Is severe deficiency of ADAMTS-13 specific for thrombotic thrombocytopenic purpura? Yes.
Tsai
H-M
HM
Division of Hematology, Montefiore Medical Center and Albert Einstein College of Medicine, Bronx, New York 10467, USA. htsai@montefiore.org
D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; D006801:Humans; D008666:Metalloendopeptidases / Q000172:deficiency* / Q000235:genetics; D009154:Mutation; D011697:Purpura, Thrombotic Thrombocytopenic / Q000201:enzymology / Q000209:etiology*; D014841:von Willebrand Factor / Q000378:metabolism
D014841:von Willebrand Factor; D051722:ADAM Proteins; D008666:Metalloendopeptidases; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human