Congenital absence of the portal vein: clinical and radiologic findings.
Congenital absence of the portal vein (CAPV) is a rare anomaly in which the intestinal and splenic venous drainage bypasses the liver and drains into the systemic veins through various venous shunts. In patients with CAPV, the portosystemic shunting causes disruption of the enterohepatic circulation and leads to various clinical manifestations. CAPV can be diagnosed without invasive techniques. This article illustrates the clinical and radiologic findings (including ultrasound, CT, and MRI) of CAPV.
Niwa
Tetsu
T
Department of Radiology, Kanagawa Children's Medical Center, Yokohama, Japan.
Aida
Noriko
N
Tachibana
Katsuhiko
K
Shinkai
Masato
M
Ohhama
Youkatsu
Y
Fujita
Kazutoshi
K
Abe
Aya
A
Lee
Jin
J
Ozawa
Yukihiko
Y
Inoue
Tomio
T
D000328:Adult; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000473:pathology*