Retroperitoneal paraganglioma in a child: resection and vena caval reconstruction.
Retroperitoneal paragangliomas (PG) are tumors of neuroectodermal origin rarely seen in children. A 10-year-old boy presented with back pain and a palpable mass secondary to a large right-sided retrocaval PG inferomedial to the kidney. Preoperative chemotherapy and perioperative embolisation were instigated to reduce tumor vascularity. En-bloc resection of the inferior vena cava below the left renal vein and above the caval bifurcation was achieved. Caval reconstruction was completed using a complex autograft of anterior uninvolved vena cava and right renal vein. At 4-year follow-up, the child remains tumor-free with normal caval flow and patency.
Bourke
C J
CJ
Department of Paediatric Surgery, University of Queensland, Royal Children's Hospital, Brisbane, Australia.
Lynch
S
S
Irving
H
H
Borzi
P A
PA
D002648:Child; D005263:Femoral Artery / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D010235:Paraganglioma / Q000601:surgery*; D011859:Radiography; D019651:Plastic Surgery Procedures; D012082:Renal Veins / Q000637:transplantation; D012186:Retroperitoneal Neoplasms / Q000601:surgery*; D014182:Transplantation, Autologous; D014682:Vena Cava, Inferior / Q000601:surgery* / Q000637:transplantation