Meningioangiomatosis: report of three cases and review of the literature.
Meningioangiomatosis is a rare condition, probably hamartomatous, characterized by proliferation of capillary-sized vessels, meningothelial cells, and fibroblasts within the cortex of the brain. Lesions may be single or diffuse and may be associated with neurofibromatosis type II. Clinically it presents with seizures but may be asymptomatic throughout life. We report 3 cases of meningioangiomatosis, 2 localized and 1 diffuse, all with different clinical manifestations. Differential diagnoses are discussed with a review of the literature. Since this condition is rare, close clinico-pathological correlation is essential. A correct diagnosis avoids further aggressive treatment.
Savargaonkar
Pratima
P
Albert Einstein School of Medicine, Long Island Jewish Medical Center, New Hyde Park, New York 11040, USA.
Chen
Sheng
S
Bhuiya
Tawfiqal
T
Valderrama
Elsa
E
Bloom
Tamara
T
Farmer
Peter M
PM
D000293:Adolescent; D000368:Aged; D000798:Angiomatosis / Q000473:pathology*; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D008577:Meningeal Neoplasms / Q000473:pathology*; D008579:Meningioma / Q000473:pathology*; D009442:Neurilemmoma / Q000473:pathology; D016518:Neurofibromatosis 2 / Q000473:pathology