title: Unusual presentation of a malignant granular cell tumor of the pelvis: case report and literature review.
abstract: BACKGROUND
  Malignant granular cell tumors are among the rarest of soft tissue cancers, currently understood to be of Schwann cell origin. As with their benign counterparts, malignant granular cell tumors (MGCTs) have a wide anatomic distribution and carry a poor prognosis, with recurrence and metastasis typically within 1 year of diagnosis. Only a handful of MGCTs have been described in the pelvis.
  
  
  METHODS
  We describe a case of malignant granular cell tumor that presented as a pararectal mass associated with severe rectal pain. The patient underwent pelvic exenteration and postoperative radiation therapy. She recurred with evidence of liver metastases on imaging studies 8 months following her exenteration.
  
  
  CONCLUSIONS
  We discuss the diagnosis and prognosis of malignant granular cell tumors arising in the pelvis.
authors.affiliation: UCI College of Medicine, University of California, Irvine, Medical Education Bldg 802, Irvine, CA 92697, USA.
authors.forename: Jena C
authors.initials: JC
authors.lastname: Berg
authors.forename: Krishnansu S
authors.initials: KS
authors.lastname: Tewari
authors.forename: Raul
authors.initials: R
authors.lastname: Del Rosario
authors.forename: Michael L
authors.initials: ML
authors.lastname: Berman
mesh_terms: D003131:Combined Modality Therapy; D005260:Female; D016586:Granular Cell Tumor / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D006801:Humans; D008875:Middle Aged; D010386:Pelvic Neoplasms / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery