[Clinical analysis of 48 cases with Mondini dysplasia].
OBJECTIVE
To improve the ability to diagnosis the Mondini dysplasis, 48 cases of Mondini dysplasis were reported.


METHODS
The clinical data of 48 cases were collected. The clinical manifestation and the examination of CT and MRI and treatment of the Mondini dysplasia were discussed.


RESULTS
Most of them were deaf when they were babies. The prolonged speaking and unsteading were important clinical feature.


CONCLUSIONS
The diagnosis of the disease is based on the examination of the hight resolution tomography and magnetic resonance image of the temporal bone. Hearing aid is common management to the disease. A part of patients should be considered cochlear implantation.
Department of Otolaryngology, First Affiliated Hospital of Zhengzhou University, Zhengzhou 450052.
Hongjian
H
Liu
Xuelei
X
Dong
Mingmin
M
Dong
Xiaolong
X
Liu
Lingling
L
Chen
D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D007758:Ear, Inner / Q000002:abnormalities* / Q000000981:diagnostic imaging; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000151:congenital / Q000175:diagnosis* / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D014057:Tomography, X-Ray Computed