Congenital aortic regurgitation due to absent aortic cusps and high-degree mitral stenosis.
Congenital absence of aortic cusps leads to severe aortic regurgitation. We present a newborn with this rare entity with extreme mitral stenosis. Hemodynamic features were those of hypoplastic left heart syndrome. Surgical management consisted of initial modified Norwood procedure followed by orthotopic heart transplantation.
Krasemann
T
T
Department of Pediatric Cardiology, University Children's Hospital Muenster, Albert-Schweitzer-Strasse 33, D-48149 Muenster, Germany.
Kehl
H G
HG
Hammel
D
D
Asfour
B
B
D001022:Aortic Valve Insufficiency / Q000150:complications / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D016027:Heart Transplantation; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D008946:Mitral Valve Stenosis / Q000150:complications / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D012086:Reoperation; D016896:Treatment Outcome