Papillon-Lefevre syndrome: a report of two cases.
Papillon-Lefevre Syndrome (PLS) is an inherited autosomal recessive disorder presenting with Palmar plantar Keratoderma and Juvenile Periodontitis leading to early loss of both the dentitions. Two cases of PLS in a family with a history of consanguineous descent are presented.
Hegde
R
R
Department of Pediatric Dentistry, H.K.E.S.N Institute Of Dental Sciences, Gulbarga, Karnataka.
Reddy
R
R
D000293:Adolescent; D000328:Adult; D010520:Aggressive Periodontitis / Q000473:pathology; D003241:Consanguinity; D005260:Female; D005808:Genes, Recessive / Q000235:genetics; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000473:pathology; D008297:Male; D010214:Papillon-Lefevre Disease / Q000235:genetics* / Q000473:pathology; D016388:Tooth Loss / Q000473:pathology; D014086:Tooth Mobility / Q000473:pathology