title: Anaesthetic and airway management in a child with Hanhart's syndrome.
abstract: Hanhart's syndrome (oromandibular-limb hypogenesis syndrome) is a rare disease characterized by hypoglossia/aglossia, various distal limb defects and micrognathia. Difficult airway due to micrognathia may complicate anaesthetic management in this syndrome. We describe the anaesthetic management of a child with Hanhart's syndrome undergoing plastic reconstructive surgery.
authors.affiliation: Department of Anaesthesiology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey. sbaris@omu.edu.tr
authors.forename: Deniz
authors.initials: D
authors.lastname: Karakaya
authors.forename: Sibel
authors.initials: S
authors.lastname: Bariş
authors.forename: Nurşen
authors.initials: N
authors.lastname: Belet
authors.forename: Ethem
authors.initials: E
authors.lastname: Güneren
authors.forename: Emre
authors.initials: E
authors.lastname: Ustün
mesh_terms: D000015:Abnormalities, Multiple; D000402:Airway Obstruction / Q000150:complications*; D000769:Anesthesia, Inhalation; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D002675:Child, Preschool; D006801:Humans; D007442:Intubation, Intratracheal; D008297:Male; D008738:Methyl Ethers / Q000627:therapeutic use; D008865:Microstomia / Q000150:complications*; D009056:Mouth Abnormalities / Q000601:surgery*; D009609:Nitrous Oxide / Q000627:therapeutic use; D010100:Oxygen / Q000627:therapeutic use; D019651:Plastic Surgery Procedures; D000077149:Sevoflurane; D013577:Syndrome; D014059:Tongue / Q000002:abnormalities
chemical_list: D018685:Anesthetics, Inhalation; D008738:Methyl Ethers; D000077149:Sevoflurane; D009609:Nitrous Oxide; D010100:Oxygen