Biliary atresia associated with a fatty acid oxidation defect.
Matthews
Randolph P
RP
Department of Pediatrics, Division of Gastroenterology and Nutrition and Fred and Suzanne Biesecker Liver Center, Philadelphia, Pennsylvania, USA.
Russo
Pierre
P
Berry
Gerard T
GT
Piccoli
David A
DA
Rand
Elizabeth B
EB
D015094:3-Hydroxyacyl CoA Dehydrogenases / Q000172:deficiency*; D001656:Biliary Atresia / Q000150:complications / Q000201:enzymology* / Q000378:metabolism / Q000628:therapy; D005227:Fatty Acids / Q000378:metabolism*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008099:Liver / Q000378:metabolism / Q000473:pathology; D008103:Liver Cirrhosis / Q000209:etiology; D016031:Liver Transplantation; D008297:Male; D010084:Oxidation-Reduction; D011171:Portoenterostomy, Hepatic
D005227:Fatty Acids; D015094:3-Hydroxyacyl CoA Dehydrogenases