title: Helical CT features of arrhythmogenic right ventricular cardiomyopathy.
abstract: Arrhythmogenic right ventricular cardiomyopathy (ARVC), also known as arrhythmogenic right ventricular dysplasia, is a disorder of the heart muscle of unknown origin. It is characterized by electrical instability of the heart as a result of replacement of the right ventricular myocardium with fatty or fibrous fatty tissue. Dilatation of the right ventricle; fatty tissue in conspicuous trabeculae of the right ventricle, especially in the anterior wall, apex, and inferior (diaphragmatic) wall; and a scalloped appearance (bulging) of the right ventricular wall are characteristic findings at helical computed tomography (CT) that may be used to diagnose ARVC. Fatty tissue in the left ventricle and ventricular septum is seen relatively frequently in ARVC, and fat in the ventricular septum is another useful finding for diagnosis of ARVC with helical CT. ARVC is usually diagnosed on the basis of clinical or pathologic findings, and electron-beam CT is superior to nongated helical CT in assessment of abnormal right ventricular function. However, with knowledge of the characteristic findings, standard nongated helical CT can be helpful in diagnosing ARVC.
authors.affiliation: Department of Radiology, Tokyo Women's Medical University, 8-1 Kawada-cho, Shinjuku-ku, Tokyo 162-8666, Japan. fumikok@rad.twmu.ac.jp
authors.forename: Fumiko
authors.initials: F
authors.lastname: Kimura
authors.forename: Fumikazu
authors.initials: F
authors.lastname: Sakai
authors.forename: Yasunari
authors.initials: Y
authors.lastname: Sakomura
authors.forename: Mikihiko
authors.initials: M
authors.lastname: Fujimura
authors.forename: Eiko
authors.initials: E
authors.lastname: Ueno
authors.forename: Naoki
authors.initials: N
authors.lastname: Matsuda
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Kasanuki
authors.forename: Norio
authors.initials: N
authors.lastname: Mitsuhashi
mesh_terms: D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000000981:diagnostic imaging* / Q000473:pathology; D006801:Humans; D014057:Tomography, X-Ray Computed