Neuro-Behçet's disease mimicking a cerebral tumor: a case report.
We report a rare case of neuro-Behcet's disease (NBD) presenting as an inflammatory pseudotumor in the brain. A 52-year-old woman was evaluated for subacute dizziness and headache. Brain magnetic resonance (MR) imaging showed a right cerebellar mass, which disappeared 2 weeks later. After a year, recurrent mucocutaneous manifestations of Beh et's disease were observed. Immunosuppressant and steroid maintenance treatment were started. She experienced two more neurologic attacks and brain MR imaging revealed an enhancing mass in the right temporal lobe. The second attack showed a good response to steroid pulse therapy, but the third attack did not respond to steroid and her neurologic signs suggested an impending transtentorial hernia. The right temporal lobectomy was performed for the purpose of life-saving. The pathologic finding of the mass was a chronic inflammatory vasculitis, compatible with NBD.
Park
Jeong-Ho
JH
Department of Neurology, College of Medicine, Soonchunhyang University Hospital, Chunan, Korea.
Jung
Myung-Keun
MK
Bang
Cha-Ok
CO
Park
Hyung-Kook
HK
Sung
Ki-Bum
KB
Ahn
Moo-Young
MY
Bae
Won-Kyeong
WK
Chi
Je G
JG
D001528:Behcet Syndrome / Q000175:diagnosis* / Q000601:surgery; D001927:Brain Diseases / Q000175:diagnosis* / Q000601:surgery; D001932:Brain Neoplasms / Q000175:diagnosis*; D003937:Diagnosis, Differential; D005260:Female; D006104:Granuloma, Plasma Cell / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged