Mediastinal cavernous haemangioma in a patient with Klippel-Trenaunay syndrome.
The Klippel-Trenaunay syndrome (KTS) is a rare syndrome characterised by the triad of varicose veins, bony and soft tissue hypertrophy, and cutaneous haemangioma. A 30 year old man with KTS with a right mediastinal mass which progressively enlarged over 5 years is described. Computed tomography, magnetic resonance imaging, and bronchial angiography revealed a vascular lesion in the azygous area. After complete excision of the mass, histological examination revealed cavernous haemangioma. To our knowledge, this is the first report of intrathoracic haemangioma in KTS.
Kuo
P-H
PH
Department of Internal Medicine, National Taiwan University Hospital, Taipei, Taiwan.
Chang
Y-C
YC
Liou
J-H
JH
Lee
J-M
JM
D000328:Adult; D006392:Hemangioma, Cavernous / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D008479:Mediastinal Neoplasms / Q000175:diagnosis / Q000209:etiology*; D014057:Tomography, X-Ray Computed / Q000379:methods