[New approach in the surgical treatment of the urogenital sinus].
The urogenital sinus is an embriological anomaly which consists on a common channel from the urethra and vagina. The major incidence is produced in the congenital adrenal hyperplasia's context. In certain occasions it can be associated to an imperforate anus, then the malformation is called a cloacal defect. There are multiple surgical techniques to correct this malformation and different therapeutical approaches (without surgery, surgery at one or various times, early or delayed surgery) being the newest one the total urogenital mobilization. The purpose of this work is to reflect our experience with this technique. We present seven girls with urogenital sinus (3 with congenital adrenal hyperplasia, 2 with a cloacal defect, and the other 2 associated to ambiguous genitalia). Five patients were operated in the first year of life. The outcome has been favorable, and the cosmetic and functional results have been very good. The surgical technique consists on posterior sagittal incision, it can be done transanorectal if necessary, the urethrovaginal union is achieved and both structures are mobilized together, connecting them to the perineum, as a single unit. We believe that the total urogenital mobilization is actually the surgical technique to be chosen in every of urogenital sinus, for being easier, allowing early realization (girls under 1 year old), correcting simultaneously other anomalies, reducing the complications (urethrovaginal fistula, vaginal structure, or acquired vaginal atresia); and the result is excellent.
Molina
E
E
Servicio de Cirugía Pediátrica, Hospital General Universitario Gregorio Marañón, Madrid. jmesa@vitanet.euroredes.es
Cerdá
J
J
Sánchez-Martín
R
R
Romero
R
R
Estellés
C
C
Aguilar
F
F
Vázquez
J
J
D000015:Abnormalities, Multiple / Q000601:surgery*; D000293:Adolescent; D002648:Child; D002988:Cloaca / Q000601:surgery*; D005260:Female; D006801:Humans; D007223:Infant; D013577:Syndrome; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery*; D013520:Urologic Surgical Procedures / Q000379:methods; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery*