[Surgical management of Mondini dysplasia with cerebrospinal fluid leakage].
OBJECTIVE
To evaluate the clinical manifestation and surgical technique of Mondini dysplasia with cerebrospinal fluid (CSF) leakage.


METHODS
Three Mondini dysplasia with spontaneous cerebrospinal fluid leakage were treated by the authors. A transcanal tympanotomy were used to pack the vestibular cavity with muscle.


RESULTS
Three children were first manifested with recurrent meningitis and spontaneous cerebrospinal fluid rhinorrhea. Further examinations found that the leakages were otogenic. One side or both sides Mondini dysplasia were confirmed by CT scanning of temporal bones. The leakages were all stopped by the primary surgical closure.


CONCLUSIONS
Mondini dysplasia should be considered in children with spantaneous cerebrospinal fluid otorhinorrhea. A temporal bone CT scan can confirmed the diagnosis. A transtympanic closure is very effective in the management.
Department of Otolaryngology-Head and Neck Surgery, Xinhua Hospital, Shanghai Second Medical University, Shanghai 200092.
Hao
H
Wu
Rongping
R
Cao
Xiangping
X
Chen
Mingliang
M
Xiang
Guozhen
G
Meng
Qi
Q
Huang
D002558:Cerebrospinal Fluid Otorrhea / Q000209:etiology / Q000601:surgery*; D002559:Cerebrospinal Fluid Rhinorrhea / Q000209:etiology / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D007758:Ear, Inner / Q000002:abnormalities*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008297:Male; D010046:Oval Window, Ear / Q000601:surgery