Chylotamponade: an unusual presentation of Gorham's syndrome.
Gorham's Syndrome, also known as massive osteolysis or "vanishing bone disease" results from lymphangiomatosis with adjacent bone resorption. Chylothorax is a common complication in cases of mediastinal involvement. We report a case of Gorham's Syndrome presenting as chylotamponade successfully treated with pericardial drainage, early parenteral nutritional support, bilateral pleurodesis for chylous effusions, and adjuvant external beam radiation.
Swelstad
Matthew Reed
MR
Department of Surgery, University of Wisconsin, Madison, Wisconsin, USA.
Frumiento
Carmine
C
Garry-McCoy
Alice
A
Agni
Rashmi
R
Weigel
Tracey L
TL
D000328:Adult; D002305:Cardiac Tamponade / Q000209:etiology* / Q000628:therapy; D005260:Female; D006801:Humans; D010015:Osteolysis, Essential / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D010490:Pericardial Effusion / Q000209:etiology* / Q000628:therapy; D012272:Ribs / Q000473:pathology; D013904:Thoracic Vertebrae / Q000473:pathology