Nevi flammei affecting two contralateral quadrants and nevus depigmentosus: a new type of phacomatosis pigmentovascularis?
Here, we report on a 64-year-old-woman with nevi flammei affecting two contralateral quadrants, venous insufficiency of the right leg, and asymmetry of the arms, in association with a linear nevus depigmentosus. This combination of vascular and pigmentary abnormalities may represent a novel type of phacomatosis pigmentovascularis caused by non-allelic twin-spotting.
Department of Dermatology, Venereology, and Allergology, University Medical Center, Mannheim, Ruprecht-Karl University of Heidelberg, Mannheim, Germany.
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E
Dippel
J
J
Utikal
G
G
Feller
N
N
Fackel
C D
CD
Klemke
R
R
Happle
S
S
Goerdt
D005260:Female; D006801:Humans; D007866:Leg / Q000098:blood supply; D008875:Middle Aged; D020752:Neurocutaneous Syndromes / Q000235:genetics / Q000503:physiopathology*; D019339:Port-Wine Stain / Q000235:genetics / Q000503:physiopathology*