Hyper immunoglobulin-E syndrome: a case with chronic ear draining mimicking polypoid otitis media.
The hyper-IgE syndrome is a rare, complex immunoregulatory disorder characterized by pruritic dermatitis, recurrent staphylococcus skin abscesses and extremely elevated levels of IgE in serum. In this report, an 8-year-old girl with hyper-IgE syndrome is presented. She had pruritic dermatitis and skin abscesses on her extremities and scalp. Discharge and granulation tissue in right external ear canal were recognized in otorhinolaryngologic examination. Cultures of the suppuration of the external ear canal yielded S. aureus. Biopsy of the lesion was reported as granulation tissue. Local treatment of the ear canal was performed with ear wick soaked with steroid and antibiotic solutions two times per day.
Görür
Kemal
K
Fatih mah, Babil cad, Girne sitesi, D. blok, No: 1/1. 33170 Mezitli, Mersin, Turkey. kgorur@mersin.edu.tr
Ozcan
Cengiz
C
Unal
Murat
M
Akbaş
Yücel
Y
Vayisoğlu
Yusuf
Y
D002648:Child; D003937:Diagnosis, Differential; D004322:Drainage; D004424:Ear Canal; D005260:Female; D006801:Humans; D007589:Job Syndrome / Q000175:diagnosis* / Q000188:drug therapy; D010034:Otitis Media with Effusion / Q000175:diagnosis* / Q000188:drug therapy; D013203:Staphylococcal Infections / Q000175:diagnosis* / Q000188:drug therapy