Adrenal extramedullary hematopoiesis: report on a pediatric case and update of the literature.
The authors report on a rare pediatric case of adrenal extramedullary hematopoiesis in a patient with beta-thalassemia disease. The lesion was clinically discovered as incidentaloma of the right adrenal gland and treated by surgery. Adrenal extramedullary hematopoiesis may clinically be detected as incidentaloma. Adrenal incidentalomas presenting with hematologic disorders, such as agnogenic myeloid aplasia and beta-thalassemia, need careful imaging as well as adrenal hormonal investigation in order to exclude malignancy and subclinical hypersecretory syndromes. Ultrasound or CT-FNA of the lesion are effective in finding out the disease.
Porcaro
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AB
Department of Urology, University Hospital, Verona, Italy. drporcaro@yahoo.com
Novella
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G
Antoniolli
S Z
SZ
Martignoni
G
G
Brunelli
M
M
Curti
P
P
D000310:Adrenal Gland Neoplasms / Q000150:complications / Q000175:diagnosis*; D000311:Adrenal Glands / Q000502:physiology; D002648:Child; D017809:Fatal Outcome; D005260:Female; D006411:Hematopoiesis, Extramedullary; D006801:Humans; D033162:Incidental Findings; D017086:beta-Thalassemia / Q000150:complications