title: General anaesthesia in a child with Larsen syndrome.
abstract: Larsen syndrome is a rare congenital connective tissue disorder which is characterized by multiple dislocations of major joints, typical facial appearance, cervical spine narrowing and instability and respiratory difficulties secondary to laryngotracheomalacia. A case of general anaesthesia for laparoscopic hernia repair in a male child aged 16 months with this syndrome is presented. Anaesthesia was well tolerated though intubation proved difficult. Cervical spine instability and postoperative respiratory complications are potential problems.
authors.affiliation: Department of Anaesthesia and Intensive Care, Chinese University of Hong Kong, Prince of Wales Hospital, Shatin, New Territories, Hong Kong, China.
authors.forename: L A H
authors.initials: LA
authors.lastname: Critchley
authors.forename: L
authors.initials: L
authors.lastname: Chan
mesh_terms: D000768:Anesthesia, General; D018686:Anesthetics, Intravenous; D003240:Connective Tissue Diseases / Q000151:congenital*; D005283:Fentanyl; D006552:Hernia, Inguinal / Q000601:surgery*; D006801:Humans; D007223:Infant; D010535:Laparoscopy; D008297:Male
chemical_list: D018686:Anesthetics, Intravenous; D005283:Fentanyl