title: [Case report Brown-Vialetto-Van laere syndrome].
abstract: A case of a young man (36 years old) suffering from a progressive bulbo-pontine palsy, bilateral central deafness and respiratory failure, clinically known as Brown-Vialetto-Van Laere syndrome (BVVL) is reported. The illness occurred at 24 years and, after a period of quiescence of 12 years, led to a serious dependence from mechanical ventilation. In tyhis report the most important points of view about resuscitation and intensive treatment, such as neuromuscular failure and locked-in condition, are discussed.
authors.affiliation: Servizio di Anestesia Rianimazione e Terapia Intensiva, Ospedale Vallecamonica, Esine (Brescia), Italy.
authors.forename: S
authors.initials: S
authors.lastname: Introini
authors.forename: G M
authors.initials: GM
authors.lastname: Sasso
authors.forename: G
authors.initials: G
authors.lastname: Moioli
authors.forename: W L
authors.initials: WL
authors.lastname: Morandini
mesh_terms: D000328:Adult; D001921:Brain / Q000473:pathology; D010244:Bulbar Palsy, Progressive / Q000473:pathology* / Q000628:therapy; D006313:Hearing Loss, Central / Q000473:pathology* / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012121:Respiration, Artificial; D012131:Respiratory Insufficiency / Q000473:pathology* / Q000628:therapy; D013577:Syndrome