A spinal intradural enterogenous cyst with well-differentiated muscularis propria.
We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to severe myelopathy led to the death of the child 19 days postpartum. At autopsy, a well-differentiated enterogenous cyst was found, the cyst wall containing gastric and esophageal type mucosa, and a bona fide muscularis propria. The gastrointestinal tract was completely normal. The possible developmental history of intradural enterogenous cysts is discussed.
ten Donkelaar
H J
HJ
Department of Neurology, University Medical Center St. Radboud Nijmegen, P.O. Box 9101, 6500 HB Nijmegen, The Netherlands. H.tenDonkelaar@czzorlnm.azn.nl
Willemsen
M A A P
MA
van der Heijden
I
I
Beems
T
T
Wesseling
P
P
D002574:Cervical Vertebrae; D003560:Cysts / Q000150:complications / Q000473:pathology*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D013117:Spinal Cord Compression / Q000209:etiology; D013118:Spinal Cord Diseases / Q000473:pathology*; D013904:Thoracic Vertebrae