Desmoid tumor of bone with enchondromatous nodules, mistaken for chondrosarcoma.
Desmoid tumor of bone, also termed desmoplastic fibroma or aggressive fibromatosis, is a rare, locally aggressive fibroblastic tumor. We present a 16-year-old male with a huge desmoid tumor involving the iliac wing. It was associated with enchondromatous nodules mimicking malignancy. The tumor in this patient was mistaken for chondrosarcoma and hemipelvectomy was performed. To our knowledge, such a case has not previously been documented fully in the English literature. The radiographic and pathologic findings and a possible mechanism of enchondromatous nodule formation in fibrous bone tumors are discussed.
Bahk
Won-Jong
WJ
The Musculoskeletal Oncology Study Group, The Catholic University of Korea, Korea.
Kang
Yong-Koo
YK
Lee
An-Hee
AH
Mirra
Joseph M
JM
D000293:Adolescent; D001859:Bone Neoplasms / Q000175:diagnosis*; D002813:Chondrosarcoma / Q000175:diagnosis*; D003951:Diagnostic Errors; D004687:Enchondromatosis / Q000175:diagnosis*; D018220:Fibroma, Desmoplastic / Q000175:diagnosis*; D006801:Humans; D007085:Ilium / Q000000981:diagnostic imaging* / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D011859:Radiography