title: [Central agenesis of the hand].
abstract: Central aplasia represent under 10% of congenital malformations of the hand. It is characterised by the partial or complete absence of the median ray. We adopted the classification of Swanson and considered this anomaly a stop of median longitudinal development. We separate 2 groups: Hand in folk: the aplasia interested only the median digits, all metacarpal are present. Hand in lobster's pincer: all median rays are absent including the metacarpal. We report a set of 16 children carriers of 23 central aplasia of the hand, it was about 14 hands in lobster'pincer and 9 hands in folk. In any case, the gene was merely aesthetic, the hand's function was complete. A child has been operated, and benefitted a closing of the median crack defect, he had a free thumb. For the other cases, abstention has been decided, indeed to close this cracks deprive these hands of a first corner the alone present.
authors.forename: Moez
authors.initials: M
authors.lastname: Turki
authors.forename: Mehdi
authors.initials: M
authors.lastname: Daghfous
authors.forename: Khalil
authors.initials: K
authors.lastname: Ennouri
authors.forename: Faouzi
authors.initials: F
authors.lastname: Khalfaoui
authors.forename: Sayed
authors.initials: S
authors.lastname: Baccari
authors.forename: Lamjed
authors.initials: L
authors.lastname: Tarhouni
authors.forename: Hichem
authors.initials: H
authors.lastname: Bahri
mesh_terms: D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006228:Hand Deformities, Congenital / Q000145:classification / Q000000981:diagnostic imaging / Q000196:embryology / Q000235:genetics* / Q000601:surgery*; D018737:Hand Strength; D006801:Humans; D008297:Male; D010375:Pedigree; D011859:Radiography; D016059:Range of Motion, Articular; D013524:Surgical Flaps; D016896:Treatment Outcome