title: Discrepant activity levels of von Willebrand factor-cleaving protease (ADAMTS-13) in congenital thrombotic thrombocytopenic purpura.
authors.forename: Jan-Dirk
authors.initials: JD
authors.lastname: Studt
authors.forename: Johanna A
authors.initials: JA
authors.lastname: Kremer Hovinga
authors.forename: Miha
authors.initials: M
authors.lastname: Furlan
authors.forename: Bernhard
authors.initials: B
authors.lastname: Lämmle
mesh_terms: D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; D001793:Blood Preservation; D004796:Clinical Enzyme Tests / Q000592:standards; D003951:Diagnostic Errors; D006801:Humans; D008666:Metalloendopeptidases / Q000097:blood / Q000172:deficiency*; D011697:Purpura, Thrombotic Thrombocytopenic / Q000151:congenital / Q000175:diagnosis*
chemical_list: D051722:ADAM Proteins; D008666:Metalloendopeptidases; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human