title: Absent pulmonary valve syndrome with intact ventricular septum and patent ductus arteriosus: report of two cases and a short review of the literature.
abstract: We describe two patients who both presented shortly after birth with congestive heart failure due to an absent pulmonary valve and patent ductus arteriosus. Diagnostic evaluation revealed in both cases an aneurysmatic dilation of the pulmonary vascular tree and an abundant left-to-right shunt over a large patent ductus arteriosus. Ventricular septal defects were not detected. Early surgical closure of the patent ductus arteriosus improved the hemodynamic situation so that implantation of a homograft valve could be delayed.
authors.affiliation: Department of Pediatric Intensive Care, University Medical Center St. Radboud, Nijmegen, The Netherlands. hgrotenhuis@hotmail.com
authors.forename: Heynric B
authors.initials: HB
authors.lastname: Grotenhuis
authors.forename: Aagje
authors.initials: A
authors.lastname: Nijveld
authors.forename: Ad
authors.initials: A
authors.lastname: Backx
mesh_terms: D004374:Ductus Arteriosus, Patent / Q000150:complications* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities*