Normally connected anomalously draining obstructed pulmonary veins in an infant with mitral atresia: clinical presentation and catheter management.
A patient with hypoplastic left ventricle and double outlet right ventricle underwent pulmonary artery band as a newborn. At age 3 months, cardiac catheterization demonstrated complete closure of his atrial septal defect with decompression of the left atrium via a small levo-cardinal vein. Thus, he had normally connected, anomalously draining obstructed pulmonary veins. He underwent successful catheter intervention with excellent release of the obstruction. This rare finding and technical aspects of catheter intervention are discussed.
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D006328:Cardiac Catheterization / Q000379:methods*; D004310:Double Outlet Right Ventricle / Q000175:diagnosis / Q000628:therapy*; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities*; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D007223:Infant; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000503:physiopathology; D018570:Risk Assessment; D016896:Treatment Outcome