Aplasia cutis congenita of the scalp, the skull, and the dura.
A newborn baby boy presented with a full thickness defect of the scalp, skull, and dura measuring 6 x 7 cm caused by aplasia cutis congenita. Full thickness loss is extremely rare and to our knowledge this case is the twenty-first reported. It has an established mortality of up to 55%. An encephalocele forced us to do an emergency operation with a single large scalp flap based on the supratrochlear and superficial temporal arteries. After revision the child is now 9 months old and progressing well. There are several ways to treat these rare and delicate cases.
Ribuffo
D
D
Division of Plastic Surgery, La Sapienza University, Rome, Italy.
Costantini
M
M
Gullo
P
P
Houseman
N D
ND
Taylor
G I
GI
D004388:Dura Mater / Q000002:abnormalities*; D004476:Ectodermal Dysplasia / Q000453:epidemiology / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012535:Scalp / Q000002:abnormalities*; D012886:Skull / Q000002:abnormalities*; D013524:Surgical Flaps