title: Congenital partial pericardial defect in a neonate: a case report.
abstract: This report describes a neonate with congenital partial absence of the pericardium associated with hypoplastic left heart syndrome. The patient presented with severe heart failure caused by a hypoplastic left ventricle. The infant died at 15 hours of age because of intractable congestive heart failure. Necropsy revealed, in addition to a hypoplastic left ventricle, a transverse biventricular constriction suggestive of partial absence of the pericardium. In addition to cardiovascular malformations, a left hydronephrosis and a bicornuate uterus was found. We report a rare clinical entity and review the literature.
authors.affiliation: Department of Pediatrics, Jersey City Medical Center, New Jersey 07304, USA.
authors.forename: Surasak
authors.initials: S
authors.lastname: Puvabanditsin
authors.forename: Eugene
authors.initials: E
authors.lastname: Garrow
authors.forename: Anjali
authors.initials: A
authors.lastname: Biswas
authors.forename: Angela
authors.initials: A
authors.lastname: Davydov
authors.forename: Manuel
authors.initials: M
authors.lastname: Gomez
authors.forename: Passara
authors.initials: P
authors.lastname: Liangthanasarn
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000328:Adult; D000527:Alprostadil / Q000008:administration & dosage; D001021:Aortic Valve / Q000002:abnormalities; D004298:Dopamine / Q000008:administration & dosage; D004452:Echocardiography; D004461:Eclampsia; D017809:Fatal Outcome; D005260:Female; D005865:Gestational Age; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D006869:Hydronephrosis / Q000175:diagnosis; D007231:Infant, Newborn; D007235:Infant, Premature, Diseases / Q000175:diagnosis* / Q000628:therapy; D007262:Infusions, Intravenous; D008943:Mitral Valve / Q000002:abnormalities; D010496:Pericardium / Q000002:abnormalities*; D011247:Pregnancy; D013902:Radiography, Thoracic; D017211:Treatment Failure; D014599:Uterus / Q000002:abnormalities; D014683:Vena Cava, Superior / Q000002:abnormalities
chemical_list: D000527:Alprostadil; D004298:Dopamine