[A case of acute encephalitis with refractory, repetitive partial seizures (AERRPS) showing transient disappearance of the seizure with occurrence of choreo-ballistic movement].
We present here a 5-year-old girl with acute encephalities with refractory, repetitive partial seizures (AERRPS), a new clinical entity defined by the following five criteria: 1. acute encephalitis with a prolonged acute phase of more than 2 weeks, 2. persistent partial seizures with identical phenotype both in the acute and recovery phase, 3. seizures frequently evolving into convulsive status especially during the acute phase, 4. extremely intractable, and 5. no causative lesion or agent is identified. Interestingly, her seizures had completely diminished from the fifty-sixth day of her illness with concomitant appearance of choreo-ballistic involuntary movements. After the 120th day of the illness, seizures evolved again, though the involuntary movements persisted. This transient disappearance of intractable seizures might provide a clue to the pathophysiology of seizures in AERRPS.
Hamano
Kimiko
K
Department of Pediatrics, Tsuchiura Kyodo Hospital, Tsuchiura, Ibaragi.
Watanabe
Akimitsu
A
Kohyama
Jun
J
D000208:Acute Disease; D002675:Child, Preschool; D020820:Dyskinesias / Q000209:etiology* / Q000503:physiopathology; D004660:Encephalitis / Q000150:complications* / Q000503:physiopathology; D004828:Epilepsies, Partial / Q000209:etiology* / Q000503:physiopathology; D005260:Female; D006801:Humans; D012008:Recurrence; D012075:Remission, Spontaneous