Patient with Sotos syndrome, Wolff-Parkinson-White pattern on electrocardiogram, and two right-sided accessory bypass tracts.
Sotos syndrome is a growth regulation disorder. Accessory conduction pathways, the anatomical structures responsible for Wolff-Parkinson-White syndrome, are thought to result from developmental failure to eradicate the remnants of the atrioventricular connections during cardiogenesis. Although the reported prevalence of congenital heart disease in Sotos syndrome is 10 times higher than in the general population, there are no reported cases with ventricular pre-excitation. We report a patient with Sotos syndrome with two distinct accessory atrioventricular bypass tracts documented by invasive electrophysiology testing and a curative catheter ablation procedure.
Sharma
Param P
PP
Division of Cardiology, Marshfield Clinic, Marshfield, Wisconsin 54449, USA. Sharmap@mfldclin.edu
Vidaillet
Humberto
H
Dietz
Julie
J
D000293:Adolescent; D001283:Atrioventricular Node / Q000002:abnormalities* / Q000601:surgery; D004562:Electrocardiography; D004594:Electrophysiology; D006329:Heart Conduction System / Q000002:abnormalities*; D006330:Heart Defects, Congenital / Q000209:etiology; D006801:Humans; D008297:Male; D014927:Wolff-Parkinson-White Syndrome / Q000473:pathology* / Q000503:physiopathology