title: MURCS association and rectovestibular fistula: case report of a patient treated with one-stage posterior sagittal anorectoplasty and sigmoid loop vaginoplasty.
abstract: MURCS association is rare, first described by Duncan in 1979, including nonrandom association of Mullerian duct aplasia or hypoplasia (MU), renal agenesis or ectopy (R), and cervicothoracic somite dysplasia. A 5-year-old girl was admitted to the clinic with a complaint of anteriorly located anus. Physical and radiologic examination of the patient found MURCS association with anorectal malformation (ARM) of rectovestibular-type fistula. She had multiple vertebral anomalies, left renal agenesis, vaginal and uterine agenesia, with a normal female 46,XX karyotype. Posterior sagittal anorectoplasty (PSARP) and sigmoid loop vaginal reconstruction was performed as a one-stage operation for the treatment of vaginal agenesis and ARM. There were no complications in the postoperative period. This combined one-stage operation can be used easily in the treatment of some components of the MURCS association such as vaginal agenesis and ARM as an associated anomaly.
authors.affiliation: Department of Pediatric Surgery, Celal Bayar University, Medical Faculty, Manisa, Turkey.
authors.forename: Cüneyt
authors.initials: C
authors.lastname: Günşar
authors.forename: Abdülkadir
authors.initials: A
authors.lastname: Genç
authors.forename: Aydin
authors.initials: A
authors.lastname: Sencan
authors.forename: Zafer
authors.initials: Z
authors.lastname: Dağlar
authors.forename: Oğuz
authors.initials: O
authors.lastname: Alparslan
authors.forename: Erol
authors.initials: E
authors.lastname: Mir
mesh_terms: D001003:Anal Canal / Q000002:abnormalities* / Q000601:surgery*; D002675:Child, Preschool; D012809:Colon, Sigmoid / Q000601:surgery / Q000637:transplantation; D005260:Female; D006130:Growth Disorders; D006801:Humans; D007668:Kidney / Q000002:abnormalities; D009333:Neck / Q000002:abnormalities; D010502:Perineum / Q000601:surgery; D012006:Rectovaginal Fistula / Q000601:surgery*; D012007:Rectum / Q000601:surgery; D012272:Ribs / Q000002:abnormalities; D012600:Scoliosis / Q000151:congenital; D013131:Spine / Q000002:abnormalities; D013577:Syndrome; D014599:Uterus / Q000002:abnormalities; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery*