title: Recurrent syncope in a young patient with long QT syndrome: possible relationship of atrioventricular nodal re-entrant tachycardia with neurally mediated spells?
abstract: This is a case of a 15-year-old woman with long QT syndrome (LQTS) and a history of 14 events of syncope, demonstrating that the underlying mechanism for any symptomatic episode is not necessarily based on torsades de pointes. The need for careful distinction between true ventricular tachyarrhythmia and other forms of supraventricular tachycardia in the LQTS is the subject of the article. To the knowledge of the authors, this is the first reported case of an association of LQTS with AV nodal re-entrant tachycardia.
authors.affiliation: Herzzentrum Wuppertal, Universität Witten/Herdecke, Medizinische Klinik 3, Kardiologie, Arrenberger Str. 20, D-42117 Wuppertal, Germany. mhorlitz@hotmail.com
authors.forename: Marc
authors.initials: M
authors.lastname: Horlitz
authors.forename: Phillip
authors.initials: P
authors.lastname: Schley
authors.forename: Roger
authors.initials: R
authors.lastname: Marx
authors.forename: Michael
authors.initials: M
authors.lastname: Klein
authors.forename: Alexander
authors.initials: A
authors.lastname: Bufe
authors.forename: Harald
authors.initials: H
authors.lastname: Lapp
authors.forename: Ingo
authors.initials: I
authors.lastname: Krakau
authors.forename: Hartmut
authors.initials: H
authors.lastname: Gülker
authors.forename: Wilhelm
authors.initials: W
authors.lastname: Haverkamp
mesh_terms: D000293:Adolescent; D002304:Cardiac Pacing, Artificial; D017115:Catheter Ablation; D003937:Diagnosis, Differential; D004562:Electrocardiography; D015716:Electrocardiography, Ambulatory; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008133:Long QT Syndrome / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D019462:Syncope, Vasovagal / Q000175:diagnosis / Q000209:etiology* / Q000235:genetics; D013611:Tachycardia, Atrioventricular Nodal Reentry / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D016171:Torsades de Pointes / Q000175:diagnosis / Q000235:genetics