Systemic capillary leak syndrome.
Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock attributable to increased systemic capillary leakage. A 46-year-old man was admitted to our hospital because of recurrent episodes of generalized edema with hypovolemic shock. Blood laboratory data revealed severe hypoproteinemia with a small monoclonal IgG-kappa protein. These findings suggested strongly the diagnosis of SCLS. A regimen with steroid pulse therapy was tried; however, intravascular overloading accompanied by the recruitment of the initially extravasated fluids resulted in acute pulmonary edema. Intensive care and careful monitoring of fluid volume are required in SCLS.
Chihara
Ruri
R
Department of Nephrology, Saitama Medical School, Iruma-gun, Saitama.
Nakamoto
Hidetomo
H
Arima
Hiroshi
H
Moriwaki
Kenshi
K
Kanno
Yoshihiko
Y
Sugahara
Soichi
S
Okada
Hirokazu
H
Suzuki
Hiromichi
H
D019559:Capillary Leak Syndrome / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008297:Male; D008875:Middle Aged