title: Primary malignant fibrous histiocytoma of the small intestine presenting as an intussusception: report of a case.
abstract: Malignant fibrous histiocytoma occurs most commonly in the extremities and trunk, but rarely in the visceral organs. Malignant fibrous histiocytoma of the small intestine is an extremely rare condition. To our knowledge, only ten cases of primary tumors involving the small intestine have been described up to now. Among them only one case has been reported to lead to intussusception. This case report documents the appearance of a storiform-pleomorphic type primary malignant fibrous histiocytoma of the ileum, which led to intussusception, in a 58-year-old man with a 3-month history of dyspepsia, weight loss, general fatigue, and nonspecific abdominal pain. The patient was well with no sign of disease at 8 months after surgery. The clinical and pathologic characteristics of malignant fibrous histiocytoma of the small intestine as found in the literature are also reviewed.
authors.affiliation: Department of Surgery, Yüzüncü Yil University School of Medicine, YYU Tip Fakültesi, Genel Cerrahi AD, 65200 Van, Turkey.
authors.forename: Cetin
authors.initials: C
authors.lastname: Kotan
authors.forename: Mustafa
authors.initials: M
authors.lastname: Kosem
authors.forename: Süleyman
authors.initials: S
authors.lastname: Alici
authors.forename: Mahmut
authors.initials: M
authors.lastname: Ilhan
authors.forename: Ilyas
authors.initials: I
authors.lastname: Tuncer
authors.forename: Mustafa
authors.initials: M
authors.lastname: Harman
mesh_terms: D018219:Histiocytoma, Benign Fibrous / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007078:Ileal Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D007443:Intussusception / Q000209:etiology*; D008297:Male; D008875:Middle Aged; D011379:Prognosis