title: Rapidly progressive bilateral sensory neural hearing loss as a presentation of mitochondrial neurogastrointestinal encephalomyopathy.
authors.affiliation: Department of Otolaryngology-Head and Neck Surgery, Institute of Diagnostic Imaging, Rambam Medical Center and Technion Faculty of Medicine, Haifa, Israel.
authors.forename: Orit
authors.initials: O
authors.lastname: Kaidar-Person
authors.forename: Avishay
authors.initials: A
authors.lastname: Golz
authors.forename: Aviram
authors.initials: A
authors.lastname: Netzer
authors.forename: Dorit
authors.initials: D
authors.lastname: Goldsher
authors.forename: Henry Zvi
authors.initials: HZ
authors.lastname: Joachims
authors.forename: David
authors.initials: D
authors.lastname: Goldenberg
mesh_terms: D000328:Adult; D001301:Audiometry, Pure-Tone; D003937:Diagnosis, Differential; D018450:Disease Progression; D005260:Female; D005500:Follow-Up Studies; D006312:Hearing Loss, Bilateral / Q000175:diagnosis / Q000209:etiology; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D017237:Mitochondrial Encephalomyopathies / Q000150:complications* / Q000175:diagnosis*; D018570:Risk Assessment; D012720:Severity of Illness Index