[A case of relapsing polychondritis with severe involvement of the lower airway in 10 years old boy].
Relapsing polychondritis is a very rare disease of the connective tissue in children. Inflammation may affect all cartilaginous structures. The study presents the case of a 10 years old boy with bilateral conchitis as a prominent symptom of the disease. In our patient lower airways were seriously affected. The detection of the degree of the disease in respiratory tract was facilitated to a large degree by pulmonary function tests and high resolution computed tomography. Histopathological picture of the inflamed cartilage of the tracheobronchial tree finally confirmed the diagnosis.
Postepski
Jacek
J
Jacek Postepski, Klinika Pediatrii, Chorób Płuc i Reumatologii AM, Dzieciecy Szpital Kliniczny, ul. Chodźki 2, 20-093 Lublin.
Korobowicz
Agnieszka
A
Krupski
Witold
W
Skomra
Danuta
D
Emeryk
Andrzej
A
D000402:Airway Obstruction / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology* / Q000503:physiopathology; D001987:Bronchiectasis / Q000209:etiology / Q000473:pathology; D002648:Child; D004425:Ear Cartilage / Q000473:pathology; D006801:Humans; D008297:Male; D011081:Polychondritis, Relapsing / Q000150:complications* / Q000188:drug therapy; D012129:Respiratory Function Tests; D013997:Time Factors; D016896:Treatment Outcome
Nawrotowe zapalenie chrzastki z powaznym zajeciem dolnych dróg oddechowych u dziesiecioletniego chłopca.