Scimitar syndrome: complete anatomical and functional diagnosis with gadolinium-enhanced and velocity-encoded cine MRI.
We report an asymptomatic 8-year-old girl with anomalous pulmonary venous connection to the IVC and systemic arterial supply (scimitar syndrome). We present for the first time a description of gadolinium-enhanced 3D MR angiography that provided concurrent non-invasive complete anatomical (arterial and venous supply) and 'functional' (calculation of left-to-right shunt using phase-contrast-MRI performed in the ascending aorta, main pulmonary artery and anomalous pulmonary vein) diagnosis, avoiding the need for more traditional invasive techniques. As the shunt quantification was less than 2:1, conservative management was decided upon.
Marco de Lucas
Enrique
E
Department of Radiology, Hospital Universitario Marques de Valdecilla, Santander, Spain. radmle@humv.es
Canga
Ana
A
Sadaba
Pablo
P
Martin-Duran
Rafael
R
Otero
Macarena
M
Cerezal
Luis
L
D002648:Child; D003287:Contrast Media; D005260:Female; D019786:Gadolinium DTPA; D006801:Humans; D021621:Imaging, Three-Dimensional; D018810:Magnetic Resonance Angiography; D019028:Magnetic Resonance Imaging, Cine; D012587:Scimitar Syndrome / Q000175:diagnosis* / Q000473:pathology
D003287:Contrast Media; C064925:gadodiamide; D019786:Gadolinium DTPA