title: Organ-confined primitive neuroectodermal tumor arising from the kidney.
abstract: Primitive neuroectodermal tumor (PNET) of the kidney is a rare entity with high malignant potential. Of the reported cases of renal PNET, patients presented with metastatic disease and had a poor response to therapy. The authors describe a rare case of an organ-confined primary PNET arising from the kidney in a 16-year-old girl who presented with vague abdominal pain. Tumor behavior and treatment modalities are discussed.
authors.affiliation: Department of Urology, Children's Hospital of New York, Columbia University College of Physicians and Surgeons, New York, New York, USA.
authors.forename: John S
authors.initials: JS
authors.lastname: Lam
authors.forename: Terry W
authors.initials: TW
authors.lastname: Hensle
authors.forename: Larisa
authors.initials: L
authors.lastname: Debelenko
authors.forename: Linda
authors.initials: L
authors.lastname: Granowetter
authors.forename: Steven Y
authors.initials: SY
authors.lastname: Tennenbaum
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000008:administration & dosage / Q000627:therapeutic use; D003131:Combined Modality Therapy; D003520:Cyclophosphamide / Q000008:administration & dosage; D004317:Doxorubicin / Q000008:administration & dosage; D005047:Etoposide / Q000008:administration & dosage; D005260:Female; D006801:Humans; D007069:Ifosfamide / Q000008:administration & dosage; D007680:Kidney Neoplasms / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D009392:Nephrectomy; D018242:Neuroectodermal Tumors, Primitive / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D012074:Remission Induction; D014750:Vincristine / Q000008:administration & dosage; D015431:Weight Loss
chemical_list: D014750:Vincristine; D005047:Etoposide; D004317:Doxorubicin; D003520:Cyclophosphamide; D007069:Ifosfamide