title: Fatal cardiovascular complications in a patient with Ehlers-Danlos syndrome type IV and dextrocardia.
abstract: A report is presented of a 31 year female patient with Ehlers-Danlos syndrome type IV who presented a bilateral renal artery dissection and a hematoma of the ascending aorta simultaneously. She had had an uneventful delivery six months before. We also discovered a situs solitus with dextrocardia in this patient. These complications were managed conservatively. Unfortunately the patient died of a pulmonary infection and a multi-organ failure syndrome several days after her admission.
authors.affiliation: Service de Chirurgie Cardio-vasculaire, 2 Bd Maréchal de Lattre de Tassigny, BP 1542, 21034 Dijon Cedex, France. saed.jazayeri@chu-dijon.fr
authors.forename: S
authors.initials: S
authors.lastname: Jazayeri
authors.forename: M C
authors.initials: MC
authors.lastname: Gomez
authors.forename: E
authors.initials: E
authors.lastname: Tatou
authors.forename: M
authors.initials: M
authors.lastname: Saleh
authors.forename: J P
authors.initials: JP
authors.lastname: Parthiot
authors.forename: R
authors.initials: R
authors.lastname: Brenot
authors.forename: M
authors.initials: M
authors.lastname: David
mesh_terms: D000328:Adult; D000784:Aortic Dissection / Q000175:diagnosis* / Q000000981:diagnostic imaging; D001018:Aortic Diseases / Q000000981:diagnostic imaging; D003914:Dextrocardia / Q000175:diagnosis* / Q000000981:diagnostic imaging; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000175:diagnosis*; D017809:Fatal Outcome; D005260:Female; D006406:Hematoma / Q000000981:diagnostic imaging; D006801:Humans; D011859:Radiography; D012077:Renal Artery / Q000000981:diagnostic imaging; D014463:Ultrasonography