Byler's disease and anesthetic consideration.
Byler's disease is an autosomal recessive condition characterized by intrahepatic cholestasis, progressive fibrotic changes and finally cirrhosis that leads to death during childhood. This is a report of a six-year-old girl with Byler's disease and retrobulbar hematoma as a result of trauma who underwent enucleation and implantation. This case report describes the anesthetic features of a patient with Byler's disease in which anesthetic agents with no or minimal hepatotoxic effect should be used to avoid deterioration of liver function.
Dal
Didem
D
Department of Anesthesiology and Reanimation, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Salman
Ebru
E
Başgül
Elif
E
D000768:Anesthesia, General; D002648:Child; D002780:Cholestasis, Intrahepatic / Q000150:complications / Q000503:physiopathology*; D005260:Female; D005283:Fentanyl; D006801:Humans; D008738:Methyl Ethers; D019315:Retrobulbar Hemorrhage / Q000150:complications / Q000601:surgery*; D000077149:Sevoflurane
D008738:Methyl Ethers; D000077149:Sevoflurane; D005283:Fentanyl