Upper airways abnormalities and tracheal problems in Morquio's disease.
Morquio's disease is a metabolic disorder that can cause various respiratory abnormalities. Patients who live into adulthood are likely to develop upper airway problems and respiratory failure. With advances in home ventilation, these patients are increasingly likely to be referred to specialist respiratory units. We describe our experiences with two such patients.
Department of Respiratory Medicine, University Hospital Aintree, Liverpool, UK. paulpwalker@hotmail.com
P P
PP
Walker
E
E
Rose
J G
JG
Williams
D000328:Adult; D000402:Airway Obstruction / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009085:Mucopolysaccharidosis IV / Q000150:complications* / Q000473:pathology; D012121:Respiration, Artificial; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000473:pathology / Q000628:therapy; D014133:Tracheal Diseases / Q000209:etiology* / Q000473:pathology; D015300:Ventilator Weaning