Anaesthetic and airway management in a child with Hanhart's syndrome.
Hanhart's syndrome (oromandibular-limb hypogenesis syndrome) is a rare disease characterized by hypoglossia/aglossia, various distal limb defects and micrognathia. Difficult airway due to micrognathia may complicate anaesthetic management in this syndrome. We describe the anaesthetic management of a child with Hanhart's syndrome undergoing plastic reconstructive surgery.
Karakaya
Deniz
D
Department of Anaesthesiology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey. sbaris@omu.edu.tr
Bariş
Sibel
S
Belet
Nurşen
N
Güneren
Ethem
E
Ustün
Emre
E
D000015:Abnormalities, Multiple; D000402:Airway Obstruction / Q000150:complications*; D000769:Anesthesia, Inhalation; D018685:Anesthetics, Inhalation / Q000627:therapeutic use; D002675:Child, Preschool; D006801:Humans; D007442:Intubation, Intratracheal; D008297:Male; D008738:Methyl Ethers / Q000627:therapeutic use; D008865:Microstomia / Q000150:complications*; D009056:Mouth Abnormalities / Q000601:surgery*; D009609:Nitrous Oxide / Q000627:therapeutic use; D010100:Oxygen / Q000627:therapeutic use; D019651:Plastic Surgery Procedures; D000077149:Sevoflurane; D013577:Syndrome; D014059:Tongue / Q000002:abnormalities
D018685:Anesthetics, Inhalation; D008738:Methyl Ethers; D000077149:Sevoflurane; D009609:Nitrous Oxide; D010100:Oxygen