Congenital pulmonary capillary hemangiomatosis: Report of two cases and review of the literature.
Pulmonary capillary hemangiomatosis (PCH) is a rare disease characterized by pulmonary hypertension and excessive neovascularization within the pulmonary interstitium, vasculature, and airways. We describe two unusual cases of congenital PCH. Both cases had concurrent anomalies, including renal and urinary bladder agenesis and hypertropic cardiomyopathy. In one case, capillary proliferation caused significant impingement of the proximal bronchial airways. A review of the current literature is described.
Oviedo
Angelica
A
Department of Pathology, Northwestern University Medical School, Chicago, Illinois, USA.
Abramson
Lisa P
LP
Worthington
Ross
R
Dainauskas
John R
JR
Crawford
Susan E
SE
D002312:Cardiomyopathy, Hypertrophic; D005260:Female; D018324:Hemangioma, Capillary / Q000150:complications / Q000151:congenital / Q000473:pathology*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D007231:Infant, Newborn; D008175:Lung Neoplasms / Q000150:complications / Q000151:congenital / Q000473:pathology*; D008297:Male; D008944:Mitral Valve Insufficiency; D011247:Pregnancy; D011256:Pregnancy Outcome; D014427:Twins