Perioperative course in two cases of tetralogy of fallot with portal venous atresia.
We report here two rare surgical cases of tetralogy of Fallot with portal venous atresia. Both patients, previously diagnosed with tetralogy of Fallot, developed portal hypertension and showed hematemesis and/or melena. One patient needed endoscopic sclerotherapy. Intracardiac repair was performed under cardiopulmonary bypass (CPB) with moderate hypothermia. After surgery, one of the patients developed cardiogenic shock due to cardiac tamponade with accumulated chyle in the pericardial sac in the ninth postoperative day, and showed deteriorated liver function, suggesting that liver might have been vulnerable because of the absence of portal blood.
Division of Cardiology and Cardiovascular Surgery, Saitama Children's Medical Center, Magome 2100, Iwatsuki, Saitama 339-8551, Japan. a1075097@pref.saitama.jp
T
T
Hishitani
K
K
Hoshino
K
K
Ogawa
K
K
Koyanagi
Y
Y
Nakamura
D017023:Coronary Angiography; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000175:diagnosis / Q000209:etiology; D007223:Infant; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013771:Tetralogy of Fallot / Q000150:complications* / Q000601:surgery*; D014057:Tomography, X-Ray Computed