Oral manifestations of triple A syndrome.
Triple A (four A; Allgrove syndrome) syndrome is a an autosomal recessive disorder characterized by alacrimia, achalasia, adrenocortical insufficiency, and various neurological abnormalities. We report a case of triple A syndrome in a 14-year-old female patient together with oral manifestations. The importance of this case report is to highlight the necessity of referring the young patients with xerostomia from dental to medical specialists.
Vucicevic-Boras
V
V
Department of Oral Medicine, School of Dental Medicine, Zagreb, Croatia. vvboras@hotmail.com
Juras
D
D
Gruden-Pokupec
J S
JS
Vidovic
A
A
D000293:Adolescent; D000309:Adrenal Insufficiency / Q000150:complications; D004931:Esophageal Achalasia / Q000150:complications; D005260:Female; D006801:Humans; D007766:Lacrimal Apparatus Diseases / Q000150:complications; D013577:Syndrome; D014059:Tongue / Q000473:pathology; D014987:Xerostomia / Q000175:diagnosis / Q000209:etiology / Q000235:genetics