[Cholangiocarcinoma developing in von Meyenburg complexes in haemochromatosis].
A 63-year-old man with genetic haemochromatosis underwent resection of a cholangiocarcinoma that developed in von Meyenburg complexes; the liver was not cirrhotic. Patients with an association of genetic haemochromatosis and von Meyenburg complexes might have a predisposition to cholangiocarcinoma, even before cirrhosis occurs. Patients with this association should undergo regular and early hepatic surveillance of hemochromatosis.
Wisniewski
Benjamin
B
Service d'Hépato-Gastroentérologie, Centre Hospitalier Intercommunal de Villeneuve-Saint-Georges, France.
Tordjman
Gilles
G
Tran Van Nhieu
Jeanne
J
Bettan
Louis
L
Courillon-Mallet
Anne
A
D001649:Bile Duct Diseases / Q000150:complications* / Q000473:pathology; D001650:Bile Duct Neoplasms / Q000209:etiology* / Q000473:pathology; D001653:Bile Ducts, Intrahepatic / Q000473:pathology; D018281:Cholangiocarcinoma / Q000209:etiology* / Q000473:pathology; D006222:Hamartoma / Q000150:complications* / Q000473:pathology; D006432:Hemochromatosis / Q000150:complications* / Q000235:genetics / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D012307:Risk Factors