Presentation of Degos syndrome as acute small-bowel perforation.
Malignant atrophic papulosis is an uncommon vasculopathy affecting multiple systems and frequently associated with a poor prognosis. We describe a 56-year-old patient with this rare disorder whose death was the result of intestinal involvement. Clinical diagnostic features of malignant atrophic papulosis as well as the main therapeutic approaches suggested in the literature are presented herein.
González Valverde
Francisco Miguel
FM
Department of Surgery, Hospital General Vega Baja, Servicio de Cirugía General, Murcia, Spain. migova@terra.es
Menarguez Pina
Francisco
F
Ruiz
Jose Antonio
JA
Gómez Ramos
Maria Jesus
MJ
Mauri Barbera
Francisco
F
Luri Prieto
Paloma
P
García Marcilla
Jose Antonio
JA
Vázquez Rojas
Jose Luis
JL
D000208:Acute Disease; D003937:Diagnosis, Differential; D013505:Digestive System Surgical Procedures; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007416:Intestinal Perforation / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D007421:Intestine, Small; D008875:Middle Aged; D017445:Skin Diseases, Vascular / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy*