[Noncompaction of the left ventricular myocardium. Case report and review of the literature].
Left ventricular non-compaction is an unclassified cardiomyopathy characterized by an excessively prominent trabecular meshwork due to an arrest in myocardial morphogenesis. We report on a 51-year-old female patient with abnormal myocardial trabeculations associated with a congenital mitral valve stenosis post commissurotomy at the age of 14. In the present case report, clinical manifestation of the disorder included impaired left ventricular systolic function and atrial fibrillation. Noncompaction was diagnosed by echocardiography and levocardiography. In addition, a review of the literature on this rare disorder is presented.
Skowasch
D
D
Medizinische Klinik und Poliklinik II Universitätsklinikum Bonn Sigmund-Freud-Str. 25, 53105 Bonn, Germany. Dirk.Skowasch@ukb.uni-bonn.de
Lentini
S
S
Kubini
R
R
Lüderitz
B
B
Bauriedel
G
G
D000293:Adolescent; D001281:Atrial Fibrillation / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology; D002306:Cardiac Volume / Q000502:physiology; D009202:Cardiomyopathies / Q000175:diagnosis* / Q000503:physiopathology; D017023:Coronary Angiography; D003324:Coronary Artery Disease / Q000175:diagnosis / Q000503:physiopathology; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006333:Heart Failure / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology; D006352:Heart Ventricles / Q000000981:diagnostic imaging; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D008875:Middle Aged; D008943:Mitral Valve / Q000002:abnormalities / Q000601:surgery; D008946:Mitral Valve Stenosis / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D009200:Myocardial Contraction / Q000502:physiology*; D011183:Postoperative Complications / Q000175:diagnosis / Q000503:physiopathology; D013599:Systole / Q000502:physiology; D018487:Ventricular Dysfunction, Left / Q000151:congenital* / Q000175:diagnosis / Q000503:physiopathology; D016277:Ventricular Function, Left / Q000502:physiology