Primitive neuroectodermal tumor of the thumb metacarpal bone: a case report and literature review.
A 27-year-old otherwise healthy patient was diagnosed with a primitive neuroectodermal tumor of the thumb metacarpal bone of the left hand. Based on a common chromosomal translocation this tumor shows a close relationship to Ewing's sarcoma. Its occurrence in the extremities is uncommon and involvement of the hand is extremely rare. The treatment consisted of neo- and adjuvant chemotherapy and marginal resection of the affected thumb metacarpal bone including periosseous soft tissue and reconstruction of the thumb by an intercalated segmental index pollicization.
Harder
Yves
Y
Department of Orthopaedic, Plastic, Reconstructive, Aesthetic and Hand Surgery, Division of Hand Surgery, Inselspital Berne, University Hospital of Berne, Berne, Switzerland.
Buechler
Ueli
U
Vögelin
Esther
E
D000328:Adult; D001859:Bone Neoplasms / Q000000981:diagnostic imaging / Q000601:surgery*; D005260:Female; D006801:Humans; D008663:Metacarpus / Q000473:pathology*; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000000981:diagnostic imaging / Q000601:surgery*; D011859:Radiography; D013933:Thumb / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*