Intrathoracic desmoid tumor with invasion of the great vessels.
A desmoid tumor of the mediastinum was diagnosed and treated in a 35-year-old white male who presented with a right supraclavicular mass. He was treated with resection, which involved several vascular structures, requiring multiple vascular reconstructions followed by post-operative radiotherapy. The authors concluded that, when located in the mediastinum, the invasive character of such tumors and its tendency to recur may pose a considerable surgical challenge, requiring careful pre-operative planning and long term post-operative follow -up. The role of radiation therapy is limited to the control of local recurrences.
Cardoso
P F G
PF
Department of Surgery, Division of Thoracic Surgery, Santa Casa de Misericórdia de Porto Alegre (ISCMPA)-Fundacao Faculdade Federal de Ciencias Medicas de Porto Alegre, Porto Alegre, Brazil. cardoso@via-rs.net
da Silva
L C C
LC
Bonamigo
T P
TP
Geyer
G
G
D000328:Adult; D001013:Aorta, Thoracic / Q000473:pathology; D018222:Desmoid Tumors / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008297:Male; D008479:Mediastinal Neoplasms / Q000473:pathology / Q000601:surgery*; D009361:Neoplasm Invasiveness; D014683:Vena Cava, Superior / Q000473:pathology