title: Auditory brainstem implant in bilateral and completely ossified cochleae.
abstract: OBJECTIVE
  To report and evaluate the results of auditory brainstem implantation in a case of postmeningitis hearing loss with totally ossified cochleae on both sides.
  
  
  METHODS
  Case report.
  
  
  METHODS
  Tertiary referral center.
  
  
  METHODS
  A 49-year-old man was referred to the authors' department for bilateral total hearing loss subsequent to bacterial meningitis 2 years earlier. Pure tone audiometry, auditory brainstem response tests, and promontory tests did not reveal any cochlear activity. Computed tomography showed bilateral and totally ossified cochleae. Magnetic resonance imaging confirmed the diagnosis by showing no cochlear signal on T2-weighed images and ruled out brainstem and cerebellopontine angle abnormalities.
  
  
  METHODS
  A left auditory brainstem implantation was performed through a translabyrinthine route, using a Nucleus 22-channel device.
  
  
  METHODS
  Word and sentence recognition tests in sound-only and sound plus vision modes.
  
  
  RESULTS
  No postoperative complication was observed. Twelve electrodes could be activated, and their tonotopy was defined. Nine other electrodes were inactivated because of an absence of auditory response (4 electrodes) or paresthesia (5 electrodes). At the last follow-up visit, 26 months after the implantation, 50% of disyllabic word scores and 60% of sentence scores were achieved using auditory brainstem implant sound only. These scores reached 80% and 93%, respectively, with lip-reading.
  
  
  CONCLUSIONS
  Auditory brainstem implantation is an efficient means of auditory rehabilitation in cases of bilateral total hearing loss with totally ossified cochleae. It should be considered in cases of predictable failure in cochlear implantation.
authors.affiliation: Department of Otolaryngology-Head and Neck Surgery, Hôpital Beaujon AP-HP and Faculté Xavier Bichat, INSERM, Université Paris, France. alexis.bozorg-grayeli@bjn.ap-hop-paris.fr
authors.forename: Alexis Bozorg
authors.initials: AB
authors.lastname: Grayeli
authors.forename: Didier
authors.initials: D
authors.lastname: Bouccara
authors.forename: Michel
authors.initials: M
authors.lastname: Kalamarides
authors.forename: Emmanuelle
authors.initials: E
authors.lastname: Ambert-Dahan
authors.forename: Christelle
authors.initials: C
authors.lastname: Coudert
authors.forename: Françoise
authors.initials: F
authors.lastname: Cyna-Gorse
authors.forename: Wolfgang-Peter
authors.initials: WP
authors.lastname: Sollmann
authors.forename: Alain
authors.initials: A
authors.lastname: Rey
authors.forename: Olivier
authors.initials: O
authors.lastname: Sterkers
mesh_terms: D001933:Brain Stem / Q000503:physiopathology / Q000601:surgery*; D015834:Cochlear Diseases / Q000503:physiopathology / Q000534:rehabilitation*; D019929:Cochlear Implantation / Q000379:methods*; D003638:Deafness / Q000503:physiopathology / Q000534:rehabilitation*; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D016920:Meningitis, Bacterial / Q000150:complications*; D008875:Middle Aged; D009999:Ossification, Heterotopic / Q000503:physiopathology / Q000534:rehabilitation*; D011183:Postoperative Complications / Q000503:physiopathology*; D011474:Prosthesis Design; D013067:Speech Perception / Q000502:physiology*; D014057:Tomography, X-Ray Computed