Pulmonary valvuloplasty in a case of vascular Ehlers-Danlos syndrome.
A 15-year-old girl with known Ehlers-Danlos syndrome (EDS) type IV presented with severe pulmonary valve stenosis requiring intervention. We describe successful pulmonary valvuloplasty using a 90% balloon/annulus angioplasty balloon. The procedure was complicated by early restenosis suggesting an abnormal scarring response in EDS IV.
Department of Paediatric Cardiology, Royal Hospital for Sick Children, Bristol, England. bev@nixal.com
Beverly
B
Tsai-Goodman
Robin P
RP
Martin
F Michael
FM
Pope
A Graham
AG
Stuart
D000293:Adolescent; D002404:Catheterization; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000628:therapy*; D005260:Female; D006801:Humans; D011664:Pulmonary Valve / Q000601:surgery*; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000628:therapy*