[Right mid-ventricular stenosis with intact interventricular septum].
Pure infundibular stenosis of the right ventricle is a rare congenital anomaly. Right midventricular stenosis with intact interventricular septum is even rarer. It consists of obstruction of the trabecular zone of the right ventricle by a hypertrophied moderator band with or without abnormal muscle bundles. This anomaly can now be diagnosed by transthoracic echocardiography, while haemodynamic and angiographic diagnosis is reserved for doubtful cases. Two cases of midventricular stenosis are reported. In both patients, the diagnosis was suspected bu ultrasonography which showed a right intraventricular gradient of about 80 mmHg without identifying the exact site (infundibular or midventricular). The diagnosis was corrected by the operative findings. A good postoperative course was observed for both patients.
Kraiem
S
S
Service de Cardiologie, Hôpital Habib Thameur, Tunis, Tunisie.
Lahidheb
D
D
Ben Ameur
Y
Y
Chehaibi
N
N
Slimane
M L
ML
D000293:Adolescent; D003251:Constriction, Pathologic; D017023:Coronary Angiography; D004417:Dyspnea / Q000145:classification / Q000209:etiology; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006346:Heart Septum; D006439:Hemodynamics; D006801:Humans; D008297:Male; D012720:Severity of Illness Index; D016896:Treatment Outcome; D014694:Ventricular Outflow Obstruction / Q000151:congenital* / Q000175:diagnosis* / Q000601:surgery; D017725:Ventricular Pressure