Ultrasound biomicroscopic findings in hallerman-streiff syndrome.
OBJECTIVE
To demonstrate the usefulness of ultrasound biomicroscopy in detecting the morphological changes in the lens caused by the spontaneous absorption of lens material and to detect fundus abnormalities in a patient with Hallermann-Streiff syndrome.


METHODS
Case report of an infant diagnosed at the age of 2 months as having Hallermann-Streiff syndrome.


RESULTS
Spontaneous lens absorption occurred during the course of follow-up and was detected only by ultrasound biomicroscopy after the patient was prepared for cataract surgery. The changes in the anterior chamber depth and lens shapes were documented by ultrasound biomicroscopy. Retinal folds that were barely observable by conventional ophthalmoscopy because of a dense cataract were clearly shown by ultrasound biomicroscopy.


CONCLUSIONS
Ultrasound biomicroscopy can be used to examine the lenses of eyes that are not observable with conventional optical instruments. Ultrasound biomicroscopy can also be used to study the posterior segment of microphthalmic eyes. We recommend preoperative ultrasound biomicroscopy to prevent unnecessary anesthesia and surgical preparation.
Sato
Miho
M
Department of Ophthalmology, Nagoya University School of Medicine, Nagoya, Japan.
Terasaki
Hiroko
H
Amano
Emil
E
Okamoto
Yoko
Y
Miyake
Yozo
Y
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000867:Anterior Chamber / Q000002:abnormalities / Q000000981:diagnostic imaging; D005124:Eye Abnormalities / Q000000981:diagnostic imaging*; D017809:Fatal Outcome; D006210:Hallermann's Syndrome / Q000000981:diagnostic imaging*; D006801:Humans; D007223:Infant; D007908:Lens, Crystalline / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008297:Male; D012160:Retina / Q000002:abnormalities / Q000000981:diagnostic imaging; D014463:Ultrasonography