Thoracic malignant peripheral nerve sheath tumour mimicking a pleural tumour: a rare pedunculated appearance.
A malignant peripheral nerve sheath tumour (MPNST) generally occurs in adults and often in patients with neurofibromatosis-1 (NF-1). We present a rare case of a huge thoracic MPNST arising from the intercostal nerve in a 12-year-old girl without NF-1. In addition to the unusual occurrence in a child without NF-1, MRI demonstrated a unique pedunculated appearance mimicking a pleural tumour. In this report, we present the CT and MRI findings of our case, together with the histopathological findings, and review previous reports.
Komori
Masahiro
M
Department of Radiology, National Kyushu Cancer Centre, 3-1-1 Notame, Minami-ku, Fukuoka 811-1395, Japan. masakomori2002@ybb.ne.jp
Yabuuchi
Hidetake
H
Kuroiwa
Toshiro
T
Nagatoshi
Yoshihisa
Y
Ichinose
Yukito
Y
Hachitanda
Yoichi
Y
D002648:Child; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D005260:Female; D006801:Humans; D018317:Nerve Sheath Neoplasms / Q000175:diagnosis* / Q000473:pathology; D010997:Pleural Neoplasms / Q000175:diagnosis; D013899:Thoracic Neoplasms / Q000175:diagnosis* / Q000473:pathology