Complete thoracic ectopia cordis.
Thoracic ectopia cordis is a rare congenital defect with very few reported survivors after surgical correction. We report a case of complete thoracic ectopia cordis with double outlet right ventricle. The diagnosis was established antenatally and a repair was undertaken soon after birth. The child remained stable and was extubated on the fifth post-operative day. Forty-eight hours later the child succumbed to an unexplained respiratory arrest. Also presented is a review of the different surgical strategies for this unusual condition.
Alphonso
N
N
Department of Congenital Heart Disease, Guy's Hospital, Guy's and St Thomas' Hospitals NHS Trust, St Thomas' Street, London SE1 9RT, UK. nelson.a@bigfoot.com
Venugopal
P S
PS
Deshpande
R
R
Anderson
D
D
D006348:Cardiac Surgical Procedures / Q000379:methods; D004310:Double Outlet Right Ventricle / Q000601:surgery; D017809:Fatal Outcome; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D013249:Sternum / Q000002:abnormalities