title: Congenital pulmonary capillary hemangiomatosis: Report of two cases and review of the literature.
abstract: Pulmonary capillary hemangiomatosis (PCH) is a rare disease characterized by pulmonary hypertension and excessive neovascularization within the pulmonary interstitium, vasculature, and airways. We describe two unusual cases of congenital PCH. Both cases had concurrent anomalies, including renal and urinary bladder agenesis and hypertropic cardiomyopathy. In one case, capillary proliferation caused significant impingement of the proximal bronchial airways. A review of the current literature is described.
authors.affiliation: Department of Pathology, Northwestern University Medical School, Chicago, Illinois, USA.
authors.forename: Angelica
authors.initials: A
authors.lastname: Oviedo
authors.forename: Lisa P
authors.initials: LP
authors.lastname: Abramson
authors.forename: Ross
authors.initials: R
authors.lastname: Worthington
authors.forename: John R
authors.initials: JR
authors.lastname: Dainauskas
authors.forename: Susan E
authors.initials: SE
authors.lastname: Crawford
mesh_terms: D002312:Cardiomyopathy, Hypertrophic; D005260:Female; D018324:Hemangioma, Capillary / Q000150:complications / Q000151:congenital / Q000473:pathology*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D007231:Infant, Newborn; D008175:Lung Neoplasms / Q000150:complications / Q000151:congenital / Q000473:pathology*; D008297:Male; D008944:Mitral Valve Insufficiency; D011247:Pregnancy; D011256:Pregnancy Outcome; D014427:Twins