Eosinophilic fasciitis leading to painless contractures.
We report on an 11-year-old girl who developed multiple joint contractures over a period of 3 months. The disease presented with progressive involvement of the fingers, elbows, shoulders, knees and feet and was not accompanied by other symptoms. Laboratory investigations showed eosinophilia and hypergammaglobulinaemia. Muscle ultrasound and magnetic resonance imaging of the right forearm revealed thickened fascia and a full thickness biopsy confirmed the diagnosis of eosinophilic fasciitis. Following treatment with pulsed steroids, the contractures resolved.


CONCLUSIONS
our case shows that eosinophilic fasciitis can present without skin involvement and arthritis and therefore has to be regarded as a differential diagnosis of contractures in childhood. Pulsed steroid treatment was effective and without side-effects.
Huppke
Peter
P
Abteilung Kinderheilkunde, Schwerpunkt Neuropädiatrie, Georg-August-Universität Göttingen, Robert Koch Strasse 40, 37075 Göttingen, Germany. phuppke@med.uni-goettingen.de
Wilken
Bernd
B
Brockmann
Knut
K
Sattler
Bernd
B
Hanefeld
Folker
F
D001706:Biopsy; D002648:Child; D003286:Contracture / Q000209:etiology*; D018450:Disease Progression; D004802:Eosinophilia / Q000150:complications*; D005208:Fasciitis / Q000150:complications*; D005260:Female; D006801:Humans; D007596:Joints / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D010146:Pain / Q000209:etiology*