Organ-confined primitive neuroectodermal tumor arising from the kidney.
Primitive neuroectodermal tumor (PNET) of the kidney is a rare entity with high malignant potential. Of the reported cases of renal PNET, patients presented with metastatic disease and had a poor response to therapy. The authors describe a rare case of an organ-confined primary PNET arising from the kidney in a 16-year-old girl who presented with vague abdominal pain. Tumor behavior and treatment modalities are discussed.
Lam
John S
JS
Department of Urology, Children's Hospital of New York, Columbia University College of Physicians and Surgeons, New York, New York, USA.
Hensle
Terry W
TW
Debelenko
Larisa
L
Granowetter
Linda
L
Tennenbaum
Steven Y
SY
D015746:Abdominal Pain / Q000209:etiology; D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000008:administration & dosage / Q000627:therapeutic use; D003131:Combined Modality Therapy; D003520:Cyclophosphamide / Q000008:administration & dosage; D004317:Doxorubicin / Q000008:administration & dosage; D005047:Etoposide / Q000008:administration & dosage; D005260:Female; D006801:Humans; D007069:Ifosfamide / Q000008:administration & dosage; D007680:Kidney Neoplasms / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D009392:Nephrectomy; D018242:Neuroectodermal Tumors, Primitive / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D012074:Remission Induction; D014750:Vincristine / Q000008:administration & dosage; D015431:Weight Loss
D014750:Vincristine; D005047:Etoposide; D004317:Doxorubicin; D003520:Cyclophosphamide; D007069:Ifosfamide