[ACTH-producing paraganglioma of the paranasal sinuses].
Paragangliomas are tumours of neuroectodermal origin and hormonally active in rare instances. They are very unusual in the paranasal sinuses. We report on the first case--as far as we know--of a recurrent nasal paraganglioma, which started to produce ACTH after a period of ten years and resulted in Cushing's syndrome. Resection of the tumour normalised ACTH and cortisol secretion.
Lieberum
B
B
Klinikum Minden, Hals-Nasen-Ohren-Klinik.
Jaspers
C
C
Münzenmaier
R
R
D000182:ACTH Syndrome, Ectopic / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D005626:Frontal Sinus / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D008443:Maxillary Sinus / Q000473:pathology / Q000601:surgery; D008444:Maxillary Sinus Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D018365:Neoplasm, Residual / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D010235:Paraganglioma / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D010255:Paranasal Sinus Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D012086:Reoperation; D014057:Tomography, X-Ray Computed