Hemopneumothorax associated with Marfan syndrome and congenital afibrinogenemia.
In patients with afibrinogenemia who require operation, prophylaxis against bleeding is important. We report the case of a 14-year-old boy with Marfan syndrome and congenital afibrinogenemia in whom hemopneumothorax developed. Video-assisted thoracoscopic surgery was performed successfully under intravenous administration of fibrinogen and with careful monitoring of plasma fibrinogen level.
Kanno
Ryuzo
R
First Department of Surgery, Fukushima Medical University, Hikarigaoka, Fukushima, Japan. ryuzo@fmu.ac.jp
Suzuki
Hiroyuki
H
Fujiu
Koichi
K
Yoshino
Yasuaki
Y
Ohishi
Akio
A
Gotoh
Mitsukazu
M
D000293:Adolescent; D000347:Afibrinogenemia / Q000150:complications / Q000151:congenital*; D005340:Fibrinogen / Q000008:administration & dosage; D006468:Hemopneumothorax / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D020775:Thoracic Surgery, Video-Assisted
D005340:Fibrinogen