Laryngotracheal involvement of relapsing polychondritis in a Korean girl.
We describe a young girl presenting with acute dyspnea because of laryngotracheal involvement of relapsing polychondritis (RP). RP, a multisystemic disorder of unknown etiology, is a very rare disease in children. It is characterized by inflammation and destruction of the cartilaginous structure of many organs, including the respiratory tract. Early respiratory tract involvement in younger patients is the greatest threat to life, and aggressive therapy, including tracheostomy and intravenous high-dose steroids, is advocated.
Kim
Cheol-Min
CM
Department of Pediatrics, Asan Medical Center, College of Medicine, Ulsan University, Seoul, Korea.
Kim
Bong-Seong
BS
Cho
Kyung-Ja
KJ
Hong
Soo-Jong
SJ
D000293:Adolescent; D000402:Airway Obstruction / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D003251:Constriction, Pathologic; D003413:Cricoid Cartilage / Q000000981:diagnostic imaging / Q000473:pathology; D004417:Dyspnea / Q000209:etiology*; D005260:Female; D005931:Glottis / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D011081:Polychondritis, Relapsing / Q000150:complications* / Q000473:pathology; D011856:Radiographic Image Enhancement; D013957:Thyroid Cartilage / Q000473:pathology; D014057:Tomography, X-Ray Computed; D014139:Tracheostomy