title: A rare vascular malformation, Klippel-Trenaunay syndrome. Report of a case with deep vein agenesis and review of the literature.
abstract: The Klippel-Trenaunay syndrome (KTS) is a rare anomaly characterized by naevus, soft tissue hypertrophy and varicosities which is mainly unknown etiology. Associated deep venous system abnormalities have been reported with KTS. Here, a 4-year-old-boy with KTS was reported, because of the associated popliteal vein, common femoral vein with its deep and superficial branches, and external iliac vein agenesis. The originality of the presented case is that we have never observed such a case before.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Hacettepe University, Ankara, Turkey. rdogan@hacettepe.edu.tr
authors.forename: R
authors.initials: R
authors.lastname: Doğan
authors.forename: O Faruk
authors.initials: OF
authors.lastname: Doğan
authors.forename: M
authors.initials: M
authors.lastname: Oç
authors.forename: D
authors.initials: D
authors.lastname: Akata
authors.forename: B
authors.initials: B
authors.lastname: Gümüş
authors.forename: F
authors.initials: F
authors.lastname: Balkanci
mesh_terms: D002675:Child, Preschool; D005268:Femoral Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007084:Iliac Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis*; D007866:Leg / Q000098:blood supply / Q000000981:diagnostic imaging; D008297:Male; D010690:Phlebography; D018615:Ultrasonography, Doppler, Color