[Congenital cystic dilatation of the cystic duct associated with an anomalous pancreaticobiliary ductal junction].
We report a case of congenital cystic dilatation of the cystic duct detected in a 40-year-old woman. She had intermittent pain in the right upper quadrant of the abdomen independent of the intake of meals for the last two years. In the ultrasound we found a cystic formation in the vicinity of the enlarged gallbladder, the common hepatic duct/common bile duct and the portal vein. The endoscopic retrograde cholangiography confirmed a cystic duct malformation, which was associated with an anomalous pancreaticobiliary ductal junction (APBDJ). A cholecystectomy with excision of the whole cystic duct and common bile duct and Roux-en-Y hepaticojejunostomy is indicated because there is an increased risk of the development of bile duct cancer and gallbladder cancer in the presence of biliary cystic duct anomalies and APBDJ.
Weiler
H
H
Medizinische Klinik I, Schwerpunkt Gastroenterologie/Hepatologie, Klinikum Ludwigsburg.
Grandel
A
A
Frühmorgen
P
P
D000328:Adult; D001649:Bile Duct Diseases / Q000151:congenital / Q000000981:diagnostic imaging* / Q000601:surgery; D001652:Bile Ducts / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D002760:Cholangiopancreatography, Endoscopic Retrograde; D002763:Cholecystectomy; D003549:Cystic Duct / Q000002:abnormalities / Q000000981:diagnostic imaging* / Q000601:surgery; D004108:Dilatation, Pathologic; D005260:Female; D006801:Humans; D010179:Pancreas / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D010182:Pancreatic Diseases / Q000151:congenital / Q000000981:diagnostic imaging / Q000601:surgery; D014463:Ultrasonography