Primary extrarenal rhabdoid tumor of the ovary. A case report.
BACKGROUND
Malignant rhabdoid tumors are rare, aggressive neoplasms that consist of both renal and extrarenal subtypes. Although extrarenal rhabdoid tumors have been documented at multiple extrarenal sites, to our knowledge no primary ovarian cases have been reported.


METHODS
An 18-year-old, Caucasian woman was diagnosed with a pure primary extrarenal rhabdoid tumor of the ovary following diagnostic laparoscopy for pelvic pain. The tumor exhibited rapid growth, failed to respond to chemotherapy and led rapidly to death.


CONCLUSIONS
Although no other reports on primary ovarian extrarenal rhabdoid tumor have been published, the aggressive behavior of the tumor in this patient was similar to that seen in patients with metastatic disease.
Department of Obstetrics and Gynecology, University of Alabama at Birmingham, 340 Old Hillman Building, 619 19th Street South, Birmingham, AL 35249-7333, USA. trey_leath@yahoo.com
Charles A
CA
Leath
Warner K
WK
Huh
Michael
M
Conner
Mack N
MN
Barnes
D000293:Adolescent; D001707:Biopsy, Needle; D017024:Chemotherapy, Adjuvant; D003131:Combined Modality Therapy; D018450:Disease Progression; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D010535:Laparoscopy / Q000379:methods; D009367:Neoplasm Staging; D010051:Ovarian Neoplasms / Q000473:pathology* / Q000628:therapy; D017699:Pelvic Pain / Q000175:diagnosis / Q000209:etiology; D035583:Rare Diseases; D018335:Rhabdoid Tumor / Q000473:pathology* / Q000628:therapy