Phacomatosis pigmentovasculosebacea: an unusual case of phacomatosis multiplex.
A 13-year-old Taiwanese boy had an unusual combination of nevus fuscocoeruleus, large café-au-lait macules, nevus achromicus, large telangiectatic nevi and systematized nevus sebaceus. The term "phacomatosis pigmentovasculosebacea" is proposed to describe the concurrence of these multiple nevi derived from pigmentary, vascular and epithelial cells.
Chen
Wenchieh
W
Department of Dermatology, College of Medicine, National Cheng Kung University, 138 Sheng-Li Road, 704 Tainan, Taiwan. wchen@mail.ncku.edu.tw
Happle
Rudolf
R
D000293:Adolescent; D001415:Back; D003937:Diagnosis, Differential; D006801:Humans; D007866:Leg; D008297:Male; D008548:Melanosis / Q000175:diagnosis* / Q000473:pathology; D009333:Neck; D020752:Neurocutaneous Syndromes / Q000175:diagnosis* / Q000473:pathology; D009626:Terminology as Topic