[Pourfour du Petit syndrome: a rare aetiology of unilateral exophtalmos with mydriasis and lid retraction].
BACKGROUND
Pourfour du Petit syndrome, rarely reported, is the opposite of Claude Bernard-Horner syndrome.


METHODS
A 67 years old female is hospitalised for dysphagia, allowing the discovery of oesophagus carcinoma with mediastinal, pleural and costal extension. The discovery of left unilateral mydriasis associated with exophthalmos and eyelid retraction suggest Pourfour du Petit syndrome; this diagnosis is confirmed by CT-scan, finding pedicular lysis of high dorsal vertebras and intra-canalar tumoral extension.


CONCLUSIONS
Pourfour du Petit syndrome has the same localisation value and the same aetiologies as Claude Bernard-Horner syndrome, but its mechanism proceeds byan exciting lesion of cervical sympathetic nervous system. The recognition of this entity can allow the diagnosis of pathologies that need emergency treatment.
Aouba
A
A
Service de médecine interne, hôpital européen Georges-Pompidou, 20, rue Leblanc, 75908 Paris cedex 15, France. achille.aouba@wanadoo.fr
Der Agopian
P
P
Genty-Le Goff
I
I
Mutschler
C
C
Janin
N
N
Patri
B
B
D000368:Aged; D001342:Autonomic Nervous System Diseases / Q000209:etiology*; D003680:Deglutition Disorders / Q000209:etiology; D004938:Esophageal Neoplasms / Q000150:complications* / Q000188:drug therapy; D005094:Exophthalmos / Q000209:etiology*; D005141:Eyelid Diseases / Q000209:etiology*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D015878:Mydriasis / Q000209:etiology*; D035583:Rare Diseases / Q000209:etiology*; D013577:Syndrome; D014057:Tomography, X-Ray Computed
Le syndrome de Pourfour du Petit : une cause rare d'exophtalmie unilatérale avec mydriase et élargissement de la fente palpébrale.