title: Scimitar syndrome: complete anatomical and functional diagnosis with gadolinium-enhanced and velocity-encoded cine MRI.
abstract: We report an asymptomatic 8-year-old girl with anomalous pulmonary venous connection to the IVC and systemic arterial supply (scimitar syndrome). We present for the first time a description of gadolinium-enhanced 3D MR angiography that provided concurrent non-invasive complete anatomical (arterial and venous supply) and 'functional' (calculation of left-to-right shunt using phase-contrast-MRI performed in the ascending aorta, main pulmonary artery and anomalous pulmonary vein) diagnosis, avoiding the need for more traditional invasive techniques. As the shunt quantification was less than 2:1, conservative management was decided upon.
authors.affiliation: Department of Radiology, Hospital Universitario Marques de Valdecilla, Santander, Spain. radmle@humv.es
authors.forename: Enrique
authors.initials: E
authors.lastname: Marco de Lucas
authors.forename: Ana
authors.initials: A
authors.lastname: Canga
authors.forename: Pablo
authors.initials: P
authors.lastname: Sadaba
authors.forename: Rafael
authors.initials: R
authors.lastname: Martin-Duran
authors.forename: Macarena
authors.initials: M
authors.lastname: Otero
authors.forename: Luis
authors.initials: L
authors.lastname: Cerezal
mesh_terms: D002648:Child; D003287:Contrast Media; D005260:Female; D019786:Gadolinium DTPA; D006801:Humans; D021621:Imaging, Three-Dimensional; D018810:Magnetic Resonance Angiography; D019028:Magnetic Resonance Imaging, Cine; D012587:Scimitar Syndrome / Q000175:diagnosis* / Q000473:pathology
chemical_list: D003287:Contrast Media; C064925:gadodiamide; D019786:Gadolinium DTPA