Recurrent syncope in a young patient with long QT syndrome: possible relationship of atrioventricular nodal re-entrant tachycardia with neurally mediated spells?
This is a case of a 15-year-old woman with long QT syndrome (LQTS) and a history of 14 events of syncope, demonstrating that the underlying mechanism for any symptomatic episode is not necessarily based on torsades de pointes. The need for careful distinction between true ventricular tachyarrhythmia and other forms of supraventricular tachycardia in the LQTS is the subject of the article. To the knowledge of the authors, this is the first reported case of an association of LQTS with AV nodal re-entrant tachycardia.
Horlitz
Marc
M
Herzzentrum Wuppertal, Universität Witten/Herdecke, Medizinische Klinik 3, Kardiologie, Arrenberger Str. 20, D-42117 Wuppertal, Germany. mhorlitz@hotmail.com
Schley
Phillip
P
Marx
Roger
R
Klein
Michael
M
Bufe
Alexander
A
Lapp
Harald
H
Krakau
Ingo
I
Gülker
Hartmut
H
Haverkamp
Wilhelm
W
D000293:Adolescent; D002304:Cardiac Pacing, Artificial; D017115:Catheter Ablation; D003937:Diagnosis, Differential; D004562:Electrocardiography; D015716:Electrocardiography, Ambulatory; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008133:Long QT Syndrome / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D019462:Syncope, Vasovagal / Q000175:diagnosis / Q000209:etiology* / Q000235:genetics; D013611:Tachycardia, Atrioventricular Nodal Reentry / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D016171:Torsades de Pointes / Q000175:diagnosis / Q000235:genetics