title: [Anesthetic management of a patient with oculopharyngodistal-myopathy].
abstract: Oculopharyngodistal-myopathy (OPDM) is an autosomal dominant, heredofamilial myopathy accompanied with slowly progressive ptosis and extraocular palsy, and weakness of the masseter, facial, and bulbar muscles, as well as distal involvement of the limbs starting around 40 years of age or later. A 54-year-old female with OPDM underwent resection of the uterus for uterus body cancer. We speculated the patient might be at the risk of aspiration pneumonia, prolonged respiratory depression, and malignant hyperthermia, and chose spinal and epidural anesthesia. The operation was performed successfully and the patient was discharged uneventfully.
authors.affiliation: Tsukuba University Hospital, Tsukuba 305-8575.
authors.forename: Masahiro
authors.initials: M
authors.lastname: Yagihara
authors.forename: Taeko
authors.initials: T
authors.lastname: Fukuda
authors.forename: Masayuki
authors.initials: M
authors.lastname: Miyabe
authors.forename: Masahiko
authors.initials: M
authors.lastname: Watanabe
authors.forename: Hidenori
authors.initials: H
authors.lastname: Toyooka
mesh_terms: D000767:Anesthesia, Epidural / Q000379:methods*; D000775:Anesthesia, Spinal / Q000379:methods*; D001763:Blepharoptosis / Q000150:complications; D005158:Facial Paralysis / Q000150:complications; D005260:Female; D006801:Humans; D008875:Middle Aged; D009136:Muscular Dystrophies / Q000601:surgery*; D009801:Oculomotor Muscles; D009886:Ophthalmoplegia / Q000150:complications; D010609:Pharyngeal Muscles