Aplasia cutis congenita of the trunk with fetus papyraceus.
Aplasia cutis congenita (ACC) is the absence of localized or widespread areas of skin at birth. A frequently cited classification schema is based on location and the presence of associated anomalies. Histologically it is characterized by dermal fibrosis and absence of adenexal structures. We present a newborn female with extensive truncal ACC associated with fetus papyraceus.
Kelly
Benjamin J
BJ
Department of Medicine, Division of Dermatology and Cutaneous Surgery, and Department of Pathology, University of Florida, Gainesville, Florida 32610-0277, USA.
Samolitis
Nancy J
NJ
Xie
Don-Ling
DL
Skidmore
Robert A
RA
D001707:Biopsy, Needle; D004200:Diseases in Twins / Q000175:diagnosis*; D004476:Ectodermal Dysplasia / Q000175:diagnosis* / Q000473:pathology; D004817:Epidermis / Q000473:pathology; D005260:Female; D005313:Fetal Death; D006801:Humans; D007231:Infant, Newborn; D011379:Prognosis; D018570:Risk Assessment