Pulmonary sequestration presenting as fetal hydrops.
Pulmonary sequestration is a rare developmental anomaly of the lung characterized by nonfunctional pulmonary tissue without communication with the tracheobronchial tree and receiving an aberrant systemic arterial blood supply. Few cases of non-immune hydrops fetalis associated with this entity have been reported. A 2 day old male baby born by cesarean section at 31 weeks gestational age due to fetal hydrops is presented. Autopsy revealed a hydropic baby with extralobar pulmonary sequestration and bilateral pulmonary hypoplasia. The clinicopathologic presentation of this unusual pulmonary developmental anomaly is discussed.
Correa-Rivas
Maria S
MS
Department of Pathology and Laboratory Medicine, Medical Sciences Campus, University of Puerto Rico, San Juan, Puerto Rico, PO Box 365067, San Juan, Puerto Rico 00936-5067.
Ferrá
Ochoa Susana
OS
D001998:Bronchopulmonary Sequestration / Q000150:complications* / Q000628:therapy; D017809:Fatal Outcome; D006801:Humans; D015160:Hydrops Fetalis / Q000209:etiology* / Q000628:therapy; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities* / Q000473:pathology; D008297:Male