Hepatocarcinoma with congenital agenesis of the portal vein.
The association of congenital absence of the portal vein and hepatocellular carcinoma has been described, but is rare. It is most frequently discovered fortuitously in children. The absence of intrahepatic portal circulation may predispose to the development of hepatocarcinoma.
Pichon
Nicolas
N
Department of Hepatology-Gastroenterology, Dupuytren University Hospital, Limoges, France. n.pichon@libertysurf.fr
Maisonnette
Franck
F
Pichon-Lefièvre
Florence
F
Valleix
Denis
D
Pillegand
Bernard
B
D000328:Adult; D006528:Carcinoma, Hepatocellular / Q000000981:diagnostic imaging / Q000209:etiology*; D005260:Female; D006801:Humans; D008113:Liver Neoplasms / Q000000981:diagnostic imaging / Q000209:etiology*; D011169:Portal Vein / Q000002:abnormalities*; D014463:Ultrasonography