Pseudotumor cerebri associated with Sjögren's syndrome.
OBJECTIVE
To report a case of papilledema and pseudotumor cerebri developed in association with Sjögren's syndrome.


METHODS
Case-report of a 38-year-old woman with history, imaging and histology confirming the diagnosis of both pseudotumor cerebri and Sjögren's syndrome who presented with bilateral decrease of vision.


RESULTS
Papilledema associated with pseudotumor cerebri was observed in both eyes. The patient's visual acuity improved transiently with the administration of intravenous steroids and cyclophosphamide; subsequently she needed a ventriculoperitoneal shunt.


CONCLUSIONS
Sjögren's syndrome should be considered in the different etiologies of pseudotumor cerebri. The major improvement with corticosteroids and ventriculoperitoneal shunt makes prompt diagnosis essential.
Department of Ophthalmology, Pitié-Salpétrière Hospital, Paris, France.
Dinu
D
Stanescu
Bahram
B
Bodaghi
Du Le Thi
DL
Huong
Dan
D
Milea
B
B
Goulet-Salmon
Jean-Charles
JC
Piette
Phuc
P
LeHoang
D000328:Adult; D005260:Female; D005451:Fluorescein Angiography; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D010211:Papilledema / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D011559:Pseudotumor Cerebri / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D017287:Ventriculoperitoneal Shunt; D014792:Visual Acuity
D005938:Glucocorticoids