Multiple macrodontic multituberculism.
Ekman-Westborg and Julin [1974: Oral Surg 38:217-222], described multiple macrodontia and multituberculism affecting the teeth without other anomalies (E-WJ). We describe a Chilean case in a 12-year-old with the typical dental alterations and with histopathologic findings that include absence of predentin layer and prominent reduced enamel epithelium. E-WJ is not a syndrome and we propose "multiple macrodontic multituberculism" as a better name for this anomaly of uncertain etiology affecting only the crowns of the teeth.
Benjamin
Martinez R
MR
Oral Pathology, School of Dentistry, Universidad Mayor, Santiago, Chile.
Rodrigo
Fariña S
FS
Gorlin
Robert J
RJ
D001641:Bicuspid / Q000000981:diagnostic imaging / Q000473:pathology; D002648:Child; D003481:Cuspid / Q000002:abnormalities; D003743:Dental Enamel / Q000002:abnormalities / Q000000981:diagnostic imaging; D003782:Dental Pulp / Q000473:pathology; D005260:Female; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D008963:Molar / Q000002:abnormalities / Q000473:pathology; D011859:Radiography; D009626:Terminology as Topic; D014071:Tooth Abnormalities / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D014092:Tooth Root / Q000002:abnormalities; D014095:Tooth, Impacted / Q000000981:diagnostic imaging / Q000473:pathology