title: Endomyocardial fibrosis in infancy.
abstract: The patient was a 4-month-old infant, who underwent persistent ductus arteriosus interruption with titanium clips at the age of 13 days and, since the age of 2 months, had crises of hypoxia and hypertonicity. After clinical investigation, the presence of pulmonary hypertension was confirmed and left ventricular inflow tract obstruction was suspected. The patient underwent surgical treatment at the age of 4 months, during which right and left ventricular endocardial fibrosis was identified. The fibrosis was resected, but the infant had an unfavorable clinical evolution with significant diastolic restriction and died on the sixth postoperative day. Anatomicopathological and surgical findings suggested endomyocardial fibrosis, although that pathology is very rare at the patient's age.
authors.affiliation: Divisão Cirúrgica, Setor de Cirurgia Cardíaca Pediátrica, Instituto do Coração, Hospital das Clínicas, FMUSP, Sao Paulo, SP, Brazil. mbjatene@uol.com.br
authors.forename: Marcelo Biscegli
authors.initials: MB
authors.lastname: Jatene
authors.forename: Ivan Salvador Bonillo
authors.initials: IS
authors.lastname: Contreras
authors.forename: Laura C Riera
authors.initials: LC
authors.lastname: Lameda
authors.forename: José de Lima
authors.initials: Jde L
authors.lastname: Oliveira
authors.forename: Munir
authors.initials: M
authors.lastname: Ebaid
authors.forename: Elisa Rumiko
authors.initials: ER
authors.lastname: Iwahashi
authors.forename: Deipara Monteiro
authors.initials: DM
authors.lastname: Abellan
authors.forename: Vera Demarchi
authors.initials: VD
authors.lastname: Aiello
authors.forename: Miguel Barbero
authors.initials: MB
authors.lastname: Marcial
authors.forename: Sérgio Almeida
authors.initials: SA
authors.lastname: de Oliveira
mesh_terms: D004719:Endomyocardial Fibrosis / Q000150:complications / Q000473:pathology* / Q000601:surgery; D017809:Fatal Outcome; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D007223:Infant; D008297:Male