Maxillonasal dysplasia (Binder syndrome): a lateral cephalometric assessment.
Binder syndrome or maxillonasal dysplasia was first described by Binder in 1962, and is a disorder characterised by nasomaxillary hypoplasia. The records of 33 patients who had been diagnosed clinically with Binder syndrome at the Royal Children's Hospital of Melbourne were examined. Of these 33 patients, 14 were selected because they met the incusion criteria: that they had not had prior surgical and/or orthodontic treatment, and that high-quality lateral cephalometric radiographs were available. The craniofacial morphology of these patients was determined on lateral cephalometric radiographs and compared with published age- and sex-matched norms. In agreement with published studies, the anteroposterior lengths of the anterior cranial base and maxilla were reduced, and the majority of patients had a Class III skeletal relationship. Although the lower incisors tended to be prominent, both overjet and overbite 'ell within the ranges for the normal population. Despite the fact that the orthodontic and surgical treatment for patients with Binder syndrome is normally carried out within specialised units, clinicians should be aware of the variety of ways in which this condition may present.
Carach
Barbara
B
School of Dental Science, The University of Melbourne, Victoria, Australia.
Woods
Michael
M
Scott
Peter
P
D000293:Adolescent; D000328:Adult; D016022:Case-Control Studies; D002508:Cephalometry; D002648:Child; D005147:Facial Bones / Q000002:abnormalities*; D019066:Facies; D005260:Female; D006801:Humans; D008046:Lip / Q000002:abnormalities; D008297:Male; D008313:Malocclusion, Angle Class III / Q000473:pathology*; D019767:Maxillofacial Abnormalities / Q000473:pathology*; D009666:Nose / Q000002:abnormalities; D012189:Retrospective Studies; D012737:Sex Factors; D019291:Skull Base / Q000002:abnormalities; D013577:Syndrome; D014716:Vertical Dimension