title: [Primary leptomeningeal sarcomatosis. Case report].
abstract: Primary intracranial sarcomas are very rare and aggressive tumors. A case of a 40-year-old woman with primary leptomeningeal sarcomatosis is presented. Initially her clinical symptoms resembled those of a pseudo tumor cerebri. Neuroimaging did not allow establishing a diagnosis of leptomeninges neoplastic infiltration. The patient died 8 months since the onset of symptoms. A neuropathological examination revealed diffuse thickening of leptomeninges. Microscopically a widespread sarcomatous infiltration of the subarachnoid space was shown, as well as a neoplastic infiltration of the choroid plexus and of some perivascular spaces in the cerebral cortex. On the grounds of a review of the literature diagnostic problems, differential diagnosis and clinical course of primary leptomeningeal sarcomatosis are discussed.
authors.affiliation: Oddziału Neurologii Szpitala Wojewódzkiego im. Jana Pawła II w Bełchatowie.
authors.forename: Arkadiusz
authors.initials: A
authors.lastname: Weglewski
authors.forename: Jacek
authors.initials: J
authors.lastname: Juryńczyk
authors.forename: Wielisław
authors.initials: W
authors.lastname: Papierz
mesh_terms: D000328:Adult; D001921:Brain / Q000473:pathology*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008577:Meningeal Neoplasms / Q000473:pathology*; D012509:Sarcoma / Q000473:pathology*