Chylotamponade: an unusual presentation of Gorham's syndrome.
Gorham's Syndrome, also known as massive osteolysis or "vanishing bone disease" results from lymphangiomatosis with adjacent bone resorption. Chylothorax is a common complication in cases of mediastinal involvement. We report a case of Gorham's Syndrome presenting as chylotamponade successfully treated with pericardial drainage, early parenteral nutritional support, bilateral pleurodesis for chylous effusions, and adjuvant external beam radiation.
Department of Surgery, University of Wisconsin, Madison, Wisconsin, USA.
Matthew Reed
MR
Swelstad
Carmine
C
Frumiento
Alice
A
Garry-McCoy
Rashmi
R
Agni
Tracey L
TL
Weigel
D000328:Adult; D002305:Cardiac Tamponade / Q000209:etiology* / Q000628:therapy; D005260:Female; D006801:Humans; D010015:Osteolysis, Essential / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D010490:Pericardial Effusion / Q000209:etiology* / Q000628:therapy; D012272:Ribs / Q000473:pathology; D013904:Thoracic Vertebrae / Q000473:pathology