Moyamoya disease in a child with previous acute necrotizing encephalopathy.
A previously healthy 24-day-old boy presented with a 2-day history of fever and had a convulsion on the day of admission. MRI showed abnormal signal in the thalami, caudate nuclei and central white matter. Acute necrotising encephalopathy was diagnosed, other causes having been excluded after biochemical and haematological analysis of blood, urine and CSF. He recovered, but with spastic quadriparesis. At the age of 28 months, he suffered sudden deterioration of consciousness and motor weakness of his right limbs. MRI was consistent with an acute cerebrovascular accident. Angiography showed bilateral middle cerebral artery stenosis or frank occlusion with numerous lenticulostriate collateral vessels consistent with moyamoya disease.
Kim
Taik-Kun
TK
Department of Diagnostic Radiology, Korea University College of Medicine, Ansan Hospital, 516 Kojan-Dong, Ansan City, Kyungki-Do 425-020, Korea. myrmidon@freechal.com
Eun
Baik-Lin
BL
Cha
Sang Hoon
SH
Chung
Kyoo Byung
KB
Kim
Jung Hyuck
JH
Kim
Baek Hyun
BH
Chung
Hwan Hoon
HH
D000208:Acute Disease; D001921:Brain / Q000473:pathology*; D001927:Brain Diseases / Q000150:complications* / Q000473:pathology; D002533:Cerebral Angiography; D002675:Child, Preschool; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D009072:Moyamoya Disease / Q000150:complications* / Q000473:pathology