Nevi flammei affecting two contralateral quadrants and nevus depigmentosus: a new type of phacomatosis pigmentovascularis?
Here, we report on a 64-year-old-woman with nevi flammei affecting two contralateral quadrants, venous insufficiency of the right leg, and asymmetry of the arms, in association with a linear nevus depigmentosus. This combination of vascular and pigmentary abnormalities may represent a novel type of phacomatosis pigmentovascularis caused by non-allelic twin-spotting.
Dippel
E
E
Department of Dermatology, Venereology, and Allergology, University Medical Center, Mannheim, Ruprecht-Karl University of Heidelberg, Mannheim, Germany.
Utikal
J
J
Feller
G
G
Fackel
N
N
Klemke
C D
CD
Happle
R
R
Goerdt
S
S
D005260:Female; D006801:Humans; D007866:Leg / Q000098:blood supply; D008875:Middle Aged; D020752:Neurocutaneous Syndromes / Q000235:genetics / Q000503:physiopathology*; D019339:Port-Wine Stain / Q000235:genetics / Q000503:physiopathology*