title: A case of unilateral, systematized linear hair follicle nevi associated with epidermal nevus-like lesions.
abstract: Multiple hair follicle nevi are an extremely rare condition. In 1998, a case of unilateral multiple hair follicle nevi, ipsilateral alopecia and ipsilateral leptomeningeal angiomatosis of the brain was first reported from Japan. Very recently, hair follicle nevus in a distribution following Blaschko's lines has also been reported. In this paper, we observed a congenital case of unilateral, systematized linear hair follicle nevi associated with congenital, ipsilateral, multiple plaque lesions resembling epidermal nevi but lacking leptomeningeal angiomatosis of the brain. These cases implicate the possibility of a novel neurocutaneous syndrome. Additional cases should be sought in order to determine whether this condition is pathophysiologically distinct.
authors.affiliation: Department of Dermatology, Juntendo University School of Medicine, Tokyo, Japan. ikeda@med.juntendo.ac.jp
authors.forename: Shigaku
authors.initials: S
authors.lastname: Ikeda
authors.forename: Juri
authors.initials: J
authors.lastname: Kawada
authors.forename: Hitoshi
authors.initials: H
authors.lastname: Yaguchi
authors.forename: Hideoki
authors.initials: H
authors.lastname: Ogawa
mesh_terms: D004817:Epidermis / Q000473:pathology; D005260:Female; D006201:Hair Diseases / Q000151:congenital / Q000473:pathology; D018859:Hair Follicle / Q000473:pathology; D006801:Humans; D007223:Infant; D009378:Neoplasms, Multiple Primary / Q000151:congenital* / Q000473:pathology; D009506:Nevus / Q000150:complications / Q000151:congenital*; D012878:Skin Neoplasms / Q000150:complications / Q000151:congenital* / Q000473:pathology