Orthostatic paroxysmal dystonia.
A 52-year-old man with a history of cerebrovascular disease presented with a 3-year history of paroxysmal hemidystonia precipitated by assuming an upright position after sitting or lying down. MRA showed occlusion of the contralateral internal carotid artery (ICA) and near-total occlusion of the ipsilateral ICA. Subtraction single proton emission computed tomography demonstrated decreased perfusion in the contralateral frontoparietal cortex during the typical dystonic spell. We have coined the term "orthostatic paroxysmal dystonia" for this phenomenon.
Sethi
Kapil D
KD
Department of Neurology, Medical College of Georgia, Augusta, Georgia 30912, USA. ksethi@neuro.mcg.edu
Lee
Ki Hyeong
KH
Deuskar
Vasanti
V
Hess
David C
DC
D002343:Carotid Artery, Internal; D016893:Carotid Stenosis / Q000175:diagnosis* / Q000503:physiopathology; D004292:Dominance, Cerebral / Q000502:physiology; D004421:Dystonia / Q000000981:diagnostic imaging* / Q000503:physiopathology; D005625:Frontal Lobe / Q000098:blood supply* / Q000503:physiopathology; D006801:Humans; D018810:Magnetic Resonance Angiography; D008297:Male; D008875:Middle Aged; D010296:Parietal Lobe / Q000098:blood supply* / Q000503:physiopathology; D011187:Posture / Q000502:physiology*; D015899:Tomography, Emission-Computed, Single-Photon