Giant fibrosarcoma arising in dermatofibrosarcoma protuberans on the scalp during pregnancy.
BACKGROUND
Dermatofibrosarcoma protuberans (DFSP) is a low-grade malignant soft tissue tumor of subcutaneous tissues that has a propensity for local recurrence; however, it seldom metastasizes. Most lesions occur over the trunk or proximal extremities, and there is slight male preponderance. DFSP is rare on the head and neck. Less than 5% tumors are located on the scalp.


OBJECTIVE
To describe a case of giant fibrosarcoma arising in DFSP on the scalp during pregnancy.


METHODS
In our patient, the tumor was on scalp and measured 15 x 11 x 7 cm. The recurrent tumor that developed in the same region was measured 33 x 30 x 15 cm. Histopathologic examination of this mass revealed fibrosarcoma. The mass was excised from the subperiosteal plane with a 3-cm free margin. Because of the high possibility of recurrence, the defect site was reconstructed with a split-thickness skin graft.


RESULTS
After 1 year of follow-up, no recurrence or metastasis was detected.


CONCLUSIONS
We present a unique case in which the person has a giant fibrosarcoma on her scalp arising from DFSP with fibrosarcomatous change during pregnancy.
Cakir
Bariş
B
Department of Plastic and Reconstructive Surgery, Dr. Lütfi Kirdar Education and Research Hospital, Istanbul, Turkey. drbariscakir1@hotmail.com
Misirlioğlu
Aykut
A
Gideroğlu
Kaan
K
Aköz
Tayfun
T
D000328:Adult; D018223:Dermatofibrosarcoma / Q000473:pathology* / Q000601:surgery; D005260:Female; D005354:Fibrosarcoma / Q000473:pathology* / Q000601:surgery; D006258:Head and Neck Neoplasms / Q000473:pathology* / Q000601:surgery; D006801:Humans; D011247:Pregnancy; D011252:Pregnancy Complications, Neoplastic / Q000473:pathology* / Q000601:surgery; D012535:Scalp; D012878:Skin Neoplasms / Q000473:pathology* / Q000601:surgery; D016038:Skin Transplantation; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000601:surgery