Forty-one year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: cerebellar atrophy, multiphasic relapses, and response to IVIG.
We report on an adult with opsoclonus-myoclonus-ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described.
Pranzatelli
Michael R
MR
The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine, Springfield, Illinois 62702, USA. mpranzatelli@siumed.edu
Tate
Elizabeth D
ED
Kinsbourne
Marcel
M
Caviness
Verne S
VS
Mishra
Bibhuti
B
D000293:Adolescent; D000324:Adrenocorticotropic Hormone / Q000627:therapeutic use; D000328:Adult; D001284:Atrophy; D002524:Cerebellar Ataxia / Q000175:diagnosis / Q000188:drug therapy*; D002531:Cerebellum / Q000473:pathology*; D002648:Child; D002675:Child, Preschool; D005500:Follow-Up Studies; D006801:Humans; D007116:Immunization, Passive; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D009460:Neurologic Examination; D009483:Neuropsychological Tests; D020361:Paraneoplastic Syndromes, Nervous System / Q000175:diagnosis / Q000188:drug therapy*; D012008:Recurrence; D016896:Treatment Outcome
D000324:Adrenocorticotropic Hormone