Multiple endocrine neoplasia type 1: duodenopancreatic tumours.
The pancreaticoduodenal disease in Multiple endocrine neoplasia type 1 (MEN1) is the most frequent cause of death due to the syndrome, and the most controversial with regard to its management. This article discusses the current data and recommendations with respect to disease screening, functional tumour diagnosis, natural history, preoperative imaging, operative strategy and follow-up.
Doherty
G M
GM
Department of Surgery, University of Michigan, Ann Arbor, MI 48109, USA. gerardd@umich.edu
Thompson
N W
NW
D000368:Aged; D018273:Carcinoma, Islet Cell / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery; D004379:Duodenal Neoplasms / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery; D019160:Endosonography; D005260:Female; D015408:Gastrinoma / Q000175:diagnosis / Q000401:mortality / Q000601:surgery; D005820:Genetic Testing / Q000379:methods; D006579:Heterozygote; D006801:Humans; D008297:Male; D008875:Middle Aged; D018761:Multiple Endocrine Neoplasia Type 1 / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery; D010187:Pancreatic Hormones / Q000097:blood; D010190:Pancreatic Neoplasms / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery; D011182:Postoperative Care; D014057:Tomography, X-Ray Computed
D010187:Pancreatic Hormones