Severe unilateral pulmonary vascular changes in child with polysplenia.
A 12-year-old boy with polysplenia and single ventricle experienced recurrent episodes of pneumonia, hemoptysis, and pulmonary hypertension. Unilateral pulmonary vein obstruction was diagnosed, and a left pneumonectomy was performed. Microscopy of the resected specimen revealed pulmonary veno-occlusive disease in the small pulmonary venules, and old arteritis in the small pulmonary arteries.
Maeda
Katsuhide
K
Department of Cardiothoracic Surgery, Faculty of Medicine, University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan. maedak-tky@umin.ac.jp
Yamaki
Shigeo
S
Murakami
Arata
A
Nakajima
Jun
J
Hishi
Toshio
T
Takamoto
Shinichi
S
D001167:Arteritis / Q000150:complications* / Q000473:pathology* / Q000601:surgery; D002648:Child; D006469:Hemoptysis / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D008297:Male; D011013:Pneumonectomy; D011014:Pneumonia / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D011651:Pulmonary Artery / Q000473:pathology* / Q000601:surgery; D011652:Pulmonary Circulation; D011668:Pulmonary Veno-Occlusive Disease / Q000150:complications* / Q000473:pathology* / Q000601:surgery; D012720:Severity of Illness Index; D013158:Splenic Diseases / Q000150:complications* / Q000473:pathology* / Q000601:surgery