title: Hemopneumothorax associated with Marfan syndrome and congenital afibrinogenemia.
abstract: In patients with afibrinogenemia who require operation, prophylaxis against bleeding is important. We report the case of a 14-year-old boy with Marfan syndrome and congenital afibrinogenemia in whom hemopneumothorax developed. Video-assisted thoracoscopic surgery was performed successfully under intravenous administration of fibrinogen and with careful monitoring of plasma fibrinogen level.
authors.affiliation: First Department of Surgery, Fukushima Medical University, Hikarigaoka, Fukushima, Japan. ryuzo@fmu.ac.jp
authors.forename: Ryuzo
authors.initials: R
authors.lastname: Kanno
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Suzuki
authors.forename: Koichi
authors.initials: K
authors.lastname: Fujiu
authors.forename: Yasuaki
authors.initials: Y
authors.lastname: Yoshino
authors.forename: Akio
authors.initials: A
authors.lastname: Ohishi
authors.forename: Mitsukazu
authors.initials: M
authors.lastname: Gotoh
mesh_terms: D000293:Adolescent; D000347:Afibrinogenemia / Q000150:complications / Q000151:congenital*; D005340:Fibrinogen / Q000008:administration & dosage; D006468:Hemopneumothorax / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D020775:Thoracic Surgery, Video-Assisted
chemical_list: D005340:Fibrinogen