title: Moyamoya disease in a child with previous acute necrotizing encephalopathy.
abstract: A previously healthy 24-day-old boy presented with a 2-day history of fever and had a convulsion on the day of admission. MRI showed abnormal signal in the thalami, caudate nuclei and central white matter. Acute necrotising encephalopathy was diagnosed, other causes having been excluded after biochemical and haematological analysis of blood, urine and CSF. He recovered, but with spastic quadriparesis. At the age of 28 months, he suffered sudden deterioration of consciousness and motor weakness of his right limbs. MRI was consistent with an acute cerebrovascular accident. Angiography showed bilateral middle cerebral artery stenosis or frank occlusion with numerous lenticulostriate collateral vessels consistent with moyamoya disease.
authors.affiliation: Department of Diagnostic Radiology, Korea University College of Medicine, Ansan Hospital, 516 Kojan-Dong, Ansan City, Kyungki-Do 425-020, Korea. myrmidon@freechal.com
authors.forename: Taik-Kun
authors.initials: TK
authors.lastname: Kim
authors.forename: Baik-Lin
authors.initials: BL
authors.lastname: Eun
authors.forename: Sang Hoon
authors.initials: SH
authors.lastname: Cha
authors.forename: Kyoo Byung
authors.initials: KB
authors.lastname: Chung
authors.forename: Jung Hyuck
authors.initials: JH
authors.lastname: Kim
authors.forename: Baek Hyun
authors.initials: BH
authors.lastname: Kim
authors.forename: Hwan Hoon
authors.initials: HH
authors.lastname: Chung
mesh_terms: D000208:Acute Disease; D001921:Brain / Q000473:pathology*; D001927:Brain Diseases / Q000150:complications* / Q000473:pathology; D002533:Cerebral Angiography; D002675:Child, Preschool; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D009072:Moyamoya Disease / Q000150:complications* / Q000473:pathology