Monosegmental living-donor liver transplantation for infantile hepatic hemangioendothelioma.
Infantile hepatic hemangioendothelioma (IHHE) is a rare vascular tumor that presents before the age of 6 months. The patients with IHHE suffer from high-output congestive heart failure caused by major arteriovenous fisutulas in the liver, which leads to respiratory compromise and results in a high mortality rate despite medical treatments. A case of 4-month-old baby with liver failure caused by IHHE is reported. The baby received an urgent liver transplantation from a living donor. A monosegmental graft was used to mitigate graft-to- recipient size mismatching. The surgical procedure of monosegmental living donor liver transplantation also is discussed.
Kasahara
Mureo
M
Organ Transplant Unit, Department of Transplant Surgery, Kyoto University Hospital, Kyoto, Japan.
Kiuchi
Tetsuya
T
Haga
Hironori
H
Uemoto
Shinji
S
Uryuhara
Kenji
K
Fujimoto
Yasuhiro
Y
Ogura
Yasuhiro
Y
Oike
Fumitaka
F
Yokoi
Akiko
A
Kaihara
Satoshi
S
Egawa
Hiroto
H
Tanaka
Koichi
K
D006390:Hemangioendothelioma / Q000601:surgery*; D006801:Humans; D007223:Infant; D008113:Liver Neoplasms / Q000601:surgery*; D016031:Liver Transplantation / Q000379:methods*; D019520:Living Donors; D008297:Male