title: Lymphangioleiomyomatosis and SZ alpha(1)-antitrypsin disease: a unique combination?
abstract: We describe a case of a 37-year-old female ex-smoker with lymphangioleiomyomatosis and SZ alpha(1)-antitrypsin disease who underwent successful bilateral sequential lung transplantation. While this disease combination has not been described previously, we recommend vigilance for the possibility of such combinations in patients with chronic lung disease. The possible mechanisms of interaction resulting from both disease processes are discussed.
authors.affiliation: University of California, Davis Medical Center, Sacramento, CA, USA. alchan@ucdavis.edu
authors.forename: Andrew L
authors.initials: AL
authors.lastname: Chan
authors.forename: Sunye
authors.initials: S
authors.lastname: Kwack
authors.forename: Kirk D
authors.initials: KD
authors.lastname: Jones
authors.forename: Marilyn K
authors.initials: MK
authors.lastname: Glassberg
authors.forename: Charles R
authors.initials: CR
authors.lastname: Gherman
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D016040:Lung Transplantation; D018192:Lymphangioleiomyomatosis / Q000150:complications* / Q000473:pathology / Q000601:surgery; D012129:Respiratory Function Tests; D019896:alpha 1-Antitrypsin Deficiency / Q000150:complications*