Pseudoexstrophy associated with megalourethra.
Pseudoexstrophy is a rare exstrophy variant that has musculoskeletal stigmata of the exstrophy complex without any associated defect in the urinary system. The authors report a case of pseudoexstrophy with scaphoid megalourethra, and anorectal malformation. Kidneys and ureters were normal. Preliminary surgery consisted of a divided high sigmoid colostomy. The rare combination of pseudoexstrophy and megalourethra is discussed.
Devendra
Kumar
K
Department of Pediatric Surgery, Advanced Pediatric Centre, PGIMER, Chandigarh, India.
Mahajan
J K
JK
Rao
K L N
KL
D000015:Abnormalities, Multiple; D001006:Anus, Imperforate; D001746:Bladder Exstrophy; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010413:Penis / Q000002:abnormalities; D014521:Urethra / Q000002:abnormalities*