[Landau-Kleffner syndrome (acquired epileptic aphasia)].
Landau-Kleffner syndrome is characterized by a complex group of symptoms including deterioration in language skills, seizures, and abnormal electroencephalography findings. A six-year-old male patient had aphasia for three years and generalized tonic-clonic epileptic seizures for two years. Pure-tone audiometry and auditory brain-stem response audiometry findings were normal. He had verbal auditory agnosia rather than true aphasia. Cranial computed tomography and magnetic resonance imaging studies did not show any abnormal findings. Single-photon emission computed tomography showed hypoperfusion in the right hemispheric temporal lobe. Despite treatment with corticosteroids and intravenous immunoglobulins, multiple exacerbations were interspersed in a four-year follow-up period.
Erdem
Tamer
T
Department of Otolaryngology, Medicine Faculty of Inönü University, 44100 Malatya, Turkey. tamerdem@hotmail.com
Kirazli
Tayfun
T
Tütüncüoğlu
Sarenur
S
D000377:Agnosia / Q000150:complications; D001301:Audiometry, Pure-Tone; D002648:Child; D003937:Diagnosis, Differential; D004569:Electroencephalography; D016057:Evoked Potentials, Auditory, Brain Stem; D006801:Humans; D018887:Landau-Kleffner Syndrome / Q000150:complications / Q000175:diagnosis* / Q000503:physiopathology; D008297:Male; D013702:Temporal Lobe / Q000098:blood supply; D015899:Tomography, Emission-Computed, Single-Photon