title: Presentation of Degos syndrome as acute small-bowel perforation.
abstract: Malignant atrophic papulosis is an uncommon vasculopathy affecting multiple systems and frequently associated with a poor prognosis. We describe a 56-year-old patient with this rare disorder whose death was the result of intestinal involvement. Clinical diagnostic features of malignant atrophic papulosis as well as the main therapeutic approaches suggested in the literature are presented herein.
authors.affiliation: Department of Surgery, Hospital General Vega Baja, Servicio de Cirugía General, Murcia, Spain. migova@terra.es
authors.forename: Francisco Miguel
authors.initials: FM
authors.lastname: González Valverde
authors.forename: Francisco
authors.initials: F
authors.lastname: Menarguez Pina
authors.forename: Jose Antonio
authors.initials: JA
authors.lastname: Ruiz
authors.forename: Maria Jesus
authors.initials: MJ
authors.lastname: Gómez Ramos
authors.forename: Francisco
authors.initials: F
authors.lastname: Mauri Barbera
authors.forename: Paloma
authors.initials: P
authors.lastname: Luri Prieto
authors.forename: Jose Antonio
authors.initials: JA
authors.lastname: García Marcilla
authors.forename: Jose Luis
authors.initials: JL
authors.lastname: Vázquez Rojas
mesh_terms: D000208:Acute Disease; D003937:Diagnosis, Differential; D013505:Digestive System Surgical Procedures; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007416:Intestinal Perforation / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D007421:Intestine, Small; D008875:Middle Aged; D017445:Skin Diseases, Vascular / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy*