[Chronic inflammatory demyelinating polyradiculoneuropathy with hypertrophy of spinal roots, brachial plexus and cranial nerves].
We report two patients who presented an atypical chronic inflammatory demyelinating polyradiculoneuropathy with massive nerve root and brachial plexus hypertrophy, and pseudotumoral supraclavicular mass. They also presented an hypertrophy of oculomotor and trigeminal nerves causing an exophthalmos and ocular palsy. Spinal root enlargement and cranial nerve hypertrophy was demonstrated by CT scanner and MRI. Brachial plexus biopsy showed a similar aspect of sural nerve, with an extensive onion bulb formation and perivascular inflammatory cell infiltration. There was an excellent response to steroids in both patients.
Aïdi
S
S
Service de neurologie.
El Alaoui Faris
M
M
Amarti
A
A
Belaïdi
H
H
Jiddane
M
M
Guezzaz
M
M
Medjel
A
A
Chkili
T
T
D000328:Adult; D005260:Female; D006801:Humans; D006984:Hypertrophy / Q000150:complications / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D009802:Oculomotor Nerve / Q000473:pathology; D020277:Polyradiculoneuropathy, Chronic Inflammatory Demyelinating / Q000150:complications / Q000473:pathology*; D013126:Spinal Nerve Roots / Q000473:pathology*; D013497:Sural Nerve / Q000473:pathology; D014276:Trigeminal Nerve / Q000473:pathology