title: Atypical Carney's triad with coincidental clear cell renal carcinoma in an 84-year old patient-a finding at autopsy.
abstract: Carney's triad is a syndrome of unknown etiology, representing a combination of gastrointestinal stromal tumors, bronchial chondromas and vagal, adrenal or paraadrenal paragangliomas. Two of the Carney's triad components-the paragangliomas and the gastrointestinal stromal tumors-are potentially lethal. Since its first description in 1977, 79 cases have been reported so far. We report an 84-year-old male patient, who died of a hypertensive cerebral hemorrhage. Well-differentiated clear cell carcinoma of the right kidney, chondroma of the right bronchus and multiple jejunal stromal tumors were detected at autopsy. To our knowledge, this is the first report of a coincidental clear cell renal carcinoma in a patient with an atypical Carney's triad.
authors.affiliation: Institute of Pathology, University of Innsbruck, Müllerstr. 44, A-6020, Innsbruck, Austria. alexandar.tzankov@uibk.ac.at
authors.forename: Alexandar
authors.initials: A
authors.lastname: Tzankov
authors.forename: Josef
authors.initials: J
authors.lastname: Schwanninger
authors.forename: Gregor
authors.initials: G
authors.lastname: Mikuz
authors.forename: Thomas
authors.initials: T
authors.lastname: Mairinger
mesh_terms: D000368:Aged; D000369:Aged, 80 and over; D001344:Autopsy; D002812:Chondroma / Q000473:pathology*; D005770:Gastrointestinal Neoplasms / Q000473:pathology*; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008175:Lung Neoplasms / Q000473:pathology*; D008297:Male; D017154:Stromal Cells / Q000473:pathology; D013577:Syndrome