Hemichorea as an initial manifestation of moyamoya disease: reversible striatal hypoperfusion demonstrated on single photon emission computed tomography.
We describe a case with unilateral moyamoya disease that showed progressive hemichorea as an initial manifestation. Single photon emission computed tomography showed perfusion defect in the contralateral basal ganglia although magnetic resonance imaging was unremarkable. Hemichorea improved along with normalization of perfusion after bypass surgery, suggestive of striatal hypoperfusion as the cause of hemichorea.
Hong
Yoon-Ho
YH
Department of Neurology, Clinical Research Institute, Seoul National University Hospital, SNUMRC, College of Medicine, Seoul National University, Seoul, South Korea.
Ahn
Tae-Beom
TB
Oh
Chang Wan
CW
Jeon
Beom S
BS
D000328:Adult; D002545:Brain Ischemia / Q000000981:diagnostic imaging* / Q000601:surgery; D016893:Carotid Stenosis / Q000000981:diagnostic imaging / Q000601:surgery; D002548:Cerebral Revascularization; D002819:Chorea / Q000000981:diagnostic imaging* / Q000601:surgery; D003342:Corpus Striatum / Q000098:blood supply* / Q000000981:diagnostic imaging; D004292:Dominance, Cerebral / Q000502:physiology; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D009072:Moyamoya Disease / Q000000981:diagnostic imaging* / Q000601:surgery; D015899:Tomography, Emission-Computed, Single-Photon