title: Deadly defects. Managing the pediatric patient with a congenital heart defect.
abstract: CHD-specific emergencies may be managed quite effectively in the prehospital environment. The key to successful prehospital management of CHDs is identifying the cardiac anomaly, obtaining an effective history and physical assessment, and providing supportive care. When obtaining a history, it is important to remember that parents know their children and their children's diseases very well. An EMS provider who ignores information from a parent is doomed to failure. Realizing that most EMS providers are not well-versed in the various CHDs and are not likely to have a great deal of experience in working with CHD patients, conferring with medical control prior to initiation of any treatments is strongly encouraged. Finally, remember that patients with CHDs are sick and have traditionally been sick for quite a while. Because of the chronic illness, it is easy to focus on the congenital defect when called to the scene for an ill child and neglect the potential for a noncardiac-related pathology. Although the most commonly seen congenital heart defects have been reviewed here, there are others that have not been addressed. Garnering an understanding of each individual defect is not nearly as important as understanding the difference between cyanotic and acyanotic defects. Prehospital care for the CHD patient is primarily supportive, but, in certain cases, may require substantial intervention. EMS providers should not be concerned with diagnosing specific defects, but should be aware of the global effects that various defects have on normal perfusion. EMS providers' comprehension of the pathophysiology of CHDs and prompt actions will play a vital role in the outcome of the acutely ill CHD patient.
authors.affiliation: Emergency Medicine Special Operations Institute, University of Cincinnati College of Medicine, Cincinnati, OH, USA.
authors.forename: William
authors.initials: W
authors.lastname: Krost
mesh_terms: D002648:Child; D004632:Emergency Medical Services / Q000379:methods*; D004638:Emergency Treatment; D006330:Heart Defects, Congenital / Q000453:epidemiology / Q000503:physiopathology / Q000628:therapy*; D006801:Humans; D014481:United States / Q000453:epidemiology