title: [Von Hippel-Lindau disease and obstetric anaesthesia: 3 cases report].
abstract: Von Hippel-Lindau (VHL) disease is a rare autosomal dominant genetic disorder with retinal and nervous system haemangioblastomas, phaeochromocytomia, kidney, pancreas and endolymphatic tumors. The management of childbirth, including epidural anaesthesia is controversial. The possible presence of vascular malformations (retinal and central nervous system and spinal haemangioblastomas) increases the risk of disrupting central nervous system haemangioblastoma during delivery and when epidural anaesthesia is initiated. We report 3 cases of patient with VHL disease with successful epidural anaesthesia 2 for delivery and 1 for Caesarean section.
authors.affiliation: Département d'anesthésie et de réanimation chirurgicale, unité de la maternité, groupe hospitalier Necker-Enfants-Malades, 149, rue de Sèvres, 75743 cedex 15, Paris, France. monique.berl@nck.ap-hop-paris.fr <monique.berl@nck.ap-hop-paris.fr>
authors.forename: M
authors.initials: M
authors.lastname: Berl
authors.forename: L
authors.initials: L
authors.lastname: Dubois
authors.forename: H
authors.initials: H
authors.lastname: Belkacem
authors.forename: P
authors.initials: P
authors.lastname: Dailland
authors.forename: P
authors.initials: P
authors.lastname: Carli
mesh_terms: D000328:Adult; D000767:Anesthesia, Epidural; D000773:Anesthesia, Obstetrical; D002585:Cesarean Section; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011247:Pregnancy; D011256:Pregnancy Outcome; D006623:von Hippel-Lindau Disease / Q000150:complications*