Klippel-Trenaunay syndrome and pregnancy.
General recommendations on how to deal with pregnancy in patients with Klippel-Trenaunay syndrome (KTS) are rare. We describe the case of a 32-year-old female with KTS, involving the head and the left arm and leg, delivering a healthy female child, and are reviewing the recent literature. The risk to deliver an ill child is low in women with KTS. At the end of the 1st trimester a sonographic investigation can exclude angiodysplastic alterations of the fetus. If the fetus shows changes compatible with KTS, a termination can be discussed because the risk of fatal complications after delivery is high. During pregnancy the careful monitoring of coagulopathic disorders is necessary. Prior to delivery an MR-scan may be useful to detect angiodysplastic vascular structures next to the spinal cord, pelvic structures or the lower abdominal wall, which might complicate peridural anesthesia or caesarean section.
Hergesell
K
K
Department of Angiology, University of Essen, Essen, Germany.
Kröger
K
K
Petruschkat
S
S
Santosa
F
F
Herborn
C
C
Rudofsky
G
G
D000328:Adult; D000925:Anticoagulants / Q000627:therapeutic use; D001458:Bandages; D005260:Female; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis* / Q000628:therapy; D007866:Leg / Q000098:blood supply; D008429:Maternal Welfare; D011247:Pregnancy; D015912:Thrombolytic Therapy; D020246:Venous Thrombosis / Q000175:diagnosis / Q000628:therapy
D000925:Anticoagulants