title: Epithelial cell chloride channel activity correlates with improved airway function in cystic fibrosis patients with the major mutant: Delta F508.
authors.affiliation: Programme in Structural Biology and Biochemistry, Research Institute, Hospital for Sick Children and Department of Biochemistry, Faculty of Medicine, Toronto, Canada M5G 1X8.
authors.forename: Jacqueline F
authors.initials: JF
authors.lastname: Kidd
authors.forename: Christine E
authors.initials: CE
authors.lastname: Bear
mesh_terms: D002712:Chlorides / Q000378:metabolism*; D003062:Codon / Q000235:genetics; D003550:Cystic Fibrosis / Q000235:genetics / Q000503:physiopathology*; D019005:Cystic Fibrosis Transmembrane Conductance Regulator / Q000235:genetics* / Q000502:physiology; D004847:Epithelial Cells / Q000378:metabolism; D005838:Genotype; D006031:Glycosylation; D006801:Humans; D017136:Ion Transport; D009297:Nasal Mucosa / Q000378:metabolism / Q000473:pathology; D017510:Protein Folding; D011499:Protein Processing, Post-Translational; D017384:Sequence Deletion
chemical_list: C505032:CFTR protein, human; D002712:Chlorides; D003062:Codon; D019005:Cystic Fibrosis Transmembrane Conductance Regulator