Erdheim-Chester disease.
BACKGROUND
Erdheim-Chester disease is a rare non-Langerhans' cell histiocytosis.


OBJECTIVE
This case report is presented to familiarize clinicians with Erdheim-Chester disease and its differential diagnosis.


CONCLUSIONS
Erdheim-Chester disease presents with unique clinical and pathologic findings. Its xanthoma-like lesions can cause significant morbidity and mortality.
Lenahan
Susan E
SE
Department of Pathology, The Milton S. Hershey Medical Center, Penn State University, Hershey, Pennsylvania, USA.
Helm
Klaus F
KF
Hopper
Kenneth D
KD
D000328:Adult; D003937:Diagnosis, Differential; D031249:Erdheim-Chester Disease / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed