title: Congenital absence of the portal vein: clinical and radiologic findings.
abstract: Congenital absence of the portal vein (CAPV) is a rare anomaly in which the intestinal and splenic venous drainage bypasses the liver and drains into the systemic veins through various venous shunts. In patients with CAPV, the portosystemic shunting causes disruption of the enterohepatic circulation and leads to various clinical manifestations. CAPV can be diagnosed without invasive techniques. This article illustrates the clinical and radiologic findings (including ultrasound, CT, and MRI) of CAPV.
authors.affiliation: Department of Radiology, Kanagawa Children's Medical Center, Yokohama, Japan.
authors.forename: Tetsu
authors.initials: T
authors.lastname: Niwa
authors.forename: Noriko
authors.initials: N
authors.lastname: Aida
authors.forename: Katsuhiko
authors.initials: K
authors.lastname: Tachibana
authors.forename: Masato
authors.initials: M
authors.lastname: Shinkai
authors.forename: Youkatsu
authors.initials: Y
authors.lastname: Ohhama
authors.forename: Kazutoshi
authors.initials: K
authors.lastname: Fujita
authors.forename: Aya
authors.initials: A
authors.lastname: Abe
authors.forename: Jin
authors.initials: J
authors.lastname: Lee
authors.forename: Yukihiko
authors.initials: Y
authors.lastname: Ozawa
authors.forename: Tomio
authors.initials: T
authors.lastname: Inoue
mesh_terms: D000328:Adult; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000473:pathology*