title: A spinal intradural enterogenous cyst with well-differentiated muscularis propria.
abstract: We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to severe myelopathy led to the death of the child 19 days postpartum. At autopsy, a well-differentiated enterogenous cyst was found, the cyst wall containing gastric and esophageal type mucosa, and a bona fide muscularis propria. The gastrointestinal tract was completely normal. The possible developmental history of intradural enterogenous cysts is discussed.
authors.affiliation: Department of Neurology, University Medical Center St. Radboud Nijmegen, P.O. Box 9101, 6500 HB Nijmegen, The Netherlands. H.tenDonkelaar@czzorlnm.azn.nl
authors.forename: H J
authors.initials: HJ
authors.lastname: ten Donkelaar
authors.forename: M A A P
authors.initials: MA
authors.lastname: Willemsen
authors.forename: I
authors.initials: I
authors.lastname: van der Heijden
authors.forename: T
authors.initials: T
authors.lastname: Beems
authors.forename: P
authors.initials: P
authors.lastname: Wesseling
mesh_terms: D002574:Cervical Vertebrae; D003560:Cysts / Q000150:complications / Q000473:pathology*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D013117:Spinal Cord Compression / Q000209:etiology; D013118:Spinal Cord Diseases / Q000473:pathology*; D013904:Thoracic Vertebrae