Fetal constrictive pericardial defect with pulmonary capillary hemangiomatosis.
Pericardial defect is a rare anomaly that has a variable presentation. Prompt recognition and early surgical intervention are associated with a favorable outcome. The authors present an unusual case of unexpected fetal demise in a 31-week-gestational-age girl who had a large pericardial defect forming a constrictive ring around both ventricular chambers. The defect coexisted with pulmonary capillary hemangiomatosis, an association that has not been reported in cases of pericardial defect.
Abramson
Lisa P
LP
Department of Pediatric Surgery & Pathology, Children's Memorial Hospital, Northwestern University Medical School, Chicago, IL 60611, USA.
Gerber
Susan
S
Chen
Yi-Hua
YH
Crawford
Susan E
SE
D005260:Female; D005313:Fetal Death; D005333:Fetus; D005865:Gestational Age; D018324:Hemangioma, Capillary / Q000150:complications*; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications*; D010496:Pericardium / Q000002:abnormalities*