[Susac syndrome as a cause of sensorineural hearing loss].
Susac's syndrome is an extremely rare clinical manifestation characterized by the triad of fluctuating sensorineural hearing loss, sudden visual loss and encephalopathy. Probably underdiagnosed, it affects young women who start the clinical history with headache, visual and hearing disturbances, with neurological findings in MRI. With unknown aetiology, pathogenesis is based on arteriolar microinfarcts in retina, cochlea, and grey and white matter in the brain. Treatment is, as stated in the bibliography and our experience, intravenous high doses of steroids followed by oral steroids together with hyperbaric oxygen to minimize ischaemic lesions. Aspirin associate to nimodipine has been useful to date in the treatment of our patient. We present a case and review the existing literature.
Cubillana Herrero
J D
JD
Servicio ORL, Hospital Virgen de la Arrixaca, Carretera Madrid-Cartagena, s/n. 30120 El Palmar, Murcia. jdcubillana@servicam.com
Soler Valcárcel
A
A
Albaladejo Devis
I
I
Rodríguez González-Herrero
B
B
Minguez Merlos
N
N
Jiménez Cervantes-Nicolás
J A
JA
D000328:Adult; D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D001241:Aspirin / Q000627:therapeutic use; D002544:Cerebral Infarction / Q000209:etiology*; D003051:Cochlea / Q000098:blood supply*; D003131:Combined Modality Therapy; D003638:Deafness / Q000209:etiology; D003937:Diagnosis, Differential; D005260:Female; D005334:Fever / Q000209:etiology; D006212:Hallucinations / Q000209:etiology; D006319:Hearing Loss, Sensorineural / Q000209:etiology*; D006801:Humans; D006931:Hyperbaric Oxygenation; D007238:Infarction / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000628:therapy; D008279:Magnetic Resonance Imaging; D008775:Methylprednisolone / Q000627:therapeutic use; D008833:Microcirculation; D019965:Neurocognitive Disorders / Q000209:etiology*; D009553:Nimodipine / Q000627:therapeutic use; D010975:Platelet Aggregation Inhibitors / Q000627:therapeutic use; D012171:Retinal Vessels / Q000473:pathology*; D013577:Syndrome; D014786:Vision Disorders / Q000209:etiology*
D000893:Anti-Inflammatory Agents; D010975:Platelet Aggregation Inhibitors; D009553:Nimodipine; D001241:Aspirin; D008775:Methylprednisolone