Gorham-Stout disease of the shoulder girdle and cervico-thoracic spine: fatal course in a 65-year-old woman.
A case of Gorham-Stout disease of the shoulder girdle and cervico-thoracic spine in a 65-year-old woman is described. The patient presented with progressive neurologic symptoms, pain, and deformities of the cervico-thoracic spine as well as of her left shoulder following a traumatic shoulder luxation. Since the patient had a history of uterine carcinoma, the current disease was clinically difficult to differentiate from osteolytic metastases. The results of the clinical, radiological and histopathologic examination leading to the diagnosis of Gorham-Stout disease are described. Neither attempted surgery nor radiotherapy produced clinical improvement and the patient died 1 year after the first clinical evaluation.
Bode-Lesniewska
B
B
Department of Pathology, University Hospital, Schmelzbergstrasse 12, 8091 Zurich, Switzerland. beata.bode@pty.usz.ch
von Hochstetter
A
A
Exner
G U
GU
Hodler
J
J
D000368:Aged; D002574:Cervical Vertebrae / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D010015:Osteolysis, Essential / Q000175:diagnosis* / Q000628:therapy; D012785:Shoulder Joint / Q000473:pathology; D013904:Thoracic Vertebrae / Q000473:pathology; D014057:Tomography, X-Ray Computed