title: [Peutz-Jeghers syndrome. Two case reports].
abstract: The Peutz jeghers syndrome is a familial affection with dominant autosomic transmission characterized by a hamartoma digestive polyposis and a cutaneous mucous lentiginosis with periorifice predominance. This affection represented 3 into 10% for the familial polyps. The digestive polyps constitute the must important part of the pentz jeghers syndrome because they determined to only the clinic manifestation and the disease prognostic with there complications: intestinal invaginations, haemorrhage. In this work, we report two observations of patients presented a Peurtz Jeghers syndrome, and we determine, after literature review the epidemiologic, pathogenic, clinic, anatomy pathologic, prognosis and therapeutics of this effection.
authors.affiliation: Service de Chirurgie Générale Hôpital Habib Bourguiba 3029 Sfax.
authors.forename: Wassim
authors.initials: W
authors.lastname: Kallel
authors.forename: Mohamed Akram
authors.initials: MA
authors.lastname: Mseddi
authors.forename: Mohamed Foued
authors.initials: MF
authors.lastname: Frikha
authors.forename: Rochdi
authors.initials: R
authors.lastname: Zouari
authors.forename: Issam
authors.initials: I
authors.lastname: Kachaou
authors.forename: Mohamed Issam
authors.initials: MI
authors.lastname: Beyrouti
mesh_terms: D000293:Adolescent; D000328:Adult; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000209:etiology; D006801:Humans; D007417:Intestinal Polyps / Q000150:complications / Q000209:etiology*; D010580:Peutz-Jeghers Syndrome / Q000150:complications / Q000473:pathology*; D011379:Prognosis