Von Recklinghausen neurofibromatosis with palatal localization. Diagnostic and surgical problems in two clinical cases.
This paper illustrates the clinical findings and aims at report surgical matters observed in 2 patients affected by neurofibromatosis type I with a rare palatal localization. By means of retrospective analysis 2 cases of neurofibromatosis type I with a palatal mass are selected. Both cases were surgically treated and underwent 12 months follow-up. Patients underwent surgical removal of the palatal neurofibroma. At 12 months follow-up a good local condition without any recurrence was observed. Malignant transformation was very rarely reported in oral neurofibromata and can follow incomplete removal. Surgical treatment of neurofibromata requires the sacrifice of the nerve trunk from where they originate, together with the complete removal of the mass with security margins. Therefore, risks and benefits from surgery should be carefully weighted in each patient and where surgery is not performed clinical and radiographic trials are advisable.
Becelli
R
R
Department of Maxillo-Facial Surgery, University of Rome La Sapienza, Rome.
Renzi
G
G
Cerulli
G
G
Saltarel
A
A
Perugini
M
M
D000293:Adolescent; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008409:Mastication; D009456:Neurofibromatosis 1 / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D010157:Palatal Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D011859:Radiography; D014832:Voice Disorders / Q000209:etiology