[Early surgery in Poland syndrome].
Poland's congenital malformation presents a variable grade of complexity, depending upon the extent of the muscular and chondro-costal defect. Surgical repair for cosmetic reasons only, may be performed during childhood or puberty due to the absence of symptoms. However, this does not occur when the costal defects has a considerable size, with pulmonary herniation and impairment of respiratory function. In this cases, early surgical correction is preferred in order to adequately stabilize the chest wall. In this paper we present our experience of early surgical treatment in 5 patients affected by a complex syndrome, that were treated with autologous costal transplants and the use pof polytetrafluoroethylene to cover the chest wall defect. We discuss the surgical procedure performed, as well as the advantages of this material with respect to others described up to date and the good results obtained in one of the cases followed-up for five years.
Bento
L
L
Servicio de Cirugía Pediátrica, Hospital Virgen del Camino, C/Irunlarrea, 3, 31008 Pamplona.
Martínez
M
M
Conde
J
J
Pérez Martínez
A
A
Esparza
J
J
González
A
A
D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011045:Poland Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D013902:Radiography, Thoracic; D013997:Time Factors