Giant desmoid tumor of the abdominal wall associated with familial adenomatous polyposis.
In this paper a case of vast desmoid tumor of the abdominal wall associated with familial adenomatous polyposis is reported. Desmoid tumors represent a particular type of fibrous neoplasms with a higher prevalence in females. They are extremely rare in the sporadic form, while they are found in about 10% of patients affected by familial adenomatous polyposis. Despite their benign histology and the absence of metastatic potential, they can be considered as fibrosarcomas with a low level of malignancy because of their locally invasive nature. The treatment of choice is surgical excision, as wide as possible, aimed at preventing recurrences, which are frequent in this tumor type. The usefulness of complementary therapies such as radiotherapy, hormone or chemotherapy, is not entirely clear.
Marone
Ugo
U
Department of Surgery B, National Cancer Institute, G Pascale Foundation, Naples, Italy. dott.marone@virgilio.it
Amore
Alfonso
A
Pezzullo
Luciano
L
Mozzillo
Nicola
N
D000008:Abdominal Neoplasms / Q000175:diagnosis* / Q000473:pathology; D011125:Adenomatous Polyposis Coli / Q000150:complications* / Q000235:genetics / Q000601:surgery; D000328:Adult; D018450:Disease Progression; D005260:Female; D018221:Fibromatosis, Abdominal / Q000473:pathology* / Q000601:surgery; D006801:Humans; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis / Q000473:pathology; D011379:Prognosis