title: ALCAPA in an adult with preserved left ventricular function.
abstract: Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is the most common congenital coronary artery defect. Left uncorrected, nearly 90% of patients will die within one year. Without surgical repair, surviving patients are subjected to risks of myocardial ischemia with global cardiomyopathy, chronic mitral regurgitation, and sudden death. We report a case of ALCAPA in a 23-year-old female with completely preserved left ventricular function. This article reviews the mechanism of this unusual presentation as well as the therapeutic options for adults presenting with ALCAPA.
authors.affiliation: Division of Cardiothoracic Surgery, University of Colorado Health Sciences Center, Denver, CO 80262, USA. craig.selzman@uchsc.edu
authors.forename: Craig H
authors.initials: CH
authors.lastname: Selzman
authors.forename: Michael A
authors.initials: MA
authors.lastname: Zimmerman
authors.forename: David N
authors.initials: DN
authors.lastname: Campbell
mesh_terms: D000328:Adult; D003330:Coronary Vessel Anomalies / Q000503:physiopathology* / Q000601:surgery; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D016277:Ventricular Function, Left