Noninvasive and invasive evaluation of noncompaction cardiomyopathy.
Noncompaction cardiomyopathy is a recently described rare congenital cardiomyopathy; patients can be asymptomatic or develop diastolic and/or systolic left ventricular dysfunction with heart failure, systemic emboli or ventricular arrhythmias. Long-term prognosis is poor. Currently, diagnosis is based on findings on 2D echocardiography; in the current case report we demonstrate the use of MRI to diagnose noncompaction cardiomyopathy.
Bax
Jeroen J
JJ
jbax@knoware.nl
Atsma
Douwe E
DE
Lamb
Hildo J
HJ
Rebergen
Sidney A
SA
Bootsma
Marianne
M
Voogd
Paul J
PJ
Somer
Soeresh
S
Schalij
Martin J
MJ
de Roos
Albert
A
van der Wall
Ernst E
EE
D000328:Adult; D009202:Cardiomyopathies / Q000175:diagnosis*; D003971:Diastole / Q000502:physiology; D004452:Echocardiography; D004562:Electrocardiography; D006331:Heart Diseases / Q000151:congenital; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000503:physiopathology; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000175:diagnosis* / Q000503:physiopathology; D008279:Magnetic Resonance Imaging; D008297:Male; D013318:Stroke Volume / Q000502:physiology; D013599:Systole / Q000502:physiology; D018487:Ventricular Dysfunction, Left / Q000175:diagnosis / Q000503:physiopathology