etiology; D006801:Humans; D007083:Iliac Artery / Q000002:abnormalities; D008297:Male; D008875:Middle Aged; D010388:Pelvis / Q000098:blood supply*