title: Type 2 segmental manifestation of congenital multiple glomangiomas.
abstract: Congenital multiple glomus tumors are extremely rare, and less than 20 cases have been well documented. We report an uncommon case of congenital multiple glomangiomas with a segmental manifestation in a 9-year-old girl. Since birth, the child had presented asymptomatic angiomatous macules arranged in a segmental pattern on the neck and trunk. During a follow-up period of 9 years, disseminated smaller papulonodular lesions developed on both arms and the left leg with a segmental distribution. Histopathology of congenital and acquired lesions confirmed the diagnosis of glomangiomas. The family history was negative for glomus tumors. This type of presentation supports the recently described type 2 segmental manifestation of multiple glomus tumors, with a segmental involvement of congenital early developing lesions.
authors.affiliation: Clinique de Dermatologie, Centre Hospitalo-Universitaire de Lille, France.
authors.forename: Carole Jouffrey
authors.initials: CJ
authors.lastname: Allombert-Blaise
authors.forename: Marie-Laure
authors.initials: ML
authors.lastname: Batard
authors.forename: Magali
authors.initials: M
authors.lastname: Ségard
authors.forename: Elisabeth
authors.initials: E
authors.lastname: Martin de Lassalle
authors.forename: Georges-Marie
authors.initials: GM
authors.lastname: Brevière
authors.forename: Frédéric
authors.initials: F
authors.lastname: Piette
mesh_terms: D001706:Biopsy; D002648:Child; D005260:Female; D005918:Glomus Tumor / Q000151:congenital / Q000473:pathology*; D006801:Humans; D012878:Skin Neoplasms / Q000151:congenital / Q000473:pathology*