title: Acral arteriovenous tumor developed within a nevus flammeus in a patient with Sturge-Weber syndrome.
abstract: The Sturge-Weber syndrome consists of a large facial nevus flammeus in the distribution of the ophthalmologic division of the trigeminal nerve accompanied by ipsilateral leptomeningeal angiomatosis. Usually, when angiomatous nodules develop in a nevus flammeus of a patient with Sturge-Weber syndrome they are pyogenic granulomas. We describe an acral arteriovenous tumor developed within the nevus flammeus of a patient with Sturge-Weber syndrome. To our knowledge, acral arteriovenous tumor has not been previously described in the cutaneous vascular malformation of patients with Sturge-Weber syndrome. The development of acral arteriovenous tumor within the vascular malformation of a nevus flammeus in this patient with Sturge-Weber syndrome probably results from a vascular proliferation secondary to underlying arteriovenous shunts.
authors.affiliation: Department of Dermatology, Fundacíon Jiménez Díaz, Universidad Autónoma, Madrid, Spain.
authors.forename: Loreto
authors.initials: L
authors.lastname: Carrasco
authors.forename: Antonia
authors.initials: A
authors.lastname: Pastor
authors.forename: Carmen
authors.initials: C
authors.lastname: Fariña
authors.forename: Lucia
authors.initials: L
authors.lastname: Martín
authors.forename: Félix
authors.initials: F
authors.lastname: Manzarbeitia
authors.forename: Luis
authors.initials: L
authors.lastname: Requena
mesh_terms: D005153:Facial Neoplasms / Q000150:complications* / Q000473:pathology; D005546:Forehead / Q000473:pathology; D006391:Hemangioma / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D019339:Port-Wine Stain / Q000150:complications* / Q000473:pathology; D012878:Skin Neoplasms / Q000150:complications* / Q000473:pathology; D013341:Sturge-Weber Syndrome / Q000150:complications* / Q000473:pathology