[Prader-Willi Syndrome (PWS) associated to morbid obesity: surgical treatment].
Prader-Willi Syndrome (PWS) is a multisystemic genetic disease characterized by hypothalamic hypogonadism, mental retardation and compulsive hyperphagia associated with early and severe obesity. Complications of overweight, such as type-2 diabetes Mellitus, dyslipidemia and diffuse atheromatosis are common. We report a 15 years old morbid obese male with PWS, with a body mass index of 57.7 kg/m2, refractory to weight-lowering treatments. He underwent preoperative evaluation and treatment by a multidisciplinary team, and subjected to a 95% gastrectomy, leaving a 50 ml remnant pouch and a long limb (120 cm) Y-Roux gastro-jejuno anastomosis. There were no surgical complications, oral feeding was initiated at the 5th day with an hypocaloric diet. During the first postoperative year, the patient lost 70 kg, achieving a body mass index of 30 kg/m2. Surgical treatment can become a therapeutic choice for obesity in PWS patients.
Braghetto
Italo
I
Departamentos de Cirugía, Anestesia, Medicina Sección Endocrinología, Hospital Clínico Universidad de Chile. ibraghet@ns.hospital.uchile.cl
Rodríguez
Alberto
A
Debandi
Aníbal
A
Brunet
Luis
L
Papapietro
Karin
K
Pineda
Pedro
P
Pacheco
María Isabel
MI
D000293:Adolescent; D015992:Body Mass Index; D018530:Gastric Stump / Q000601:surgery; D015391:Gastroplasty; D006801:Humans; D008297:Male; D009767:Obesity, Morbid / Q000209:etiology / Q000601:surgery*; D011218:Prader-Willi Syndrome / Q000150:complications* / Q000601:surgery