Fatal cardiovascular complications in a patient with Ehlers-Danlos syndrome type IV and dextrocardia.
A report is presented of a 31 year female patient with Ehlers-Danlos syndrome type IV who presented a bilateral renal artery dissection and a hematoma of the ascending aorta simultaneously. She had had an uneventful delivery six months before. We also discovered a situs solitus with dextrocardia in this patient. These complications were managed conservatively. Unfortunately the patient died of a pulmonary infection and a multi-organ failure syndrome several days after her admission.
Jazayeri
S
S
Service de Chirurgie Cardio-vasculaire, 2 Bd Maréchal de Lattre de Tassigny, BP 1542, 21034 Dijon Cedex, France. saed.jazayeri@chu-dijon.fr
Gomez
M C
MC
Tatou
E
E
Saleh
M
M
Parthiot
J P
JP
Brenot
R
R
David
M
M
D000328:Adult; D000784:Aortic Dissection / Q000175:diagnosis* / Q000000981:diagnostic imaging; D001018:Aortic Diseases / Q000000981:diagnostic imaging; D003914:Dextrocardia / Q000175:diagnosis* / Q000000981:diagnostic imaging; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000175:diagnosis*; D017809:Fatal Outcome; D005260:Female; D006406:Hematoma / Q000000981:diagnostic imaging; D006801:Humans; D011859:Radiography; D012077:Renal Artery / Q000000981:diagnostic imaging; D014463:Ultrasonography